Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.oa178
A. Bosacoma, D. Aguilar, Agustín Huete García, I. Blanco, C. Martín-Ontiyuelo, A. Ramírez, Y. Roger, J. Osorio, O. Tura-Ceide, V. Peinado, J. Barberà
{"title":"Selection of a gene panel related to pulmonary hypertension associated with respiratory diseases","authors":"A. Bosacoma, D. Aguilar, Agustín Huete García, I. Blanco, C. Martín-Ontiyuelo, A. Ramírez, Y. Roger, J. Osorio, O. Tura-Ceide, V. Peinado, J. Barberà","doi":"10.1183/13993003.congress-2021.oa178","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.oa178","url":null,"abstract":"","PeriodicalId":20724,"journal":{"name":"Pulmonary hypertension","volume":"96 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"83994333","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa1918
J. Klinger, R. Benza, Sung-A Chang, H. Ghofrani, M. Hoeper, P. Jansa, J. Ota-Arakaki, S. Rosenkranz, G. Simonneau, C. Vizza, A. Vonk-Noordegraaf, V. McLaughlin
{"title":"Switching from PDE5i to riociguat in patients with PAH: A responder analysis from REPLACE","authors":"J. Klinger, R. Benza, Sung-A Chang, H. Ghofrani, M. Hoeper, P. Jansa, J. Ota-Arakaki, S. Rosenkranz, G. Simonneau, C. Vizza, A. Vonk-Noordegraaf, V. McLaughlin","doi":"10.1183/13993003.congress-2021.pa1918","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa1918","url":null,"abstract":"","PeriodicalId":20724,"journal":{"name":"Pulmonary hypertension","volume":"39 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"83137708","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa587
V. Theobald, E. Grünig, N. Benjamin, B. Egenlauf, H. Gall, A. Ghofrani, M. Halank, S. Harutyunova, M. Hoeper, D. Jonigk, M. Schneider, H. Seyfarth, S. Richtmann, P. Xanthouli, M. Muckenthaler, C. Eichstaedt
{"title":"BMPR2 mutations and iron metabolism in pulmonary arterial hypertension patients","authors":"V. Theobald, E. Grünig, N. Benjamin, B. Egenlauf, H. Gall, A. Ghofrani, M. Halank, S. Harutyunova, M. Hoeper, D. Jonigk, M. Schneider, H. Seyfarth, S. Richtmann, P. Xanthouli, M. Muckenthaler, C. Eichstaedt","doi":"10.1183/13993003.congress-2021.pa587","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa587","url":null,"abstract":"","PeriodicalId":20724,"journal":{"name":"Pulmonary hypertension","volume":"11 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"87956675","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa590
A. Bosacoma, D. Aguilar, Tanja Paul, I. Blanco, O. Tura-Ceide, J. Barberà, V. Peinado
{"title":"Soluble guanylate cyclase stimulators revert in vitro cigarette smoke effects through JNK pathway normalization","authors":"A. Bosacoma, D. Aguilar, Tanja Paul, I. Blanco, O. Tura-Ceide, J. Barberà, V. Peinado","doi":"10.1183/13993003.congress-2021.pa590","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa590","url":null,"abstract":"","PeriodicalId":20724,"journal":{"name":"Pulmonary hypertension","volume":"6 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"88364868","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa3597
R. Tyagi, S. Kant, A. Wakhlu, A. Parihar, A. Pradhan, R. Jaiswal
{"title":"Spectrum of interstitial lung diseases (ILDs) and associated prevalence of pulmonary hypertension","authors":"R. Tyagi, S. Kant, A. Wakhlu, A. Parihar, A. Pradhan, R. Jaiswal","doi":"10.1183/13993003.congress-2021.pa3597","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3597","url":null,"abstract":"","PeriodicalId":20724,"journal":{"name":"Pulmonary hypertension","volume":"52 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"91117515","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa3594
P. Appenzeller, M. Lichtblau, C. Berlier, J. Aubert, A. Azzola, J. Fellrath, T. Geiser, F. Lador, S. Pohle, I. Opitz, M. Schwerzmann, H. Stricker, M. Tamm, S. Saxer, S. Ulrich
{"title":"The changing epidemiology of pulmonary hypertension: disease characteristics and clinical outcome over two decades of the swiss registry","authors":"P. Appenzeller, M. Lichtblau, C. Berlier, J. Aubert, A. Azzola, J. Fellrath, T. Geiser, F. Lador, S. Pohle, I. Opitz, M. Schwerzmann, H. Stricker, M. Tamm, S. Saxer, S. Ulrich","doi":"10.1183/13993003.congress-2021.pa3594","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3594","url":null,"abstract":"","PeriodicalId":20724,"journal":{"name":"Pulmonary hypertension","volume":"28 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"74825356","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa3590
I. Armstrong, C. Billings, Shaun Clayton, D. Kiely, J. Sephton, John Smith, Mary Ferguson
{"title":"The lived experiences of people shielding with pulmonary hypertension during the first wave of the COVID-19 pandemic","authors":"I. Armstrong, C. Billings, Shaun Clayton, D. Kiely, J. Sephton, John Smith, Mary Ferguson","doi":"10.1183/13993003.congress-2021.pa3590","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3590","url":null,"abstract":"","PeriodicalId":20724,"journal":{"name":"Pulmonary hypertension","volume":"8 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"75334641","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa1922
S. Saxer, L-R Calendo, M. Lichtblau, J. Müller, A. Carta, F. Gautschi, C. Berlier, E. Schwarz, K. Bloch, M. Greutmann, S. Ulrich
{"title":"Effect of short-term oxygen therapy on exercise performance in patients with cyanotic congenital heart disease","authors":"S. Saxer, L-R Calendo, M. Lichtblau, J. Müller, A. Carta, F. Gautschi, C. Berlier, E. Schwarz, K. Bloch, M. Greutmann, S. Ulrich","doi":"10.1183/13993003.congress-2021.pa1922","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa1922","url":null,"abstract":"","PeriodicalId":20724,"journal":{"name":"Pulmonary hypertension","volume":"36 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"80150079","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.pa591
T. Jujo, Yumiko Ikubo, Koji Hosomi, A. Naito, Jonguk Park, Hiroki Shoji, Rika Suda, Ayumi Sekine, A. Shigeta, S. Sakao, N. Tanabe, K. Mizuguchi, J. Kunisawa, K. Tatsumi
{"title":"Altered gut microbiota in chronic thromboembolic pulmonary hypertension","authors":"T. Jujo, Yumiko Ikubo, Koji Hosomi, A. Naito, Jonguk Park, Hiroki Shoji, Rika Suda, Ayumi Sekine, A. Shigeta, S. Sakao, N. Tanabe, K. Mizuguchi, J. Kunisawa, K. Tatsumi","doi":"10.1183/13993003.congress-2021.pa591","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa591","url":null,"abstract":"","PeriodicalId":20724,"journal":{"name":"Pulmonary hypertension","volume":"91 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"82376840","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2021-09-05DOI: 10.1183/13993003.congress-2021.oa142
A. Martínez Meñaca, V. M. Mora Cuesta, J. M. Cifrián Martínez, J. Barberà, M. López Meseguer, Juan Antonio Domingo Morena, J. Rueda Soriano, S. Alcolea, F. P. Pastor Pérez, Pliar Escribano Subias
{"title":"Lack of agreement between the exercise variables to assess the risk in PAH","authors":"A. Martínez Meñaca, V. M. Mora Cuesta, J. M. Cifrián Martínez, J. Barberà, M. López Meseguer, Juan Antonio Domingo Morena, J. Rueda Soriano, S. Alcolea, F. P. Pastor Pérez, Pliar Escribano Subias","doi":"10.1183/13993003.congress-2021.oa142","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.oa142","url":null,"abstract":"","PeriodicalId":20724,"journal":{"name":"Pulmonary hypertension","volume":"5 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"85206679","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}