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Cerebral Sinovenous Thrombosis in Neonates and Children. 新生儿和儿童脑静脉血栓形成。
Pub Date : 2016-03-01 DOI: 10.15844/pedneurbriefs-30-3-7
Melissa G Chung

Investigators from Erasmus University Hospital in Belgium and Gustave-Dron Hospital and Roger-Salengro Hospital in France studied the clinical and neuroradiologic characteristics of cerebral sinovenous thrombosis (CSVT) in neonates and children.

比利时Erasmus大学医院、法国Gustave-Dron医院和Roger-Salengro医院的研究人员研究了新生儿和儿童脑静脉血栓形成(CSVT)的临床和神经放射学特征。
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引用次数: 0
Guidelines for Corticosteroid use in Treatment of DMD. 皮质类固醇治疗DMD的指南。
Pub Date : 2016-03-01 DOI: 10.15844/pedneurbriefs-30-3-4
Vamshi K Rao

The guideline development subcommittee of the American Academy of Neurology has provided an update to the 2005 treatment guidelines for use of corticosteroids (CS) in Duchenne muscular dystrophy (DMD).

美国神经病学学会指南制定小组委员会更新了2005年治疗杜氏肌营养不良症(DMD)使用皮质类固醇(CS)的指南。
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引用次数: 2
Evidence for Resident Memory T cells in Rasmussen Encephalitis. 拉斯穆森脑炎存在常驻记忆T细胞的证据。
Pub Date : 2016-03-01 DOI: 10.15844/pedneurbriefs-30-3-5
Amer Khojah, Marisa Klein-Gitelman

Investigators from University of California Los Angeles studied the presence of different T cell subset population in the brain tissue of 7 patients with Rasmussen encephalitis, a rare neuroinflammatory disorder characterized by intractable seizures and usually associated with progressive hemi cerebral atrophy, who underwent brain surgery and compared them to patients with focal cortical dysplasia.

来自加州大学洛杉矶分校的研究人员研究了7例拉斯穆森脑炎患者脑组织中不同T细胞亚群的存在,拉斯穆森脑炎是一种罕见的神经炎性疾病,以难治性癫痫发作为特征,通常与进行性半脑萎缩有关,这些患者接受了脑部手术,并将其与局灶性皮质发育不良患者进行了比较。
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引用次数: 3
Levetiracetam for Pediatric Posttraumatic Seizure Prophylaxis. 左乙拉西坦用于儿童创伤后癫痫预防。
Pub Date : 2016-03-01 DOI: 10.15844/pedneurbriefs-30-3-1
Dragos A Nita, Cecil D Hahn

Investigators from Nationwide Children's Hospital performed an observational cohort study of early post-traumatic seizures (EPTS) among 34 children with moderate to severe traumatic brain injury (TBI) who received levetiracetam (LEV) prophylaxis following admission to their pediatric intensive care unit.

全国儿童医院的研究人员对34名中度至重度创伤性脑损伤(TBI)患儿进行了一项早期创伤后癫痫发作(EPTS)的观察性队列研究,这些患儿在进入儿科重症监护室后接受左乙拉西坦(LEV)预防治疗。
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引用次数: 4
Predicting Post-Concussion Symptom Risk in the ED. 预测急诊科脑震荡后症状风险。
Pub Date : 2016-03-01 DOI: 10.15844/pedneurbriefs-30-3-2
Anthony P Kontos, Jaime McAllister-Deitrick, Alicia M Sufrinko

Investigators from The Pediatric Emergency Research Canada (PERC) Concussion Team developed a clinical risk score for predicting persistent post-concussion symptoms (PPCS) at 28 days post injury in a large cohort of children initially evaluated at the emergency department (ED) within 48 hours of injury.

加拿大儿科急诊研究(PERC)脑震荡小组的研究人员开发了一种临床风险评分,用于预测损伤后28天持续脑震荡后症状(PPCS),该研究对受伤后48小时内在急诊科(ED)初步评估的大量儿童进行了评估。
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引用次数: 4
Predictive Power of EEG in Infants with Tuberous Sclerosis 脑电图对婴儿结节性硬化症的预测能力
Pub Date : 2016-02-01 DOI: 10.15844/pedneurbriefs-30-2-1
Molly Tracy
Investigators from University of California- Los Angeles and collaborators from across the country report on the use of prospective EEGs in infants with tuberous sclerosis complex (TSC) to predict evolution to seizures.
来自加州大学洛杉矶分校的研究人员和来自全国各地的合作者报告了在患有结节性硬化症(TSC)的婴儿中使用前瞻性脑电图来预测癫痫发作的演变。
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引用次数: 1
Language after Hemispherotomy in Rasmussen Syndrome 拉斯穆森综合征脑半球切除后的语言
Pub Date : 2016-02-01 DOI: 10.15844/pedneurbriefs-30-2-4
S. Varadkar, M. Tisdall
Investigators from Rothschild Foundation Hospital in Paris report language outcome in children after (left) dominant-hemisphere hemispherotomy for Rasmussen Syndrome.
来自巴黎罗斯柴尔德基金会医院的研究人员报告了拉斯穆森综合征(左)主脑半球切除术后儿童的语言预后。
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引用次数: 1
School-Aged Outcomes After Neonatal Arterial Ischemic Stroke 新生儿动脉缺血性卒中后学龄预后
Pub Date : 2016-02-01 DOI: 10.15844/pedneurbriefs-30-2-7
T. Czech, A. Pardo
Investigators from the Accident Vasculaire Cérébral de nouveau-né (AVCnn) Study Group, a multicenter registry in France, examined outcomes at 7 years of age in children previously identified with neonatal arterial ischemic stroke (NAIS).
来自法国一个多中心注册的意外血管病(AVCnn)研究小组的研究人员检查了7岁时被确诊为新生儿动脉缺血性中风(NAIS)的儿童的结果。
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引用次数: 2
Diffusion Tensor Imaging of Epileptogenic Lesions in TSC TSC中致痫性病变的弥散张量成像
Pub Date : 2016-02-01 DOI: 10.15844/pedneurbriefs-30-2-3
Divakar S. Mithal, Maura E. Ryan
Investigators from University of California Los Angeles, studied whether epileptogenic tubers in Tuberous Sclerosis Complex (TSC) can be identified by diffusion tensor imaging (DTI).
来自加州大学洛杉矶分校的研究人员研究了是否可以通过扩散张量成像(DTI)识别结节性硬化症(TSC)的致痫性结节。
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引用次数: 0
Clinical and Molecular Characterization of ALG1-CDG ALG1-CDG的临床和分子特征
Pub Date : 2016-02-01 DOI: 10.15844/pedneurbriefs-30-2-5
R. Dhamija, Chelsea Chambers
Investigators from the Human Genetics Program, Sanford Burnham Prebys Medical Discovery Institute, La Jolla, California and a large study group utilized a combination of exome sequencing, targeted gene panels, and Sanger sequencing to identify thirty-one pathogenic variants in thirty-nine affected individuals with ALG1-CDG from 32 families.
来自加州拉霍亚市Sanford Burnham Prebys医学发现研究所人类遗传学项目的研究人员和一个大型研究小组利用外显子组测序、靶向基因面板和Sanger测序的组合,在来自32个家庭的39名患有ALG1-CDG的个体中鉴定了31种致病变异。
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引用次数: 1
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Pediatric Neurology Briefs
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