INTERSTITIAL LUNG DISEASES IN CHILDREN: MODERN CLASSIFICATION, DIAGNOSTIC ALGORITHM, COMMON THERAPEUTIC APPROACHES

Q4 Medicine Pediatriya - Zhurnal im G.N. Speranskogo Pub Date : 2023-10-13 DOI:10.24110/0031-403x-2023-102-5-103-115

M.A. Zhestkova, D.Yu. Ovsyannikov, V.A. Strelnikova, E.S. Petryaykina, Sh.A. Gitinov, E.V. Boytsova, A.A. Pushkov, K.V. Savostyanov

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Abstract

Authors, based on bibliographical research and their own data, provide up-to-date information on interstitial lung diseases (ILD) in children. The classification of ILD in children that is used in the registry of pediatric patients with ILD in the European Union (2022) with a critical analysis is given, and the need for its practical use is substantiated. The algorithm for diagnosing childhood ILD is described in detail starting with the diagnostic criteria for childhood ILD syndrome and possible complications. The algorithm includes step-by-step, sequential steps to diagnose these rare diseases. Taking into account the latest advances in genetics and molecular biology, the main proteins and their encoding genes associated with ILD, types of inheritance and phenotypes are listed as well. Indications and findings during lung biopsy, general approaches to the treatment of ILD in children, including oxygen therapy, drug therapy and other therapy, taking into account the existing consensus of experts, are characterized.

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儿童间质性肺疾病:现代分类、诊断算法、常见治疗方法

作者基于文献研究和他们自己的数据，提供了关于儿童间质性肺病(ILD)的最新信息。本文给出了欧盟(2022)儿童ILD患者登记中使用的儿童ILD分类，并对其进行了批判性分析，并证实了其实际使用的必要性。从儿童ILD综合征的诊断标准和可能的并发症开始，详细描述了诊断儿童ILD的算法。该算法包括一步一步、连续的步骤来诊断这些罕见疾病。考虑到遗传学和分子生物学的最新进展，列出了与ILD相关的主要蛋白质及其编码基因、遗传类型和表型。在肺活检的适应症和发现，一般的方法治疗ILD在儿童，包括氧治疗，药物治疗和其他治疗，考虑到现有的专家共识，进行了特点。

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来源期刊

Pediatriya - Zhurnal im G.N. Speranskogo Medicine-Pediatrics, Perinatology and Child Health

CiteScore

0.60

自引率

0.00%

发文量

150

期刊介绍： Journal “Pediatria” named after G.N. Speransky (the official short names of the Journal are “Journal «Pediatria»,” “Pediatria,” and “«Pediatria,» the Journal”) is the oldest Soviet-and-Russian (in the Russian Federation, the CIS and former Soviet Union) scientific and practical medical periodical assigned for pediatricians that is published continuously since May, 1922, and distributed worldwide. Our mission statement specifies that we aim to the ‘raising the level of skills and education of pediatricians, organizers of children’s health protection services, medicine scientists, lecturers and students of medical institutes for higher education, universities and colleges worldwide with an emphasis on Russian-speaking audience and specific, topical problems of children’s healthcare in Russia, the CIS, Baltic States and former Soviet Union Countries and their determination with the use of the World’s best practices in pediatrics.’ As part of this objective, the Editorial of the Journal «Pediatria» named after G.N. Speransky itself adopts a neutral position on issues treated within the Journal. The Journal serves to further academic discussions of topics, irrespective of their nature - whether religious, racial-, gender-based, environmental, ethical, political or other potentially or topically contentious subjects. The Journal is registered with the ISSN, - the international identifier for serials and other continuing resources, in the electronic and print world: ISSN 0031-403X (Print), and ISSN 1990-2182 (Online). The Journal was founded by the Academician, Dr. Georgiy Nestorovich SPERANSKY, in May, 1922. Now (since 1973) the Journal bears his honorary name.