Retroperitoneal Extraskeletal Ewing’s Sarcoma in Adult

Abstract

Ewing’s sarcoma is a highly malignant tumour of osseous or non-osseous origin, typically seen in the paediatric and adolescent age group. However, extraskeletal Ewing’s sarcoma is an uncommon tumour. It could arise from the soft tissue in the paravertebral area, chest wall, head and neck, and retroperitoneum. Retroperitoneal extraosseous Ewing’s sarcoma is even rarer, with only a few reported cases in the literature. We describe the radiologic findings of this rare retroperitoneal extraskeletal Ewing sarcoma manifested in an adult patient. Our patient is a 32-year-old gentleman who presented with abdominal pain and constitutional symptoms for two months. Imaging shows a retroperitoneal tumour with local infiltration. It was confirmed via histopathological analysis as retroperitoneal Ewing’s sarcoma. We discussed the diagnostic strategy as well as the literature review of this rare disease.