Kah Ann Ho, N. Fuentes-Bolanos, A. Gifford, A. Jiwane, D. Wanaguru
Background: Fetal Lung Interstitial Tumor (FLIT) is a rare benign lung tumor. There have been 18 cases of FLIT described in the literature. FLIT is characterized by a region of arrested lung development and must be differentiated from other congenital lung lesions with poorer prognoses. Case Presentation: We report the first two known cases of FLIT in Australia and New Zealand. In both cases, the patients developed respiratory distress at birth requiring intubation. Imaging revealed solid lesions and echocardiography demonstrated pulmonary hypertension. The patients underwent surgical resection without any complications or recurrence. Conclusion: FLIT is a rare benign congenital lung tumor that can be adequately managed with surgical resection.
{"title":"Fetal Lung Interstitial Tumor (FLIT): A case series","authors":"Kah Ann Ho, N. Fuentes-Bolanos, A. Gifford, A. Jiwane, D. Wanaguru","doi":"10.47338/jns.v12.1141","DOIUrl":"https://doi.org/10.47338/jns.v12.1141","url":null,"abstract":"Background: Fetal Lung Interstitial Tumor (FLIT) is a rare benign lung tumor. There have been 18 cases of FLIT described in the literature. FLIT is characterized by a region of arrested lung development and must be differentiated from other congenital lung lesions with poorer prognoses.\u0000Case Presentation: We report the first two known cases of FLIT in Australia and New Zealand. In both cases, the patients developed respiratory distress at birth requiring intubation. Imaging revealed solid lesions and echocardiography demonstrated pulmonary hypertension. The patients underwent surgical resection without any complications or recurrence.\u0000Conclusion: FLIT is a rare benign congenital lung tumor that can be adequately managed with surgical resection.","PeriodicalId":34201,"journal":{"name":"Journal of Neonatal Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-01-03","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"43707033","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Background: Because of the high rates of Broviac catheter complications, we started an urgent quality process to reduce this morbidity. The aim is to assess the efficiency of the main actions we have taken in enhancing our practice and improving Broviac outcomes. Methods: We included all neonates and young infants requiring surgical central venous access using a Broviac tunneled catheter. We compared the catheters’ outcomes before and after the implementation of a quality program based on a nurse teaching program, patient selection, and catheter management multidisciplinary protocol. The significance threshold was set at p<0.05. Results: We included 94 patients: 51 in the protocol group and 43 in the control group. The complication rate was reduced from 60.3% to 25.5% with p=0.001. The lifetime of the catheter was improved from 11.3 ± 4.3 days to 19.1 ± 9 days with p=0.007. The catheter infection was reduced from 65.3% to 46.1% with p≤0.001. Conclusion: This quality improvement project shows the utility of a quality assurance program based on careful indications and patient selection, a nursing teaching program, and a multidisciplinary catheter management protocol, in reducing Broviac catheter-related morbidity.
{"title":"Improvement of Broviac catheter-related outcomes after the implementation of a quality management system: A before-and-after prospective observational study","authors":"Manel Kammoun, A. Jarraya, S. Ammar, K. Kolsi","doi":"10.47338/jns.v12.1156","DOIUrl":"https://doi.org/10.47338/jns.v12.1156","url":null,"abstract":"Background: Because of the high rates of Broviac catheter complications, we started an urgent quality process to reduce this morbidity. The aim is to assess the efficiency of the main actions we have taken in enhancing our practice and improving Broviac outcomes.\u0000Methods: We included all neonates and young infants requiring surgical central venous access using a Broviac tunneled catheter. We compared the catheters’ outcomes before and after the implementation of a quality program based on a nurse teaching program, patient selection, and catheter management multidisciplinary protocol. The significance threshold was set at p<0.05.\u0000Results: We included 94 patients: 51 in the protocol group and 43 in the control group. The complication rate was reduced from 60.3% to 25.5% with p=0.001. The lifetime of the catheter was improved from 11.3 ± 4.3 days to 19.1 ± 9 days with p=0.007. The catheter infection was reduced from 65.3% to 46.1% with p≤0.001.\u0000Conclusion: This quality improvement project shows the utility of a quality assurance program based on careful indications and patient selection, a nursing teaching program, and a multidisciplinary catheter management protocol, in reducing Broviac catheter-related morbidity.","PeriodicalId":34201,"journal":{"name":"Journal of Neonatal Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-01-03","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"44520945","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"My journey with the Journal of Neonatal Surgery","authors":"Parveen Kumar","doi":"10.47338/jns.v11.1173","DOIUrl":"https://doi.org/10.47338/jns.v11.1173","url":null,"abstract":"","PeriodicalId":34201,"journal":{"name":"Journal of Neonatal Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2022-12-27","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"43550083","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
An 11-day-old male neonate delivered by C-section presented to the emergency department with the misdiagnosis of umbilical hernia. The physical examination found a hernia of the umbilical cord with a defect of 3cm, and a small non-reducible umbilical mass covered with a thick and opaque membrane. The newborn has no other physical anomalies. Laboratory tests were also within normal ranges. The abdominal US was poorly contributive, and the radiologist concluded that there is an intraperitoneal structure within the sac without anomalies of the hepato-biliary and urinary tracts.
{"title":"Hernia of umbilical cord containing gallbladder","authors":"Krioudj Samia, Samari Bilel Zakaria, Zineddine Soualili","doi":"10.47338/jns.v11.1124","DOIUrl":"https://doi.org/10.47338/jns.v11.1124","url":null,"abstract":"An 11-day-old male neonate delivered by C-section presented to the emergency department with the misdiagnosis of umbilical hernia. The physical examination found a hernia of the umbilical cord with a defect of 3cm, and a small non-reducible umbilical mass covered with a thick and opaque membrane. The newborn has no other physical anomalies. Laboratory tests were also within normal ranges. The abdominal US was poorly contributive, and the radiologist concluded that there is an intraperitoneal structure within the sac without anomalies of the hepato-biliary and urinary tracts.","PeriodicalId":34201,"journal":{"name":"Journal of Neonatal Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2022-12-12","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"45658062","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
D. K. Garnaik, Rajat Piplani, S. Tomar, P. Kothari
Background: Hirschsprung’s disease (HD) rarely co-occurs with anorectal malformation (ARM). If it occurs, the classical variety of HD is mostly associated. Total Colonic Aganglionosis (TCA) in a case with ARM is exceedingly rare. Case Presentation: A 3-day-old female neonate presented with neonatal intestinal obstruction. of such a rare association. Examination revealed a perineal fistula. A colostomy was formed for persistent abdominal distension, but it did not work properly. Re-exploration revealed TCA with a transition zone at the level of the terminal ileum. Conclusion: Though ARM is associated with several anomalies of various body systems, its association with TCA is exceedingly rare.
{"title":"Total colonic aganglionosis in a case of anorectal malformation: A case report","authors":"D. K. Garnaik, Rajat Piplani, S. Tomar, P. Kothari","doi":"10.47338/jns.v11.1100","DOIUrl":"https://doi.org/10.47338/jns.v11.1100","url":null,"abstract":"Background: Hirschsprung’s disease (HD) rarely co-occurs with anorectal malformation (ARM). If it occurs, the classical variety of HD is mostly associated. Total Colonic Aganglionosis (TCA) in a case with ARM is exceedingly rare.\u0000Case Presentation: A 3-day-old female neonate presented with neonatal intestinal obstruction. of such a rare association. Examination revealed a perineal fistula. A colostomy was formed for persistent abdominal distension, but it did not work properly. Re-exploration revealed TCA with a transition zone at the level of the terminal ileum.\u0000Conclusion: Though ARM is associated with several anomalies of various body systems, its association with TCA is exceedingly rare.","PeriodicalId":34201,"journal":{"name":"Journal of Neonatal Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2022-12-06","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"43106361","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Friemann-Dahl sign is the radiological appearance of three dense lines in the abdomen converging towards the left iliac fossa. It is caused by the apposing walls of the twisted sigmoid colon (sigmoid volvulus). [1] This appearance is also variously known as the ‘omega sign’, ‘bent inner-tube sign’, ‘horse-shoe sign’, ‘convergence sign’, or ‘coffee-bean sign’. Neuhauser’s sign is a soap-bubble like appearance in the right iliac fossa. It is caused by tiny air bubbles entrapped within the viscid meconium of cystic fibrosis. [2] Originally this sign was considered pathognomonic of meconium ileus; but subsequently, it was also reported in necrotizing enterocolitis, Hirschsprung disease, and anal stenosis. [3, 4] Concomitance of both the Friemann-Dahl’s sign and the Neuhauser’s sign in a neonate caused a diagnostic dilemma.
{"title":"Coexistence of ‘Friemann-Dahl sign’ and ‘Neuhauser’s sign’ in a newborn: A diagnostic dilemma","authors":"Venkatachalam Raveenthiran","doi":"10.47338/jns.v11.1137","DOIUrl":"https://doi.org/10.47338/jns.v11.1137","url":null,"abstract":"Friemann-Dahl sign is the radiological appearance of three dense lines in the abdomen converging towards the left iliac fossa. It is caused by the apposing walls of the twisted sigmoid colon (sigmoid volvulus). [1] This appearance is also variously known as the ‘omega sign’, ‘bent inner-tube sign’, ‘horse-shoe sign’, ‘convergence sign’, or ‘coffee-bean sign’. Neuhauser’s sign is a soap-bubble like appearance in the right iliac fossa. It is caused by tiny air bubbles entrapped within the viscid meconium of cystic fibrosis. [2] Originally this sign was considered pathognomonic of meconium ileus; but subsequently, it was also reported in necrotizing enterocolitis, Hirschsprung disease, and anal stenosis. [3, 4] Concomitance of both the Friemann-Dahl’s sign and the Neuhauser’s sign in a neonate caused a diagnostic dilemma.","PeriodicalId":34201,"journal":{"name":"Journal of Neonatal Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2022-12-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"46283649","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Background: A neural tube defect is a common congenital malformation and it commonly presents as an isolated cystic swelling on the back, anywhere from occiput to sacrum. However, multiple neural tube defects are rare with less than 100 cases reported worldwide. Case Presentation: We are reporting two cases of multiple neural tube defects that presented in the newborn period with a history of concurrent swellings along the midline on the back. They were evaluated with ultrasonography and the diagnosis of double meningomyelocele was confirmed. Subsequently, they were operated on, both the lesions were excised, and the defects were repaired simultaneously. Conclusion: Double meningomyelocele is a rare form of neural tube defect. Due to its rarity, exact embryogenesis is not known and thus, there is a need for further study on its embryology.
{"title":"Double meningomyelocele - a rare variant of neural tube defect: A case series","authors":"Md Mokarram Ali, Y. Kadian","doi":"10.47338/jns.v11.1126","DOIUrl":"https://doi.org/10.47338/jns.v11.1126","url":null,"abstract":"Background: A neural tube defect is a common congenital malformation and it commonly presents as an isolated cystic swelling on the back, anywhere from occiput to sacrum. However, multiple neural tube defects are rare with less than 100 cases reported worldwide.\u0000Case Presentation: We are reporting two cases of multiple neural tube defects that presented in the newborn period with a history of concurrent swellings along the midline on the back. They were evaluated with ultrasonography and the diagnosis of double meningomyelocele was confirmed. Subsequently, they were operated on, both the lesions were excised, and the defects were repaired simultaneously.\u0000Conclusion: Double meningomyelocele is a rare form of neural tube defect. Due to its rarity, exact embryogenesis is not known and thus, there is a need for further study on its embryology.","PeriodicalId":34201,"journal":{"name":"Journal of Neonatal Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2022-11-29","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"42410852","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Sengua Koipapi, D. Msuya, Joshua Tadayo, J. Lodhia
A 16-day-old male neonate was referred with
一名16天大的男性新生儿被转诊为
{"title":"Idiopathic congenital lymphedema in a neonate","authors":"Sengua Koipapi, D. Msuya, Joshua Tadayo, J. Lodhia","doi":"10.47338/jns.v11.1140","DOIUrl":"https://doi.org/10.47338/jns.v11.1140","url":null,"abstract":"A 16-day-old male neonate was referred with","PeriodicalId":34201,"journal":{"name":"Journal of Neonatal Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2022-11-27","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"47041325","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Background: Hamartomas are developmental tumor-like malformations, comprising a mixture of cytologically mature tissues that are indigenous to their anatomical location. Within the oral cavity, these lesions are usually multifocal, relatively small, and asymptomatic, and have been frequently linked to present as a manifestation of the oro-facial-digital-syndrome. Case Presentation: A 2-day-old female newborn was referred with two masses protruding from the oral cavity, feeding difficulties, and dribbling of milk during feeding. The patient had no dysmorphic features and no obvious associated anomalies. On careful examination, there was one mass protruding from the undersurface of a bifid tongue with another larger mass that seemed to originate from the hard palate. Complete surgical excision of both masses and repair of the bifid tongue were done to relieve the baby’s feeding difficulties. Histopathological examination of both specimens confirmed the diagnosis of multiple hamartomas. Conclusion: The occurrence of multiple and large oral hamartomas in newborns might result in feeding difficulties that necessitate urgent surgical intervention. The association of lingual and palatal hamartomas, with bifid tongue and cleft palate, is a unique observation that is not reported in the English literature.
{"title":"Multiple hamartomas of the oral cavity with bifid tongue and cleft palate: A unique observation","authors":"M. Hassan","doi":"10.47338/jns.v11.1144","DOIUrl":"https://doi.org/10.47338/jns.v11.1144","url":null,"abstract":"Background: Hamartomas are developmental tumor-like malformations, comprising a mixture of cytologically mature tissues that are indigenous to their anatomical location. Within the oral cavity, these lesions are usually multifocal, relatively small, and asymptomatic, and have been frequently linked to present as a manifestation of the oro-facial-digital-syndrome.\u0000Case Presentation: A 2-day-old female newborn was referred with two masses protruding from the oral cavity, feeding difficulties, and dribbling of milk during feeding. The patient had no dysmorphic features and no obvious associated anomalies. On careful examination, there was one mass protruding from the undersurface of a bifid tongue with another larger mass that seemed to originate from the hard palate. Complete surgical excision of both masses and repair of the bifid tongue were done to relieve the baby’s feeding difficulties. Histopathological examination of both specimens confirmed the diagnosis of multiple hamartomas.\u0000Conclusion: The occurrence of multiple and large oral hamartomas in newborns might result in feeding difficulties that necessitate urgent surgical intervention. The association of lingual and palatal hamartomas, with bifid tongue and cleft palate, is a unique observation that is not reported in the English literature.","PeriodicalId":34201,"journal":{"name":"Journal of Neonatal Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2022-11-25","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"41981096","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
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