{"title":"一种罕见的呼吸困难的原因:穆尼埃·库恩综合征。","authors":"Feryal El Oualladi MD, Mohamed Labied MD, Ismail Bouzid MD, Chorouk Mountassir MD, Ghizlane Lembarki MD, Mouna Sabiri PhD, Samira Lezar PhD.","doi":"10.1016/j.radcr.2024.11.015","DOIUrl":null,"url":null,"abstract":"<div><div>Mounier-Kuhn syndrome, also known as tracheobronchomegaly, is a rare clinical and radiological condition characterized by tracheobronchial dilatation and recurrent respiratory infections. Patients may be asymptomatic or present with severe respiratory illnesses. A CT scan is sufficient to confirm the diagnosis. Treatment is symptomatic, and surgery is rarely indicated. We present the case of a 55-year-old patient with a 30-year history of chronic dyspnea, who presented with worsening shortness of breath, a productive cough, and episodes of bronchial superinfection. A chest CT scan, performed before and after contrast injection during both inspiratory and expiratory phases, confirmed the diagnosis of Mounier-Kuhn syndrome. This case aims to raise awareness of this rare condition and highlights a presentation where dyspnea is the primary symptom.</div></div>","PeriodicalId":53472,"journal":{"name":"Radiology Case Reports","volume":"20 2","pages":"Pages 1268-1272"},"PeriodicalIF":0.0000,"publicationDate":"2025-02-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11665394/pdf/","citationCount":"0","resultStr":"{\"title\":\"A rare cause of dyspnea: Mounier Kuhn syndrome\",\"authors\":\"Feryal El Oualladi MD, Mohamed Labied MD, Ismail Bouzid MD, Chorouk Mountassir MD, Ghizlane Lembarki MD, Mouna Sabiri PhD, Samira Lezar PhD.\",\"doi\":\"10.1016/j.radcr.2024.11.015\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<div><div>Mounier-Kuhn syndrome, also known as tracheobronchomegaly, is a rare clinical and radiological condition characterized by tracheobronchial dilatation and recurrent respiratory infections. Patients may be asymptomatic or present with severe respiratory illnesses. A CT scan is sufficient to confirm the diagnosis. Treatment is symptomatic, and surgery is rarely indicated. We present the case of a 55-year-old patient with a 30-year history of chronic dyspnea, who presented with worsening shortness of breath, a productive cough, and episodes of bronchial superinfection. A chest CT scan, performed before and after contrast injection during both inspiratory and expiratory phases, confirmed the diagnosis of Mounier-Kuhn syndrome. This case aims to raise awareness of this rare condition and highlights a presentation where dyspnea is the primary symptom.</div></div>\",\"PeriodicalId\":53472,\"journal\":{\"name\":\"Radiology Case Reports\",\"volume\":\"20 2\",\"pages\":\"Pages 1268-1272\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2025-02-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11665394/pdf/\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Radiology Case Reports\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://www.sciencedirect.com/science/article/pii/S193004332401286X\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"Q4\",\"JCRName\":\"Medicine\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Radiology Case Reports","FirstCategoryId":"1085","ListUrlMain":"https://www.sciencedirect.com/science/article/pii/S193004332401286X","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q4","JCRName":"Medicine","Score":null,"Total":0}
Mounier-Kuhn syndrome, also known as tracheobronchomegaly, is a rare clinical and radiological condition characterized by tracheobronchial dilatation and recurrent respiratory infections. Patients may be asymptomatic or present with severe respiratory illnesses. A CT scan is sufficient to confirm the diagnosis. Treatment is symptomatic, and surgery is rarely indicated. We present the case of a 55-year-old patient with a 30-year history of chronic dyspnea, who presented with worsening shortness of breath, a productive cough, and episodes of bronchial superinfection. A chest CT scan, performed before and after contrast injection during both inspiratory and expiratory phases, confirmed the diagnosis of Mounier-Kuhn syndrome. This case aims to raise awareness of this rare condition and highlights a presentation where dyspnea is the primary symptom.
期刊介绍:
The content of this journal is exclusively case reports that feature diagnostic imaging. Categories in which case reports can be placed include the musculoskeletal system, spine, central nervous system, head and neck, cardiovascular, chest, gastrointestinal, genitourinary, multisystem, pediatric, emergency, women''s imaging, oncologic, normal variants, medical devices, foreign bodies, interventional radiology, nuclear medicine, molecular imaging, ultrasonography, imaging artifacts, forensic, anthropological, and medical-legal. Articles must be well-documented and include a review of the appropriate literature.