Alberto De Anda-Coronado, Nohemí C López-Leonar, Eduardo Navarro-Bahena, Gerardo E Muñoz-Maldonado
{"title":"Interscapular-thoracic Amputation: A Giant Dermatofibrosarcoma Protuberans Tumor.","authors":"Alberto De Anda-Coronado, Nohemí C López-Leonar, Eduardo Navarro-Bahena, Gerardo E Muñoz-Maldonado","doi":"10.14744/etd.2022.48457","DOIUrl":null,"url":null,"abstract":"<p><strong>Background: </strong>Dermatofibrosarcoma protuberans (DFSP), an uncommon sarcoma of the dermis, is a low-grade, spindle-cell tumor that usually grows slowly and has a high local recurrence rate, but rarely metastasizes to distant sites. The diagnosis is based on histopathology and the standard treatment is wide surgical excision with tumor-free margins.</p><p><strong>Case report: </strong>Described is the case of a 75-year-old female who presented with a giant tumor on her upper right arm that had been increasing in size for a year. A biopsy provided the diagnosis of DFSP. Radical surgery was performed and the arm was disarticulated from the scapula.</p><p><strong>Conclusion: </strong>Treatment for DFSP typically involves surgical excision; however, the size of the tumor in the present case was exceptionally large. Disarticulation offered the best prognosis.</p>","PeriodicalId":43995,"journal":{"name":"Erciyes Medical Journal","volume":"10 1","pages":"300-302"},"PeriodicalIF":0.2000,"publicationDate":"2022-10-17","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC12478645/pdf/","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Erciyes Medical Journal","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.14744/etd.2022.48457","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2023/5/1 0:00:00","PubModel":"eCollection","JCR":"Q3","JCRName":"MEDICINE, GENERAL & INTERNAL","Score":null,"Total":0}
引用次数: 0
Abstract
Background: Dermatofibrosarcoma protuberans (DFSP), an uncommon sarcoma of the dermis, is a low-grade, spindle-cell tumor that usually grows slowly and has a high local recurrence rate, but rarely metastasizes to distant sites. The diagnosis is based on histopathology and the standard treatment is wide surgical excision with tumor-free margins.
Case report: Described is the case of a 75-year-old female who presented with a giant tumor on her upper right arm that had been increasing in size for a year. A biopsy provided the diagnosis of DFSP. Radical surgery was performed and the arm was disarticulated from the scapula.
Conclusion: Treatment for DFSP typically involves surgical excision; however, the size of the tumor in the present case was exceptionally large. Disarticulation offered the best prognosis.
期刊介绍:
Erciyes Medical Journal (Erciyes Med J) is the international, peer-reviewed, open access publication of Erciyes University School of Medicine. The journal, which has been in continuous publication since 1978, is a publication published on March, June, September, and December. The publication language of the journal is English. The journal accepts clinical and experimental research articles in different fields of medicine, original case reports, letters to the editor and invited reviews for publication. Research articles and case reports on regionally frequent and specific medical topics are prioritized. Manuscripts on national and international scientific meetings and symposiums and manuscripts sharing scientific correspondence and scientific knowledge between authors and their readers are also published.