An Interesting Case of Heart Failure in a Patient with Bicuspid Aortic Valve - Unveiling the Diagnosis of Amyloidosis

Abstract

Restrictive cardiomyopathy (RCMP) is infrequent in occurrence compared to the other cardiomyopathies. The stiff ventricular walls impair the diastolic function, increase the filling pressures, and thereby result in heart failure. Amyloidosis, a systemic disorder is the most common cause of RCMP. The amyloid diagnosis is often missed as the features are masqueraded by the presence of other conditions. The Bicuspid aortic valve (BAV) is the most common congenital anomaly of the cardiovascular system occurring in approximately 0.5-2% of the general population. We present a case of bicuspid aortic valvular heart disease masking the amyloidosis with heart failure in a middle-aged male.