{"title":"非流质原发性进行性失语症","authors":"N. Mahendra, Ashlyn Tadokoro","doi":"10.1097/TLD.0000000000000221","DOIUrl":null,"url":null,"abstract":"Purpose: Nonfluent primary progressive aphasia (nfvPPA) is an established language-led dementia and a known variant of frontotemporal degeneration. The purpose of this article is to report the trajectory of a single case, AC, diagnosed with nfvPPA. We describe a range of interventions offered to AC over 3 years that aimed to support her communicative function, social participation, sense of identity, and emotional well-being. We offer reflections on how these interventions align with palliative care principles, highlighting their value for guiding communication and life participation interventions for persons with nfvPPA. Method: This study used a longitudinal analysis of impairment progression, traditional outcome measures, patient-reported outcome measures, and narrative description to report on patient and family response to interventions. Results: Individual and group interventions are critical for addressing the progressive communication impairments and life participation restrictions for persons affected by nfvPPA. Palliative care principles have intuitive appeal for informing the selection of intervention approaches while focusing on managing symptoms, upholding patient autonomy and dignity, and enhancing quality of life throughout the course of rapidly progressive conditions like primary progressive aphasia. Discussion/Conclusion: Speech–language pathologist-led interventions, grounded in palliative care principles, can optimize communicative function and quality of life for persons with nfvPPA.","PeriodicalId":51604,"journal":{"name":"Topics in Language Disorders","volume":"40 1","pages":"E7 - E24"},"PeriodicalIF":1.8000,"publicationDate":"2020-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1097/TLD.0000000000000221","citationCount":"5","resultStr":"{\"title\":\"Nonfluent Primary Progressive Aphasia\",\"authors\":\"N. Mahendra, Ashlyn Tadokoro\",\"doi\":\"10.1097/TLD.0000000000000221\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Purpose: Nonfluent primary progressive aphasia (nfvPPA) is an established language-led dementia and a known variant of frontotemporal degeneration. The purpose of this article is to report the trajectory of a single case, AC, diagnosed with nfvPPA. We describe a range of interventions offered to AC over 3 years that aimed to support her communicative function, social participation, sense of identity, and emotional well-being. We offer reflections on how these interventions align with palliative care principles, highlighting their value for guiding communication and life participation interventions for persons with nfvPPA. Method: This study used a longitudinal analysis of impairment progression, traditional outcome measures, patient-reported outcome measures, and narrative description to report on patient and family response to interventions. Results: Individual and group interventions are critical for addressing the progressive communication impairments and life participation restrictions for persons affected by nfvPPA. Palliative care principles have intuitive appeal for informing the selection of intervention approaches while focusing on managing symptoms, upholding patient autonomy and dignity, and enhancing quality of life throughout the course of rapidly progressive conditions like primary progressive aphasia. Discussion/Conclusion: Speech–language pathologist-led interventions, grounded in palliative care principles, can optimize communicative function and quality of life for persons with nfvPPA.\",\"PeriodicalId\":51604,\"journal\":{\"name\":\"Topics in Language Disorders\",\"volume\":\"40 1\",\"pages\":\"E7 - E24\"},\"PeriodicalIF\":1.8000,\"publicationDate\":\"2020-07-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://sci-hub-pdf.com/10.1097/TLD.0000000000000221\",\"citationCount\":\"5\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Topics in Language Disorders\",\"FirstCategoryId\":\"3\",\"ListUrlMain\":\"https://doi.org/10.1097/TLD.0000000000000221\",\"RegionNum\":4,\"RegionCategory\":\"医学\",\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"Q1\",\"JCRName\":\"LINGUISTICS\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Topics in Language Disorders","FirstCategoryId":"3","ListUrlMain":"https://doi.org/10.1097/TLD.0000000000000221","RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q1","JCRName":"LINGUISTICS","Score":null,"Total":0}
Purpose: Nonfluent primary progressive aphasia (nfvPPA) is an established language-led dementia and a known variant of frontotemporal degeneration. The purpose of this article is to report the trajectory of a single case, AC, diagnosed with nfvPPA. We describe a range of interventions offered to AC over 3 years that aimed to support her communicative function, social participation, sense of identity, and emotional well-being. We offer reflections on how these interventions align with palliative care principles, highlighting their value for guiding communication and life participation interventions for persons with nfvPPA. Method: This study used a longitudinal analysis of impairment progression, traditional outcome measures, patient-reported outcome measures, and narrative description to report on patient and family response to interventions. Results: Individual and group interventions are critical for addressing the progressive communication impairments and life participation restrictions for persons affected by nfvPPA. Palliative care principles have intuitive appeal for informing the selection of intervention approaches while focusing on managing symptoms, upholding patient autonomy and dignity, and enhancing quality of life throughout the course of rapidly progressive conditions like primary progressive aphasia. Discussion/Conclusion: Speech–language pathologist-led interventions, grounded in palliative care principles, can optimize communicative function and quality of life for persons with nfvPPA.
期刊介绍:
Topics in Language Disorders (TLD) is a double-blind peer-reviewed topical journal that has dual purposes: (1) to serve as a scholarly resource for researchers and clinicians who share an interest in spoken and written language development and disorders across the lifespan, with a focus on interdisciplinary and international concerns; and (2) to provide relevant information to support theoretically sound, culturally sensitive, research-based clinical practices.