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ABC: Heart Failure & Cardiomyopathy最新文献

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Taquicardia Ventricular Sustentada como Apresentação Isolada de Cardiomiopatia Amiloidótica por Transtirretina - Val50Met 经视网膜- Val50Met支持的单例淀粉样变心肌病的室性心动过速
Pub Date : 1900-01-01 DOI: 10.36660/abchf.20210015
E. B. Correia, Larissa Ventura Ribeiro Bruscky, Kelin Chen, Priscila Cestari Quagliato, Yoná Afonso Francisco, Liria Maria Daldoso Silva, A. C. D. S. Murta
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引用次数: 0
Familial Transthyretin Cardiac Amyloidosis with Homozygous Val122Ile Mutation Mimicking Hypertrophic Cardiomyopathy 模仿肥厚性心肌病的纯合Val122Ile突变的家族性转甲状腺素心脏淀粉样变性
Pub Date : 1900-01-01 DOI: 10.36660/abchf.20210023
C. Cafezeiro, A. Alencar, B. V. K. Bueno, J. H. Rissato, A. Dabarian, V. T. Hotta, F. Fernandes
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引用次数: 0
ATTRv: a Multisystemic Disease Requires a Multiprofessional Approach ATTRv:多系统疾病需要多专业方法
Pub Date : 1900-01-01 DOI: 10.36660/abchf.20210026
C. L. Moreira, Wilson Marques
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引用次数: 0
Cardiac Scintigraphy with Bone Markers in Clinical Practice: When to Solicit the Exam? How to Interpret the Results? 心脏闪烁成像与骨标记在临床实践中的应用:何时要求检查?如何解读调查结果?
Pub Date : 1900-01-01 DOI: 10.36660/abchf.20210022
M. Simões
In one of the first studies to demonstrate this application, Wizenberg et al. evaluated 10 consecutive patients with biopsy-confirmed CA, having observed that all patients exhibited intense and diffuse anomalous myocardial uptake on cardiac scintigraphy with 99mTc-pyrophosphate.2 However, later studies showed variable yield of these images in patients with different forms of CA, underscoring CA associated with immunoglobulin light chains (AL-CA), in addition to transthyretin-associated CA (ATTR-CA). The mechanisms by which bone radiotracers are accumulated in tissue deposits of amyloid protein probably involve the presence of microcalcifications in these protein aggregates, as these radiotracers are highly avid for calcium deposits. It is this aspect that also makes it possible for us to detect accumulation of these radiotracers in the hearts of patients with ischemic heart disease with recent acute myocardial infarction, and this was, historically, the first clinical application of this type of image.
在证明这一应用的首批研究之一中,Wizenberg等人评估了连续10例活检证实的CA患者,观察到所有患者在99mtc焦磷酸盐心脏显像上都表现出强烈和弥漫性异常心肌摄取然而,后来的研究显示,在不同形式的CA患者中,这些图像的产量是不同的,强调了与免疫球蛋白轻链(AL-CA)相关的CA,以及转甲状腺素相关的CA (atr -CA)。骨放射性示踪剂在淀粉样蛋白组织沉积物中积累的机制可能与这些蛋白质聚集体中存在微钙化有关,因为这些放射性示踪剂对钙沉积物非常敏感。这方面也使我们有可能检测到这些放射性示踪剂在缺血性心脏病患者的心脏中积累最近的急性心肌梗死,这是,历史上,这种类型的图像的第一次临床应用。
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引用次数: 0
Algorithms for Cardiac Amyloidosis Diagnosis: How to apply them in practice? 心脏淀粉样变的诊断算法:如何在实践中应用?
Pub Date : 1900-01-01 DOI: 10.36660/abchf.20210030
L. E. Rohde
Algorithms for Cardiac Amyloidosis Diagnosis: How to apply them in practice? Luis E. Rohde1,2,3 Departamento de Medicina Interna, FAMED-UFRGS,1 Porto Alegre, RS – Brazil Programa de Insuficiência Cardíaca Avançada do Serviço de Cardiologia, Hospital de Clínicas de Porto Alegre,2 Porto Alegre, RS – Brazil Núcleo de Insuficiência Cardíaca e Cardiomiopatias do Serviço de Cardiologia, Hospital Moinhos de Vento,3 Porto Alegre, RS – Brazil
心脏淀粉样变诊断算法:如何在实践中应用?路易斯·e·Rohde1内科部门,2,3,FAMED -UFRGS 1 RS—巴西的阿雷格里港项目的重度心力衰竭临床心血管、医院服务的阿雷格里港,2 RS—巴西的阿雷格里港核心心肌病心力衰竭和心脏的,医院的风车,3 RS—巴西的阿雷格里港
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引用次数: 0
ABPAR and the Needs of Patients with Amyloidosis in Brazil ABPAR与巴西淀粉样变性患者的需求
Pub Date : 1900-01-01 DOI: 10.36660/abchf.20210018
Liana Cláudia Uriarte Ferronato
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引用次数: 0
Comprehensive Echocardiogram: What is it? For which Patients? 综合超声心动图:是什么?针对哪些患者?
Pub Date : 1900-01-01 DOI: 10.36660/abchf.20210017
Marcelo Iorio Garcia
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引用次数: 0
Ventricular Arrythmias in Cardiac Amyloidosis: It is Possible to Prevent Sudden Death? 淀粉样变性患者室性心律失常:是否有可能预防猝死?
Pub Date : 1900-01-01 DOI: 10.36660/abchf.20210035
Carlos A. Dumont, M. I. S. Liprandi
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引用次数: 1
A Practical Approach to Differential Diagnosis of Cardiomyopathies with Infiltrative Phenotypes 浸润型心肌病鉴别诊断的实用方法
Pub Date : 1900-01-01 DOI: 10.36660/abchf.20210036
L. Trevizan, S. Mangini
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引用次数: 0
Genetic Testing in Amyloidosis: For Whom? 淀粉样变性的基因检测:针对谁?
Pub Date : 1900-01-01 DOI: 10.36660/abchf.20210025
Paulo Vinícius Ramos Souza, F. Fernandes, F. Ramires
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引用次数: 0
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ABC: Heart Failure & Cardiomyopathy
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