Rapidly progressive renal dysfunction in systemic sclerosis Scleroderma renal crisis

Systemic sclerosis is an autoimmune disorder involving skin, gastro-intestinal tract, lungs, kidneys and heart. Rapidly progressive renal dysfunction and accelerated hypertension remains the hallmark for scleroderma renal crisis in patients of Systemic sclerosis. Here we present a case of 38 year old male patient who presented with clinical signs of systemic sclerosis and unexplained renal dysfunction associated with hypertension. A provisional of Scleroderma renal crisis was expected but renal biopsy, surprisingly, revealed features suggestive of Crescentric Glomerulonephritis.