Pub Date : 2023-05-01DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5474
S. Karandashova, N. Ly
{"title":"Interstitial Lung Disease in a Patient Heterozygous for Two Previously Undescribed VUS in SFPTC","authors":"S. Karandashova, N. Ly","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5474","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5474","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"82 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116311977","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-05-01DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5476
J. Ni, J. Cameron, R. Hopper, S. Tan, X. Si
{"title":"A Rare Case of Interstitial Lung Disease and Pulmonary Hypertension Associated With NKX2-1 Mutation","authors":"J. Ni, J. Cameron, R. Hopper, S. Tan, X. Si","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5476","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5476","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"3 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115265418","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-05-01DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5477
L. A. García Bonilla, J. Chiang
{"title":"Pulmonary Hemorrhage and Massive Air-leak: An Atypical Presentation for Pulmonary Interstitial Glycogenosis","authors":"L. A. García Bonilla, J. Chiang","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5477","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5477","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"19 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123703720","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-05-01DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5481
J. Kennedy, S. Vargas, M. Fishman, C. Garcia de Alba Rivas, S. Baek, N. Alesi, N. Carmichael, A. Casey, D. Khabibullin, L. Henderson, A. Wehrman, L. Collen, B. Raby
{"title":"Low Serum Progranulin Levels as a Biomarker in the First Reported Case of Progranulin (GRN) Variant Associated Fibrotic Lung and Liver Disease","authors":"J. Kennedy, S. Vargas, M. Fishman, C. Garcia de Alba Rivas, S. Baek, N. Alesi, N. Carmichael, A. Casey, D. Khabibullin, L. Henderson, A. Wehrman, L. Collen, B. Raby","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5481","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5481","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"104 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122549191","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-05-01DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5479
C. Mertens, G. B. Beltran Ale
{"title":"Miliary Pattern Chest Imaging Presentation of COPA Syndrome in a Pediatric Patient","authors":"C. Mertens, G. B. Beltran Ale","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5479","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5479","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"3 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"131255041","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-05-01DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5467
L. Feld, Z. Li, M. Josephson, J. Rice, D. Camburn, Y. Li, S. McGrath-Morrow, L. Young
{"title":"Healthcare Utilization in Childhood Interstitial Lung Disease: A Report From a Major Tertiary Care Center","authors":"L. Feld, Z. Li, M. Josephson, J. Rice, D. Camburn, Y. Li, S. McGrath-Morrow, L. Young","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5467","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5467","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"129 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133633168","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-05-01DOI: 10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5465
T. M. Maher, K. Brown, S. Cunningham, E. DeBoer, R. Deterding, E. Fiorino, M. Griese, N. Schwerk, D. Warburton, L. Young, M. Gahlemann, F. Voß, C. Stock, on behalf of the InPedILD trial investigators
{"title":"Estimating the Effect of Nintedanib on Forced Vital Capacity in Children and Adolescents With Fibrosing Interstitial Lung Disease: Extrapolation Using a Bayesian Borrowing Approach","authors":"T. M. Maher, K. Brown, S. Cunningham, E. DeBoer, R. Deterding, E. Fiorino, M. Griese, N. Schwerk, D. Warburton, L. Young, M. Gahlemann, F. Voß, C. Stock, on behalf of the InPedILD trial investigators","doi":"10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5465","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2023.207.1_meetingabstracts.a5465","url":null,"abstract":"","PeriodicalId":135744,"journal":{"name":"C60. CHILDHOOD INTERSTITIAL LUNG DISEASE (chILD)","volume":"40 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2023-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115938399","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}