Renal Amyloidosis Secondary to ANCA-Associated Vasculitis: A Case Report

Q2 Medicine Chinese Medical Sciences Journal Pub Date : 2022-12-01 DOI:10.24920/003999
Xin He , Jianping Ning , Hui Xu , Gong Xiao , Huixiang Yang , Weiyuan Wang , Xiaoying Wu , Hongling Yin , Xiaozhao Li
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引用次数: 0

Abstract

Renal amyloidosis secondary to anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis is extremely rare. Here, we reported a 77-year-old woman with ANCA-associated vasculitis. Renal biopsy with Masson trichrome staining showed pauci-immune crescentic glomerulonephritis, and electron microscopy showed amyloid deposition in the mesangial area. Immunofluorescence revealed kappa light chain and lambda light chain negative. Bone marrow biopsy revealed no clonal plasma cell. Finally, she was diagnosed as ANCA-associated vasculitis with secondary renal amyloid A amyloidosis.

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肾淀粉样变继发于anca相关血管炎1例报告
肾淀粉样变继发于抗中性粒细胞细胞质抗体(ANCA)相关的血管炎是非常罕见的。在这里,我们报告了一位77岁的女性患有anca相关的血管炎。肾活检马松三色染色显示少免疫新月型肾小球肾炎,电镜显示系膜区淀粉样蛋白沉积。免疫荧光显示kappa轻链和lambda轻链阴性。骨髓活检未见克隆浆细胞。最后,她被诊断为anca相关性血管炎伴继发性肾淀粉样蛋白A淀粉样变。
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来源期刊
Chinese Medical Sciences Journal
Chinese Medical Sciences Journal Medicine-Medicine (all)
CiteScore
2.40
自引率
0.00%
发文量
1275
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