M C Meazzini, L P Demonte, L Conti, L Autelitano, N Cohen, F Mazzoleni
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引用次数: 0
Abstract
Aim: The aim of this study was to analyse the facial characteristics and the craniofacial morphology in GGS patients in order to enable an early diagnosis.
Background: Gorlin-Goltz syndrome (GGS) is a autosomic dominant disease, characterised by basal cell carcinoma, palmar/plantar pits, maxillary and mandibular keratocysts and dental abnormalities.
Methods: Nine out of a sample of 24 GGS patients had complete cephalometric and photographic records at an average age of 8.7 years. Cephalometric and photometric analysis were carried out with standard analyses and compared with healthy patients matched for sex and age.
Conclusion: Early diagnosis of GGS based on clinical features could be useful to identify the presence of keratocysts through x-ray examination proceeding with surgical removal at an early stage, limiting space occupying damages.
期刊介绍:
The aim and scope of the European Journal of Paediatric Dentistry is to promote research in all aspects of dentistry related to children, including interceptive orthodontics and studies on children and young adults with special needs.