E. B. Correia, Larissa Ventura Ribeiro Bruscky, Kelin Chen, Priscila Cestari Quagliato, Yoná Afonso Francisco, Liria Maria Daldoso Silva, A. C. D. S. Murta
{"title":"Taquicardia Ventricular Sustentada como Apresentação Isolada de Cardiomiopatia Amiloidótica por Transtirretina - Val50Met","authors":"E. B. Correia, Larissa Ventura Ribeiro Bruscky, Kelin Chen, Priscila Cestari Quagliato, Yoná Afonso Francisco, Liria Maria Daldoso Silva, A. C. D. S. Murta","doi":"10.36660/abchf.20210015","DOIUrl":"https://doi.org/10.36660/abchf.20210015","url":null,"abstract":"","PeriodicalId":277175,"journal":{"name":"ABC: Heart Failure & Cardiomyopathy","volume":"126 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115621376","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
C. Cafezeiro, A. Alencar, B. V. K. Bueno, J. H. Rissato, A. Dabarian, V. T. Hotta, F. Fernandes
{"title":"Familial Transthyretin Cardiac Amyloidosis with Homozygous Val122Ile Mutation Mimicking Hypertrophic Cardiomyopathy","authors":"C. Cafezeiro, A. Alencar, B. V. K. Bueno, J. H. Rissato, A. Dabarian, V. T. Hotta, F. Fernandes","doi":"10.36660/abchf.20210023","DOIUrl":"https://doi.org/10.36660/abchf.20210023","url":null,"abstract":"","PeriodicalId":277175,"journal":{"name":"ABC: Heart Failure & Cardiomyopathy","volume":"12 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133778646","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"ATTRv: a Multisystemic Disease Requires a Multiprofessional Approach","authors":"C. L. Moreira, Wilson Marques","doi":"10.36660/abchf.20210026","DOIUrl":"https://doi.org/10.36660/abchf.20210026","url":null,"abstract":"","PeriodicalId":277175,"journal":{"name":"ABC: Heart Failure & Cardiomyopathy","volume":"96 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115317673","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
In one of the first studies to demonstrate this application, Wizenberg et al. evaluated 10 consecutive patients with biopsy-confirmed CA, having observed that all patients exhibited intense and diffuse anomalous myocardial uptake on cardiac scintigraphy with 99mTc-pyrophosphate.2 However, later studies showed variable yield of these images in patients with different forms of CA, underscoring CA associated with immunoglobulin light chains (AL-CA), in addition to transthyretin-associated CA (ATTR-CA). The mechanisms by which bone radiotracers are accumulated in tissue deposits of amyloid protein probably involve the presence of microcalcifications in these protein aggregates, as these radiotracers are highly avid for calcium deposits. It is this aspect that also makes it possible for us to detect accumulation of these radiotracers in the hearts of patients with ischemic heart disease with recent acute myocardial infarction, and this was, historically, the first clinical application of this type of image.
{"title":"Cardiac Scintigraphy with Bone Markers in Clinical Practice: When to Solicit the Exam? How to Interpret the Results?","authors":"M. Simões","doi":"10.36660/abchf.20210022","DOIUrl":"https://doi.org/10.36660/abchf.20210022","url":null,"abstract":"In one of the first studies to demonstrate this application, Wizenberg et al. evaluated 10 consecutive patients with biopsy-confirmed CA, having observed that all patients exhibited intense and diffuse anomalous myocardial uptake on cardiac scintigraphy with 99mTc-pyrophosphate.2 However, later studies showed variable yield of these images in patients with different forms of CA, underscoring CA associated with immunoglobulin light chains (AL-CA), in addition to transthyretin-associated CA (ATTR-CA). The mechanisms by which bone radiotracers are accumulated in tissue deposits of amyloid protein probably involve the presence of microcalcifications in these protein aggregates, as these radiotracers are highly avid for calcium deposits. It is this aspect that also makes it possible for us to detect accumulation of these radiotracers in the hearts of patients with ischemic heart disease with recent acute myocardial infarction, and this was, historically, the first clinical application of this type of image.","PeriodicalId":277175,"journal":{"name":"ABC: Heart Failure & Cardiomyopathy","volume":"102 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122481941","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Algorithms for Cardiac Amyloidosis Diagnosis: How to apply them in practice? Luis E. Rohde1,2,3 Departamento de Medicina Interna, FAMED-UFRGS,1 Porto Alegre, RS – Brazil Programa de Insuficiência Cardíaca Avançada do Serviço de Cardiologia, Hospital de Clínicas de Porto Alegre,2 Porto Alegre, RS – Brazil Núcleo de Insuficiência Cardíaca e Cardiomiopatias do Serviço de Cardiologia, Hospital Moinhos de Vento,3 Porto Alegre, RS – Brazil
{"title":"Algorithms for Cardiac Amyloidosis Diagnosis: How to apply them in practice?","authors":"L. E. Rohde","doi":"10.36660/abchf.20210030","DOIUrl":"https://doi.org/10.36660/abchf.20210030","url":null,"abstract":"Algorithms for Cardiac Amyloidosis Diagnosis: How to apply them in practice? Luis E. Rohde1,2,3 Departamento de Medicina Interna, FAMED-UFRGS,1 Porto Alegre, RS – Brazil Programa de Insuficiência Cardíaca Avançada do Serviço de Cardiologia, Hospital de Clínicas de Porto Alegre,2 Porto Alegre, RS – Brazil Núcleo de Insuficiência Cardíaca e Cardiomiopatias do Serviço de Cardiologia, Hospital Moinhos de Vento,3 Porto Alegre, RS – Brazil","PeriodicalId":277175,"journal":{"name":"ABC: Heart Failure & Cardiomyopathy","volume":"19 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"131040750","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"ABPAR and the Needs of Patients with Amyloidosis in Brazil","authors":"Liana Cláudia Uriarte Ferronato","doi":"10.36660/abchf.20210018","DOIUrl":"https://doi.org/10.36660/abchf.20210018","url":null,"abstract":"","PeriodicalId":277175,"journal":{"name":"ABC: Heart Failure & Cardiomyopathy","volume":"21 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128050512","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Comprehensive Echocardiogram: What is it? For which Patients?","authors":"Marcelo Iorio Garcia","doi":"10.36660/abchf.20210017","DOIUrl":"https://doi.org/10.36660/abchf.20210017","url":null,"abstract":"","PeriodicalId":277175,"journal":{"name":"ABC: Heart Failure & Cardiomyopathy","volume":"9 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"130877522","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Ventricular Arrythmias in Cardiac Amyloidosis: It is Possible to Prevent Sudden Death?","authors":"Carlos A. Dumont, M. I. S. Liprandi","doi":"10.36660/abchf.20210035","DOIUrl":"https://doi.org/10.36660/abchf.20210035","url":null,"abstract":"","PeriodicalId":277175,"journal":{"name":"ABC: Heart Failure & Cardiomyopathy","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129020082","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"A Practical Approach to Differential Diagnosis of Cardiomyopathies with Infiltrative Phenotypes","authors":"L. Trevizan, S. Mangini","doi":"10.36660/abchf.20210036","DOIUrl":"https://doi.org/10.36660/abchf.20210036","url":null,"abstract":"","PeriodicalId":277175,"journal":{"name":"ABC: Heart Failure & Cardiomyopathy","volume":"40 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122022050","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Paulo Vinícius Ramos Souza, F. Fernandes, F. Ramires
{"title":"Genetic Testing in Amyloidosis: For Whom?","authors":"Paulo Vinícius Ramos Souza, F. Fernandes, F. Ramires","doi":"10.36660/abchf.20210025","DOIUrl":"https://doi.org/10.36660/abchf.20210025","url":null,"abstract":"","PeriodicalId":277175,"journal":{"name":"ABC: Heart Failure & Cardiomyopathy","volume":"10 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128085414","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}