Omphalocele major with spine deformity, a congenital anomaly

Multigravida, 26 years old lady with 21 weeks gestation came with complaint of abdominal pain diagnosed as Omphalocele major with spine deformity. Due to associated anomalies, the pregnancy was terminated with parental consent. On dissection, it was observed that liver and small intestine protruded from right and left side respectively through the defect. Acute angulation of the Spine was observed. There was a privilege of intervention of omphalocele of various clinical presentations. Here is an attempt made to describe in this case which will be helpful to paediatric surgeons for interventions.