klippel - trsamnaunay综合征-一种非常罕见和有趣的综合征。

IF 1 Q4 RESPIRATORY SYSTEM Clinical Medicine Insights-Circulatory Respiratory and Pulmonary Medicine Pub Date : 2015-03-05 eCollection Date: 2015-01-01 DOI:10.4137/CCRPM.S21645
Deepak Sharma, Sachin Lamba, Aakash Pandita, Sweta Shastri
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引用次数: 35

摘要

klippel - trsamnaunay综合征(KTS或KT)是一种罕见的皮肤病综合征,通常被认为是血管畸形(毛细血管畸形或波特酒品牌)、静脉曲张、软组织和/或骨质肥大的三重症状。我们报告一个12岁的男性病例,他向我们提出了下肢静脉曲张斑块的症状,并被诊断为KTS病例。治疗通常是保守的,包括用长统袜压迫树枝以减少因慢性静脉功能不全引起的水肿;使气动压缩开关的现代装置;很少有手术矫正静脉曲张并终生随访。矫形畸形采用表皮成形术治疗,以防止(阻止)肢体过度生长,矫正骨畸形。
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Klippel-trénaunay syndrome - a very rare and interesting syndrome.

Klippel-Trénaunay syndrome (KTS or KT) is an infrequently seen dermatological syndrome, which is often viewed as a triad of vascular malformation (capillary malformations or port-wine brands), venous varicosity, and soft tissue and/or bony hypertrophy. We report a case of a 12-year-old male who presented to us with the symptoms of varicose plaques over both lower limbs and was diagnosed as a case of KTS. Management is normally conservative and includes stockings for compression of the branches to reduce edema because of chronic venous insufficiency; modern devices that cause on and off pneumatic compression; and rarely, surgical correction of varicose veins with lifelong follow-up. The orthopedic abnormalities are treated with epiphysiodesis in order to prevent (stop) overgrowing of limb and correction of bone deformity.

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CiteScore
4.20
自引率
0.00%
发文量
9
审稿时长
8 weeks
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