Pulmonary sequestration associated with congenital pulmonary airway malformation

Background: Congenital pulmonary malformations are a rare cause of neonatal morbidity. Some of them have a common origin, which allows the identification of combined lesions. Its diagnosis can be made prenatally by ultrasound, with the limitation that this study is performed in specialized centers and depends on the expertise of the operator. The association of pulmonary sequestration and congenital malformation of the airway has been described in approximately 40-60 cases since its first description in 1949. Many lesions are not perceptible in intrauterine life, and in the neonatal period, there are recurrent respiratory symptoms that in some cases are associated with a congenital pulmonary malformation. case report: We report the case of a young infant, who was diagnosed with pulmonary sequestration at 24 weeks of gestational age, undergoing intrauterine surgical treatment with a report of complete resolution of the malformation in posterior ultrasounds. She was valued by pediatric pneumology at four months of age, where angiotomography was performed, and the presence of pulmonary sequestration was confirmed by lobectomy. The histopathological study reported extralobar pulmonary sequestration with congenital malformation of the pulmonary airway type 2. The histopathological study identified these combined lesions. The treatment of choice was surgical. conclusions: Upon the confirmation of a malformation, we emphasize the importance of performing screening to search for other that could be associated.