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A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE最新文献

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Dysregulation of Sphingolipid Metabolism in Pulmonary Lymphangioleiomyomatosis (LAM) 肺淋巴管平滑肌瘤病(LAM)中鞘脂代谢失调的研究
Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1428
Jane J. Yu, Xiangdong Liu, C. Li, L. Pitstick, A. Osterburg, N. Gupta, K. Wikenheiser-Brokamp, M. Borchers, J. Woods, F. McCormack, X. Zhao, M. Soleimani, K. Setchell
{"title":"Dysregulation of Sphingolipid Metabolism in Pulmonary Lymphangioleiomyomatosis (LAM)","authors":"Jane J. Yu, Xiangdong Liu, C. Li, L. Pitstick, A. Osterburg, N. Gupta, K. Wikenheiser-Brokamp, M. Borchers, J. Woods, F. McCormack, X. Zhao, M. Soleimani, K. Setchell","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1428","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1428","url":null,"abstract":"","PeriodicalId":325582,"journal":{"name":"A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE","volume":"10 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"126606557","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Single Center Experience of Lung transplantation for Lymphangioleiomyomatosis 单中心肺移植治疗淋巴管平滑肌瘤的体会
Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1413
J. Zhang
{"title":"Single Center Experience of Lung transplantation for Lymphangioleiomyomatosis","authors":"J. Zhang","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1413","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1413","url":null,"abstract":"","PeriodicalId":325582,"journal":{"name":"A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE","volume":"11 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133977369","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Change of Pulmonary Function Test in Patients with Tuberous Sclerosis Complex - Lymphangioleiomyomatosis (TSC-LAM) 结节性硬化症-淋巴管平滑肌瘤病(TSC-LAM)患者肺功能试验的变化
Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1416
Li-Chin Chen, Y. Kuo, Po-Hsiu Kuo, Huey-Dong Wu, H.-C. Wang
{"title":"Change of Pulmonary Function Test in Patients with Tuberous Sclerosis Complex - Lymphangioleiomyomatosis (TSC-LAM)","authors":"Li-Chin Chen, Y. Kuo, Po-Hsiu Kuo, Huey-Dong Wu, H.-C. Wang","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1416","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1416","url":null,"abstract":"","PeriodicalId":325582,"journal":{"name":"A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE","volume":"29 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122295760","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Exosomes Released from Lymphangioleiomyomatosis-Derived Smooth Muscle-Like Cells Mediate Endothelial Cell Apoptosis and Vascular Network Disruption 淋巴管平滑肌瘤衍生的平滑肌样细胞释放外泌体介导内皮细胞凋亡和血管网络破坏
Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1420
M. Ho, L. Julian, W. Stanford, D. Stewart
{"title":"Exosomes Released from Lymphangioleiomyomatosis-Derived Smooth Muscle-Like Cells Mediate Endothelial Cell Apoptosis and Vascular Network Disruption","authors":"M. Ho, L. Julian, W. Stanford, D. Stewart","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1420","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1420","url":null,"abstract":"","PeriodicalId":325582,"journal":{"name":"A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE","volume":"61 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"114307029","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
An Approach to Precision Medicine for Pulmonary Alveolar Proteinosis 肺泡蛋白沉积症的精准医学探讨
Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1417
Elinor Lee, Cormac McCarthy, J. Bridges, J. Woods, Takuji Suzuki, B. Carey, Tisha Wang, B. Trapnell, E. Tarling
{"title":"An Approach to Precision Medicine for Pulmonary Alveolar Proteinosis","authors":"Elinor Lee, Cormac McCarthy, J. Bridges, J. Woods, Takuji Suzuki, B. Carey, Tisha Wang, B. Trapnell, E. Tarling","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1417","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1417","url":null,"abstract":"","PeriodicalId":325582,"journal":{"name":"A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE","volume":"48 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116545129","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Thoracic Paravertebral Lesions in Patients with IgG4-Related Respiratory Disease igg4相关呼吸系统疾病患者的胸椎旁病变
Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1415
Shoko Matsui, S. Okazawa, K. Tokui, K. Kambara, S. Imanishi, Kazuki Shimokawa, Takahiro Hirai, M. Inomata, T. Miwa, Ryuji Hayashi, Kazuyuki Tobe
{"title":"Thoracic Paravertebral Lesions in Patients with IgG4-Related Respiratory Disease","authors":"Shoko Matsui, S. Okazawa, K. Tokui, K. Kambara, S. Imanishi, Kazuki Shimokawa, Takahiro Hirai, M. Inomata, T. Miwa, Ryuji Hayashi, Kazuyuki Tobe","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1415","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1415","url":null,"abstract":"","PeriodicalId":325582,"journal":{"name":"A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE","volume":"6 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"127972305","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Pulmonary Langerhans Cell Histiocytosis in Adults 成人肺朗格汉斯细胞组织细胞增多症
Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1423
E. Radzikowska, K. Błasińska-Przerwa, M. Je, kiewicz-Kopij, R. Langfort, M. Szo, kowska, Katarzyna Modrzewska, I. Bestry, M. Za, ska, J. Szopiński, E. Wiatr, K. Roszkowski
{"title":"Pulmonary Langerhans Cell Histiocytosis in Adults","authors":"E. Radzikowska, K. Błasińska-Przerwa, M. Je, kiewicz-Kopij, R. Langfort, M. Szo, kowska, Katarzyna Modrzewska, I. Bestry, M. Za, ska, J. Szopiński, E. Wiatr, K. Roszkowski","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1423","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1423","url":null,"abstract":"","PeriodicalId":325582,"journal":{"name":"A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE","volume":"17 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"134108086","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Serum VEGF-D Level in the Periods of Not Taking mTOR Inhibitors in the Patients with Lymphangioleiomyomatosis 淋巴管平滑肌瘤患者未服用mTOR抑制剂期间血清VEGF-D水平的变化
Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1419
M. Hirose, T. Arai, C. Sugimoto, T. Takimoto, Y. Inoue
{"title":"Serum VEGF-D Level in the Periods of Not Taking mTOR Inhibitors in the Patients with Lymphangioleiomyomatosis","authors":"M. Hirose, T. Arai, C. Sugimoto, T. Takimoto, Y. Inoue","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1419","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1419","url":null,"abstract":"","PeriodicalId":325582,"journal":{"name":"A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE","volume":"71 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123228532","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Proteomic Profiling of Serum Exosomes to Identify Novel Biomarkers for Lymphangioleiomyomatosis 血清外泌体的蛋白质组学分析鉴定淋巴管平滑肌瘤病的新生物标志物
Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1425
T. Takimoto, Y. Takeda, Takashi Shiromizu, Ryohei Narumi, T. Koba, M. Kuroyama, H. Kida, M. Hirose, Y. Inoue, T. Tomonaga, A. Kumanogoh
{"title":"Proteomic Profiling of Serum Exosomes to Identify Novel Biomarkers for Lymphangioleiomyomatosis","authors":"T. Takimoto, Y. Takeda, Takashi Shiromizu, Ryohei Narumi, T. Koba, M. Kuroyama, H. Kida, M. Hirose, Y. Inoue, T. Tomonaga, A. Kumanogoh","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1425","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1425","url":null,"abstract":"","PeriodicalId":325582,"journal":{"name":"A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE","volume":"38 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116315477","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Mast Cell Recruitment in Lymphangiomatosis and Lung Cystic Destruction; Opportunities for Drug Repurposing 肥大细胞在淋巴管瘤病和肺囊性破坏中的募集药物再利用的机会
Pub Date : 2019-05-01 DOI: 10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1421
R. Jadidi, A. Dongre, D. Clements, S. Miller, S. Johnson
{"title":"Mast Cell Recruitment in Lymphangiomatosis and Lung Cystic Destruction; Opportunities for Drug Repurposing","authors":"R. Jadidi, A. Dongre, D. Clements, S. Miller, S. Johnson","doi":"10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1421","DOIUrl":"https://doi.org/10.1164/ajrccm-conference.2019.199.1_meetingabstracts.a1421","url":null,"abstract":"","PeriodicalId":325582,"journal":{"name":"A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE","volume":"5 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2019-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"130557540","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
期刊
A36. RARE LUNG DISEASES FROM BENCH TO BEDSIDE
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