复发性抗mog相关脑皮质脑炎模拟病毒性脑炎及偏瘫性偏头痛1例

Q4 Medicine Annals of Child Neurology Pub Date : 2022-12-13 DOI:10.26815/acn.2022.00318
D. Kwon, Soung-Kyung Park, J. Cho, J. Yeom
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引用次数: 0

摘要

髓鞘少突胶质细胞糖蛋白(MOG)是少突胶质表面膜的重要成分[1]。许多研究已将MOG用于免疫介导的脱髓鞘疾病,包括急性播散性脑脊髓炎、视神经炎和横贯性脊髓炎[2]。然而,MOG抗体相关疾病并不局限于脱髓鞘综合征。Ogawa等人[2]于2017年首次描述的大脑皮层脑炎(CCE)是一种新发现的MOG抗体相关疾病表型。抗MOG相关CCE的常见症状包括癫痫发作、头痛、脑炎和皮质症状,如轻瘫[2]。单侧皮质高信号
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A Case of Recurrent Anti-MOG-Associated Cerebral Cortical Encephalitis Mimicking Viral Encephalitis and Hemiplegic Migraine
Myelin oligodendrocyte glycoprotein (MOG) is an essential component of oligodendrocyte sur-face membranes [1]. Numerous studies have im-plicated MOG in immune-mediated demyelinating diseases, including acute disseminated en-cephalomyelitis, optic neuritis, and transverse myelitis [2]. However, MOG antibody-associated diseases are not limited to demyelinating syndromes. Cerebral cortical encephalitis (CCE), first described by Ogawa et al. [2] in 2017, is a newly identified phenotype of MOG antibody-associated disease. Common symptoms of anti-MOG-associated CCE include seizures, headache, encephalitic features, and cortical symptoms, such as paresis [2]. Unilateral cortical hyperintensities
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来源期刊
Annals of Child Neurology
Annals of Child Neurology Medicine-Pediatrics, Perinatology and Child Health
CiteScore
0.50
自引率
0.00%
发文量
35
审稿时长
8 weeks
期刊最新文献
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