伴有皮外肺部表现的硬肌水肿:病例报告和文献综述

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引用次数: 0

摘要

硬化性粘液性水肿是一种病因不明的皮肤纤维瘤病。它与血液学异常和多种多样的表现有关。肺血管受累很少见,需要与系统性硬化症进行鉴别诊断。本病例描述了一名伴有皮外肺部表现的硬肌水肿患者。
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Scleromyxoedema with extracutaneous pulmonary manifestation: A case report and review of the literature

Scleromyxoedema is a cutaneous fibromucinosis of unknown aetiology. It is associated with haematological dyscrasias and quite diverse manifestations. Pulmonary vascular involvement is rare and requires a differential diagnosis approach with systemic sclerosis. The case of a patient with scleromyxoedema with an extracutaneous pulmonary manifestation is described.

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