Kyota Bando, Yuki Kondo, Yuta Miyazaki, Takatoshi Hara, Yuji Takahashi
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引用次数: 0
摘要
与遗传性脊髓小脑变性(hSCD)相比,多系统萎缩-小脑型(MSA-C)的疾病进展更快。在这项研究中,我们旨在研究hSCD患者和MSA-C患者在强化康复治疗效果和可持续性方面的差异。49名患者(hSCD=30人,MSA-C=19人)接受了为期2周或4周的强化康复训练。在干预前、干预后和 6 个月的随访中,使用共济失调评估和评级量表(SARA)和平衡评估系统测试(BESTest)对患者的平衡功能进行了评估。值得注意的是,两组患者都从康复干预中获益。然而,在这些效果的程度和持续时间上却出现了差异。在 hSCD 组中,随访时的 SARA 分数与基线时的分数相似,这表明疗效具有持续性。然而,与基线分数相比,MSA-C 组的 SARA 分数有所下降,但 BESTest 分数仍有改善,这表明了部分持续性。在 hSCD 组和 MSA-C 组之间观察到了差异,主要是持续性方面的差异。这可能是由于症状进展的速度不同造成的。考虑到根据疾病类型进行随访的频率,本研究的结果具有重要意义。
Differences in the Impact of Intensive Rehabilitation on Hereditary Ataxias and the Cerebellar Subtype of Multiple System Atrophy.
Multiple system atrophy-cerebellar type (MSA-C) exhibits faster disease progression than does hereditary spinocerebellar degeneration (hSCD). In this study, we aimed to investigate the differences in the treatment effects and sustainability of intensive rehabilitation between patients with hSCD and those with MSA-C. Forty-nine patients (hSCD = 30, MSA-C = 19) underwent a 2- or 4-week intensive rehabilitation program. Balance function was evaluated using the scale for the assessment and rating of ataxia (SARA) and the balance evaluation systems test (BESTest) at pre-intervention, post-intervention, and 6-month follow-up. Notably, both groups demonstrated beneficial effects from the rehabilitation intervention. However, differences were observed in the magnitude and duration of these effects. In the hSCD group, the SARA scores at follow-up remained similar to those at baseline, indicating sustained benefits. However, the MSA-C group showed some deterioration in SARA scores compared with baseline scores but maintained improvements on the BESTest, demonstrating partial sustainability. Differences, mainly in sustainability, were observed between the hSCD and MSA-C groups. This may be due to varying rates of symptom progression. The findings of this study are significant when considering the frequency of follow-ups based on disease type.
期刊介绍:
Official publication of the Society for Research on the Cerebellum devoted to genetics of cerebellar ataxias, role of cerebellum in motor control and cognitive function, and amid an ageing population, diseases associated with cerebellar dysfunction.
The Cerebellum is a central source for the latest developments in fundamental neurosciences including molecular and cellular biology; behavioural neurosciences and neurochemistry; genetics; fundamental and clinical neurophysiology; neurology and neuropathology; cognition and neuroimaging.
The Cerebellum benefits neuroscientists in molecular and cellular biology; neurophysiologists; researchers in neurotransmission; neurologists; radiologists; paediatricians; neuropsychologists; students of neurology and psychiatry and others.