Keratosis Follicularis Spinulosa Decalvans: A New Observation

Scarring alopecia in association with follicular hyperkeratosis is the primary characteristic of keratosis pilaris atrophicans (KPA). It affects mainly the face and scalp and can be inflammatory in nature [1]. Widespread KP can also be seen. keratosis pilaris atrophicans is a group of cutaneous disorders that may represent a spectrum of 1 disease. Differences in localization and the degree of inflammation and atrophy have been used to distinguish these various disorders [1]. They are genetic disorders with different modes of inheritance. Heterogeneity in the mode of inheritance exists not only between different types of KPA but also within 1 type, such as keratosis follicularis spinulosa decalvans (KFSD) [1, 2]. The pathogenesis is not known, but abnormal follicular keratinization has been suggested.