首页 > 最新文献

Annals of Pediatric Surgery最新文献

英文 中文
Corporeal derotation for the management of dorsal penile curvature associated with epispadias or bladder exstrophy 治疗伴有尿道外翻或膀胱萎缩的阴茎背侧弯曲的体外剥离术
IF 0.4 Q4 PEDIATRICS Pub Date : 2024-07-20 DOI: 10.21608/apsj.2024.276769.1098
Mazen Kurdi
{"title":"Corporeal derotation for the management of dorsal penile curvature associated with epispadias or bladder exstrophy","authors":"Mazen Kurdi","doi":"10.21608/apsj.2024.276769.1098","DOIUrl":"https://doi.org/10.21608/apsj.2024.276769.1098","url":null,"abstract":"","PeriodicalId":43372,"journal":{"name":"Annals of Pediatric Surgery","volume":null,"pages":null},"PeriodicalIF":0.4,"publicationDate":"2024-07-20","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"141820185","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Validation of the Indonesian version of the thyroid cancer-specific quality of life as a tool to assess the quality of life among pediatric thyroid cancer patients 验证印尼版甲状腺癌生活质量表,将其作为评估小儿甲状腺癌患者生活质量的工具
IF 0.4 Q4 Medicine Pub Date : 2023-12-12 DOI: 10.1186/s43159-023-00278-4
Yohana Azhar, Dimyati Achmad, Reno Rudiman, Valeska Siulinda Candrawinata
Diagnosis and management of pediatric cancer develop a major life event that might impact psychosocial functioning and quality of life (QoL) even long after the initial therapy has been completed. Treatment outcomes have been measured in terms of survival time, but they also significantly impact survivors’ quality of life. The pediatric differentiated thyroid carcinoma survivors’ QoL has rarely been evaluated. This study aims to translate and validate the Indonesian version of the ThYCA-QoL questionnaire. The median age of 105 eligible survivors was 20.88 years old. Eighty percent of the survivors were female, were married or in a relationship (86.7%), and had paid jobs or were full-time students (71.7%). The median follow-up time was 64.82 months. Cronbach-α co-efficient was > 0.70 for psychological, concentration, throat, and mouth problems. For sympathetic, neuromuscular, voice, and sensory, the scores were < 0.70, where a multi-trait scaling analysis showed that all item correlations were > 0.40. Validity was assessed using the Pearson correlation coefficient for y-QoL with r > 0.60 and p < 0.01. The Indonesian ThYCA-QoL questionnaire is a reliable and valid tool to evaluate pediatric patients’ QoL after treatment. This simple assessment tool can be used to evaluate and manage pediatric thyroid cancer patients’ HRQoL.
小儿癌症的诊断和治疗是人生中的一件大事,即使在最初的治疗结束后很长时间,也可能会对心理社会功能和生活质量(QoL)产生影响。治疗结果以存活时间来衡量,但也会对幸存者的生活质量产生重大影响。小儿分化型甲状腺癌幸存者的生活质量很少得到评估。本研究旨在翻译和验证印尼版的ThYCA-QoL问卷。105名符合条件的幸存者的中位年龄为20.88岁。80%的幸存者为女性,已婚或有伴侣(86.7%),有带薪工作或为全日制学生(71.7%)。随访时间的中位数为 64.82 个月。心理、注意力、咽喉和口腔问题的 Cronbach-α 系数大于 0.70。交感神经、神经肌肉、嗓音和感觉问题的 Cronbach-α 系数小于 0.70,而多特质比例分析表明所有项目的相关性均大于 0.40。使用皮尔逊相关系数评估 y-QoL 的有效性,r > 0.60,p < 0.01。印尼 ThYCA QoL 问卷是评估儿科患者治疗后 QoL 的可靠有效工具。这一简单的评估工具可用于评估和管理小儿甲状腺癌患者的 HRQoL。
{"title":"Validation of the Indonesian version of the thyroid cancer-specific quality of life as a tool to assess the quality of life among pediatric thyroid cancer patients","authors":"Yohana Azhar, Dimyati Achmad, Reno Rudiman, Valeska Siulinda Candrawinata","doi":"10.1186/s43159-023-00278-4","DOIUrl":"https://doi.org/10.1186/s43159-023-00278-4","url":null,"abstract":"Diagnosis and management of pediatric cancer develop a major life event that might impact psychosocial functioning and quality of life (QoL) even long after the initial therapy has been completed. Treatment outcomes have been measured in terms of survival time, but they also significantly impact survivors’ quality of life. The pediatric differentiated thyroid carcinoma survivors’ QoL has rarely been evaluated. This study aims to translate and validate the Indonesian version of the ThYCA-QoL questionnaire. The median age of 105 eligible survivors was 20.88 years old. Eighty percent of the survivors were female, were married or in a relationship (86.7%), and had paid jobs or were full-time students (71.7%). The median follow-up time was 64.82 months. Cronbach-α co-efficient was > 0.70 for psychological, concentration, throat, and mouth problems. For sympathetic, neuromuscular, voice, and sensory, the scores were < 0.70, where a multi-trait scaling analysis showed that all item correlations were > 0.40. Validity was assessed using the Pearson correlation coefficient for y-QoL with r > 0.60 and p < 0.01. The Indonesian ThYCA-QoL questionnaire is a reliable and valid tool to evaluate pediatric patients’ QoL after treatment. This simple assessment tool can be used to evaluate and manage pediatric thyroid cancer patients’ HRQoL.","PeriodicalId":43372,"journal":{"name":"Annals of Pediatric Surgery","volume":null,"pages":null},"PeriodicalIF":0.4,"publicationDate":"2023-12-12","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"138574726","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Non-hypertrophic gastric outlet obstruction in the paediatric population: a case series with focus on management 儿科非肥厚性胃出口梗阻:以管理为重点的系列病例
IF 0.4 Q4 Medicine Pub Date : 2023-12-11 DOI: 10.1186/s43159-023-00277-5
Naser El-Mefleh, Muhammad Eyad Ba’Ath
Non-hypertrophic gastric outlet obstruction (GOO) in children is rare and usually presents beyond infancy. Aetiology is variable, and management is not well established due to its rarity. We aimed to conduct a descriptive study of these cases within our geographic area. It is a retrospective chart review of all children with non-hypertrophic gastric outlet obstruction presenting to three hospitals in northwest Syria during the period 2019–2023. Demographics, presentation, and management data were extracted. Twelve cases were identified, eight males, with age range 1–12 years and follow-up range 3–42 months. Eight patients had a history drinking battery acid and one with ingestion of high-dose ibuprofen. The other three had no clear aetiology. Five patients improved by endoscopic balloon dilatations (EBD), and seven needed surgeries. All those who had successful EBD were treated within 3 weeks of ingestion. Non-hypertrophic GOO in children is rare and mostly related to caustic material ingestion. Treatment by endoscopic balloon dilatation is likely to be successful if done within 3 weeks from caustic ingestion. After that period, often surgery is needed.
儿童非肥厚性胃出口梗阻(GOO)非常罕见,通常在婴儿期以后才出现。病因多变,由于其罕见性,治疗方法尚未得到很好的确定。我们旨在对本地区的此类病例进行描述性研究。这是一项回顾性病历审查,涉及 2019-2023 年期间在叙利亚西北部三家医院就诊的所有非肥厚性胃出口梗阻患儿。我们提取了人口统计学、发病情况和管理数据。共发现 12 例病例,其中 8 例为男性,年龄范围为 1-12 岁,随访时间范围为 3-42 个月。八名患者有饮用电池酸的病史,一名患者摄入了大剂量布洛芬。另外三名患者病因不明。五名患者通过内窥镜球囊扩张术(EBD)有所好转,七名患者需要进行手术。所有成功实施内镜下球囊扩张术的患者都是在摄入后3周内接受治疗的。儿童非肥厚性 GOO 很少见,大多与摄入腐蚀性物质有关。如果在摄入腐蚀性物质后三周内进行内窥镜球囊扩张术,治疗很可能会成功。在此之后,通常需要进行手术治疗。
{"title":"Non-hypertrophic gastric outlet obstruction in the paediatric population: a case series with focus on management","authors":"Naser El-Mefleh, Muhammad Eyad Ba’Ath","doi":"10.1186/s43159-023-00277-5","DOIUrl":"https://doi.org/10.1186/s43159-023-00277-5","url":null,"abstract":"Non-hypertrophic gastric outlet obstruction (GOO) in children is rare and usually presents beyond infancy. Aetiology is variable, and management is not well established due to its rarity. We aimed to conduct a descriptive study of these cases within our geographic area. It is a retrospective chart review of all children with non-hypertrophic gastric outlet obstruction presenting to three hospitals in northwest Syria during the period 2019–2023. Demographics, presentation, and management data were extracted. Twelve cases were identified, eight males, with age range 1–12 years and follow-up range 3–42 months. Eight patients had a history drinking battery acid and one with ingestion of high-dose ibuprofen. The other three had no clear aetiology. Five patients improved by endoscopic balloon dilatations (EBD), and seven needed surgeries. All those who had successful EBD were treated within 3 weeks of ingestion. Non-hypertrophic GOO in children is rare and mostly related to caustic material ingestion. Treatment by endoscopic balloon dilatation is likely to be successful if done within 3 weeks from caustic ingestion. After that period, often surgery is needed.","PeriodicalId":43372,"journal":{"name":"Annals of Pediatric Surgery","volume":null,"pages":null},"PeriodicalIF":0.4,"publicationDate":"2023-12-11","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"138568884","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Epidemiologic factors associated with neonatal bowel perforations in Uganda: experience from a single tertiary referral hospital 与乌干达新生儿肠穿孔相关的流行病学因素:来自单一三级转诊医院的经验
IF 0.4 Q4 Medicine Pub Date : 2023-12-05 DOI: 10.1186/s43159-023-00275-7
Innocent Okello, Nasser Kakembo, Phyllis Kisa, Stella Nimanya, Caroline Q. Stephens, Ava Yap, Anne S. Wesonga, Rovine Naluyimbazi, John Sekabira
Neonatal bowel perforations pose a significant disease burden for pediatric surgeons around the world. However, very little is known about these perforations in low-income settings. This study aims to investigate the epidemiology of neonatal perforations at a tertiary hospital in Uganda. Twenty neonates with bowel perforation who were admitted to a single national referral hospital from May 2020 to April 2021 were included. Fifty-five percent (n = 11) of the neonates in this cohort were male, and 16 were term with birth weight above 2.5 kg. Thirteen were below 1 week of age and all maternal ages were less than 40 years. Pneumoperitoneum was the most common finding on erect abdominal X-ray and colon was the frequent site of perforation. Forty percent of the babies in this cohort had blood group O+. Fifty-five percent of our patients died before discharge. Outcomes for neonatal bowel perforations are still dismal. Health workers taking care of neonates should have a high index of suspicion for neonatal gastrointestinal perforations.
新生儿肠穿孔对全世界的儿科外科医生来说是一个重大的疾病负担。然而,人们对低收入地区的穿孔情况知之甚少。本研究的目的是调查流行病学的新生儿穿孔在乌干达三级医院。纳入了2020年5月至2021年4月在一家国家转诊医院住院的20名肠穿孔新生儿。该队列中55% (n = 11)的新生儿为男性,16例足月出生体重超过2.5 kg。13例小于1周龄,产妇年龄均小于40岁。气腹是腹部直立x线片最常见的发现,结肠是最常见的穿孔部位。这个队列中40%的婴儿是O+型血。55%的病人在出院前死亡。新生儿肠穿孔的结局仍然令人沮丧。照顾新生儿的卫生工作者应该高度怀疑新生儿胃肠道穿孔。
{"title":"Epidemiologic factors associated with neonatal bowel perforations in Uganda: experience from a single tertiary referral hospital","authors":"Innocent Okello, Nasser Kakembo, Phyllis Kisa, Stella Nimanya, Caroline Q. Stephens, Ava Yap, Anne S. Wesonga, Rovine Naluyimbazi, John Sekabira","doi":"10.1186/s43159-023-00275-7","DOIUrl":"https://doi.org/10.1186/s43159-023-00275-7","url":null,"abstract":"Neonatal bowel perforations pose a significant disease burden for pediatric surgeons around the world. However, very little is known about these perforations in low-income settings. This study aims to investigate the epidemiology of neonatal perforations at a tertiary hospital in Uganda. Twenty neonates with bowel perforation who were admitted to a single national referral hospital from May 2020 to April 2021 were included. Fifty-five percent (n = 11) of the neonates in this cohort were male, and 16 were term with birth weight above 2.5 kg. Thirteen were below 1 week of age and all maternal ages were less than 40 years. Pneumoperitoneum was the most common finding on erect abdominal X-ray and colon was the frequent site of perforation. Forty percent of the babies in this cohort had blood group O+. Fifty-five percent of our patients died before discharge. Outcomes for neonatal bowel perforations are still dismal. Health workers taking care of neonates should have a high index of suspicion for neonatal gastrointestinal perforations.","PeriodicalId":43372,"journal":{"name":"Annals of Pediatric Surgery","volume":null,"pages":null},"PeriodicalIF":0.4,"publicationDate":"2023-12-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"138536054","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Safety and efficacy of central line removal by guidewire extraction technique in children 儿童导丝拔除中心线的安全性和有效性
IF 0.4 Q4 Medicine Pub Date : 2023-12-05 DOI: 10.1186/s43159-023-00276-6
Mary Froehlich, Spencer Schulte, Shirong Chang, Alan Ikeda, Michael G. Scheidler
This study reviews a university pediatric surgery practice for the incidence of stuck subcutaneous port catheter (SSPC) removal and the efficacy of a guidewire extraction technique. We reviewed all central catheter removals between 2018 and 2020. A SSPC was defined as resistance to removal after dissection of the subcutaneous tissue with signs of impending device fracture. Details of the catheter duration, initial diagnosis, and medications administered through the device were all recorded. One hundred eight patients underwent catheter removal and six were defined as SSPCs. Catheter in situ time ranged from 35 to 96 months. All six patients underwent the guidewire extraction technique and were removed in their entirety without the need for endovascular intervention or venotomy. Pediatric patients who have a SSPC should undergo the guidewire extraction technique.
本研究回顾了一所大学的儿科外科实践,探讨了卡在皮下端口导管(SSPC)拔除的发生率和导丝拔除技术的效果。我们回顾了2018年至2020年间所有中心导管移除手术。SSPC被定义为在剥离皮下组织后抵抗移除,并伴有即将发生的器械骨折的迹象。详细的导管持续时间,初步诊断,并通过设备给药的记录。108例患者接受了导管拔除,其中6例被定义为SSPCs。导管原位放置时间为35 ~ 96个月。所有6例患者均采用导丝拔除技术,并在不需要血管内介入或静脉切开术的情况下全部切除。患有SSPC的儿科患者应采用导丝拔除技术。
{"title":"Safety and efficacy of central line removal by guidewire extraction technique in children","authors":"Mary Froehlich, Spencer Schulte, Shirong Chang, Alan Ikeda, Michael G. Scheidler","doi":"10.1186/s43159-023-00276-6","DOIUrl":"https://doi.org/10.1186/s43159-023-00276-6","url":null,"abstract":"This study reviews a university pediatric surgery practice for the incidence of stuck subcutaneous port catheter (SSPC) removal and the efficacy of a guidewire extraction technique. We reviewed all central catheter removals between 2018 and 2020. A SSPC was defined as resistance to removal after dissection of the subcutaneous tissue with signs of impending device fracture. Details of the catheter duration, initial diagnosis, and medications administered through the device were all recorded. One hundred eight patients underwent catheter removal and six were defined as SSPCs. Catheter in situ time ranged from 35 to 96 months. All six patients underwent the guidewire extraction technique and were removed in their entirety without the need for endovascular intervention or venotomy. Pediatric patients who have a SSPC should undergo the guidewire extraction technique.","PeriodicalId":43372,"journal":{"name":"Annals of Pediatric Surgery","volume":null,"pages":null},"PeriodicalIF":0.4,"publicationDate":"2023-12-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"138536049","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Management of a double H-type tracheoesophageal fistula without esophageal atresia: a case report 双h型气管食管瘘无食管闭锁1例
IF 0.4 Q4 Medicine Pub Date : 2023-12-01 DOI: 10.1186/s43159-023-00274-8
Chiraz Regaieg, Taycir Cheikhrouhou, Mahdi Ben Dhaou, Mariam Ammar, Nadia Kolsi, Riadh Mhiri, Afef Ben Thabet, Nadia Hmida
Double congenital tracheoesophageal fistula (TEF) without esophageal atresia, known as double H-type fistula, is an extremely uncommon malformation. Due to its nonspecific symptoms and the small size of the fistula in infancy, H-type tracheoesophageal fistula is rarely diagnosed in the neonatal period and is also challenging to repair. We report a rare case of double H-type tracheoesophageal fistula in a 2-day-old newborn, identified with a time-lapse and repaired separately. The diagnosis was established through repeated bronchoscopy, with methylene blue injected through an esophagoscope. A right thoracotomy was performed to undertake the surgical repair after cannulating the fistula with a vascular guide wire. Five months later, the infant, who had a history of recurrent episodes of coughing and shortness of breath, was diagnosed with acute respiratory distress, and a second TEF was detected by bronchoscopy. A cervical incision was used to repair the second H-type fistula. Double H-type tracheoesophageal fistula should be considered while correcting a tracheoesophageal fistula, especially if the symptoms continue after the first operation. Repeated radiological contrast studies and bronchoscopy with methylene blue injected through an esophagoscope help the early diagnosis.
双先天性气管食管瘘(TEF)无食道闭锁,称为双h型瘘,是一种极为罕见的畸形。由于h型气管食管瘘的症状非特异性,且其在婴儿期瘘管体积小,因此在新生儿期很少被诊断出来,其修复也具有挑战性。我们报告一个罕见的病例双h型气管食管瘘在一个2天大的新生儿,确定与延时和单独修复。通过反复支气管镜检查确定诊断,并通过食管镜注射亚甲基蓝。在导管插管后行右开胸手术修复。5个月后,这名有反复咳嗽和呼吸短促病史的婴儿被诊断为急性呼吸窘迫,并通过支气管镜检查发现第二次TEF。采用宫颈切口修复第二个h型瘘管。在纠正气管食管瘘时应考虑双h型气管食管瘘,特别是首次手术后症状持续的情况下。反复放射造影检查和支气管镜通过食管镜注射亚甲基蓝有助于早期诊断。
{"title":"Management of a double H-type tracheoesophageal fistula without esophageal atresia: a case report","authors":"Chiraz Regaieg, Taycir Cheikhrouhou, Mahdi Ben Dhaou, Mariam Ammar, Nadia Kolsi, Riadh Mhiri, Afef Ben Thabet, Nadia Hmida","doi":"10.1186/s43159-023-00274-8","DOIUrl":"https://doi.org/10.1186/s43159-023-00274-8","url":null,"abstract":"Double congenital tracheoesophageal fistula (TEF) without esophageal atresia, known as double H-type fistula, is an extremely uncommon malformation. Due to its nonspecific symptoms and the small size of the fistula in infancy, H-type tracheoesophageal fistula is rarely diagnosed in the neonatal period and is also challenging to repair. We report a rare case of double H-type tracheoesophageal fistula in a 2-day-old newborn, identified with a time-lapse and repaired separately. The diagnosis was established through repeated bronchoscopy, with methylene blue injected through an esophagoscope. A right thoracotomy was performed to undertake the surgical repair after cannulating the fistula with a vascular guide wire. Five months later, the infant, who had a history of recurrent episodes of coughing and shortness of breath, was diagnosed with acute respiratory distress, and a second TEF was detected by bronchoscopy. A cervical incision was used to repair the second H-type fistula. Double H-type tracheoesophageal fistula should be considered while correcting a tracheoesophageal fistula, especially if the symptoms continue after the first operation. Repeated radiological contrast studies and bronchoscopy with methylene blue injected through an esophagoscope help the early diagnosis.","PeriodicalId":43372,"journal":{"name":"Annals of Pediatric Surgery","volume":null,"pages":null},"PeriodicalIF":0.4,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"138536043","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Extrahepatic bile duct fibroma in an infant: a case report 婴儿肝外胆管纤维瘤1例报告
IF 0.4 Q4 Medicine Pub Date : 2023-11-16 DOI: 10.1186/s43159-023-00272-w
Md. Samiul Hasan, S. M. Nazmul Islam, Umama Huq, Mashud Parvez, Hasiba Mahshed Khan, Refoyez Mahmud, Ashrarur Rahman
Extrahepatic bile duct tumor in neonates and infants is extremely rare. Fibroma in neonates and infants has been reported in different body parts but not in the bile duct. We report a 2-month-old girl with common bile duct (CBD) fibroma. A 2-month-old girl presented with jaundice and pale stool for 15 days. Her perinatal period was uneventful. On examination, we found the girl deeply icteric and having hepatomegaly but no palpable lump. Laboratory investigations revealed direct hyperbilirubinemia with elevated liver enzymes. Ultrasonography revealed hepatomegaly with focal dilatation of the extrahepatic bile duct (2.1 × 0.5 cm). Our preliminary diagnosis was a type I choledochal cyst. Considering the clinical scenario, we planned for exploration without further imaging. On exploration, we found the liver blackish and a hard mass involving the common CBD and cystic duct. The gall bladder was filled with clear mucus. After excising the mass, the gall bladder, and CBD, we reconstructed the anatomy with Roux-N-Y hepaticojejunostomy. The postoperative period was uneventful except for minor bile leakage during the first four postoperative days, which stopped spontaneously. Histopathology revealed spindle-shaped fibrous tissue admixed with collagenous tissue, compatible with a fibroma. A liver biopsy showed the features of cirrhosis. However, liver function tests were normal 2 weeks after surgery. The baby was thriving at 6 months of follow-up, hepatomegaly was resolved, and there was no clinical or radiological sign of recurrence. CBD fibroma is a rare cause of obstructive jaundice in neonates and infants. The earliest possible excision of the tumor and bile drainage restoration are necessary to halt the progression of liver damage.
肝外胆管肿瘤在新生儿和婴儿中极为罕见。纤维瘤在新生儿和婴儿已报道在不同的身体部位,但没有在胆管。我们报告一个2个月大的女孩与胆总管(CBD)纤维瘤。2个月大的女婴黄疸,大便苍白15天。她的围产期平安无事。在检查中,我们发现女孩深度黄疸和肝肿大,但没有可触及的肿块。实验室调查显示直接高胆红素血症伴肝酶升高。超声示肝肿大伴肝外胆管局灶性扩张(2.1 × 0.5 cm)。初步诊断为I型胆总管囊肿。考虑到临床情况,我们计划不做进一步的影像学检查。在检查中,我们发现肝脏发黑,硬块累及总CBD和囊管。胆囊充满了透明的粘液。在切除肿物、胆囊和CBD后,我们采用Roux-N-Y肝空肠吻合术重建解剖结构。除术后4天发生轻微胆漏外,术后无大碍,胆漏自行停止。组织病理学显示纺锤形纤维组织与胶原组织混合,与纤维瘤相容。肝活检显示肝硬化的特征。术后2周肝功能检查正常。随访6个月时,婴儿发育良好,肝肿大消退,无临床或放射学复发迹象。CBD纤维瘤是一种罕见的原因梗阻性黄疸在新生儿和婴儿。尽早切除肿瘤和恢复胆汁引流对于阻止肝损伤的进展是必要的。
{"title":"Extrahepatic bile duct fibroma in an infant: a case report","authors":"Md. Samiul Hasan, S. M. Nazmul Islam, Umama Huq, Mashud Parvez, Hasiba Mahshed Khan, Refoyez Mahmud, Ashrarur Rahman","doi":"10.1186/s43159-023-00272-w","DOIUrl":"https://doi.org/10.1186/s43159-023-00272-w","url":null,"abstract":"Extrahepatic bile duct tumor in neonates and infants is extremely rare. Fibroma in neonates and infants has been reported in different body parts but not in the bile duct. We report a 2-month-old girl with common bile duct (CBD) fibroma. A 2-month-old girl presented with jaundice and pale stool for 15 days. Her perinatal period was uneventful. On examination, we found the girl deeply icteric and having hepatomegaly but no palpable lump. Laboratory investigations revealed direct hyperbilirubinemia with elevated liver enzymes. Ultrasonography revealed hepatomegaly with focal dilatation of the extrahepatic bile duct (2.1 × 0.5 cm). Our preliminary diagnosis was a type I choledochal cyst. Considering the clinical scenario, we planned for exploration without further imaging. On exploration, we found the liver blackish and a hard mass involving the common CBD and cystic duct. The gall bladder was filled with clear mucus. After excising the mass, the gall bladder, and CBD, we reconstructed the anatomy with Roux-N-Y hepaticojejunostomy. The postoperative period was uneventful except for minor bile leakage during the first four postoperative days, which stopped spontaneously. Histopathology revealed spindle-shaped fibrous tissue admixed with collagenous tissue, compatible with a fibroma. A liver biopsy showed the features of cirrhosis. However, liver function tests were normal 2 weeks after surgery. The baby was thriving at 6 months of follow-up, hepatomegaly was resolved, and there was no clinical or radiological sign of recurrence. CBD fibroma is a rare cause of obstructive jaundice in neonates and infants. The earliest possible excision of the tumor and bile drainage restoration are necessary to halt the progression of liver damage.","PeriodicalId":43372,"journal":{"name":"Annals of Pediatric Surgery","volume":null,"pages":null},"PeriodicalIF":0.4,"publicationDate":"2023-11-16","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"138536055","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Epigastric heteropagus twinning with dextrocardia: a case report 上胃异位伴右心1例
Q4 Medicine Pub Date : 2023-11-14 DOI: 10.1186/s43159-023-00273-9
Ayesha Siddiqua, None Noor-ul-Sabah, Muhammad Ramzan Bhutta
Abstract Background Heteropagus twinning is a rare birth defect in 1 in million live births. Epigastric heteropagus is the most frequent type, in which a smaller dependent (parasite twin) is attached to the body of the host (autosite twin) to the thorax and umbilicus. Several congenital anomalies have been previously described in the host twin. We describe the first case of epigastric heteropagus twinning with dextrocardia and situs inversus in which a successful surgical separation is performed. Case presentation A 48-h-old female sex twins were presented to Bahawal Victoria Hospital. A careful anatomic study using contrast X-ray, magnetic resonance imaging, and echocardiogram showed epigastric heteropagus twinning and situs inversus in autosite twin. A successful surgical separation was performed, and the parasite twin was removed from the body of the autosite twin. Conclusions Antepartum screening detects congenital malformations; however, several pregnancies are unsupervised in underdeveloped countries. In the case of heteropagus twinning, careful surgical separation in the absence of complications leads to the favorable survival of the autosite twin.
摘要背景异位双胞胎是一种罕见的出生缺陷,发生率为百万分之一。上腹部异食虫是最常见的类型,其中一个较小的依赖性(寄生双生体)附着在宿主的身体上(寄生双生体),位于胸腔和脐部。以前曾报道过宿主双胞胎的几种先天性异常。我们描述了第一例上腹部异位双胞胎右心和逆位,其中成功的手术分离进行。一例48小时的女性双胞胎被送到Bahawal Victoria医院。仔细的解剖研究使用对比x线,磁共振成像和超声心动图显示上腹部异位双胞胎和异位双胞胎。手术成功分离后,寄生双胞胎从自体双胞胎体内取出。结论产前筛查可发现先天性畸形;然而,在不发达国家,有些怀孕是无人监督的。在异位双胞胎的情况下,在没有并发症的情况下,小心的手术分离会导致有利的异位双胞胎存活。
{"title":"Epigastric heteropagus twinning with dextrocardia: a case report","authors":"Ayesha Siddiqua, None Noor-ul-Sabah, Muhammad Ramzan Bhutta","doi":"10.1186/s43159-023-00273-9","DOIUrl":"https://doi.org/10.1186/s43159-023-00273-9","url":null,"abstract":"Abstract Background Heteropagus twinning is a rare birth defect in 1 in million live births. Epigastric heteropagus is the most frequent type, in which a smaller dependent (parasite twin) is attached to the body of the host (autosite twin) to the thorax and umbilicus. Several congenital anomalies have been previously described in the host twin. We describe the first case of epigastric heteropagus twinning with dextrocardia and situs inversus in which a successful surgical separation is performed. Case presentation A 48-h-old female sex twins were presented to Bahawal Victoria Hospital. A careful anatomic study using contrast X-ray, magnetic resonance imaging, and echocardiogram showed epigastric heteropagus twinning and situs inversus in autosite twin. A successful surgical separation was performed, and the parasite twin was removed from the body of the autosite twin. Conclusions Antepartum screening detects congenital malformations; however, several pregnancies are unsupervised in underdeveloped countries. In the case of heteropagus twinning, careful surgical separation in the absence of complications leads to the favorable survival of the autosite twin.","PeriodicalId":43372,"journal":{"name":"Annals of Pediatric Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-11-14","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"134900998","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
An unusual location of newborn huge dermoid cyst: a case report and literature review 新生儿巨大皮样囊肿异常部位1例报告并文献复习
Q4 Medicine Pub Date : 2023-11-08 DOI: 10.1186/s43159-023-00266-8
Mahaman Sani Rabiou, Maman Roufai Hamissou Moussa, Hassane Ali Amadou, Stachys Beranger Hounkpatin Seton
Abstract Background Dermoid cysts are benign germ cell tumors with ectodermal and mesodermal components. It is a slow-growing lesion that commonly arises in the midline of the head and neck. The last location represented 7%, and the periorbital region was the most frequently arising area. True lateral neck dermoid cysts are rare. We present an unusual location of a dermoid cyst in a newborn. Case presentation We report an unusual location of a 10-day newborn giant dermoid cyst with multiple implantation sites, namely the shoulder, scapula, cervical, temporal, and occipital scalp. Successful surgical resection was achieved, and the patient was discharged after the removal of the stitches. Conclusion Dermoid cysts are unusual neoplasms with rare diagnoses at birth, but often in childhood. Concomitant implantation locations on the shoulder, neck, temporal, and occipital scalps are rare.
皮样囊肿是一种具有外胚层和中胚层成分的良性生殖细胞肿瘤。这是一种生长缓慢的病变,通常出现在头部和颈部的中线。最后发生部位占7%,眶周是最常发生的部位。真正的外侧颈部皮样囊肿是罕见的。我们提出一个新生儿的皮样囊肿的不寻常的位置。我们报告了一个罕见的10天的新生儿巨大皮样囊肿,有多个着床部位,即肩部,肩胛骨,颈椎,颞部和枕部头皮。手术切除成功,患者拆线后出院。结论皮样囊肿是一种罕见的肿瘤,出生时很少诊断,但在儿童期很常见。肩关节、颈部、颞部和枕部同时植入的情况很少见。
{"title":"An unusual location of newborn huge dermoid cyst: a case report and literature review","authors":"Mahaman Sani Rabiou, Maman Roufai Hamissou Moussa, Hassane Ali Amadou, Stachys Beranger Hounkpatin Seton","doi":"10.1186/s43159-023-00266-8","DOIUrl":"https://doi.org/10.1186/s43159-023-00266-8","url":null,"abstract":"Abstract Background Dermoid cysts are benign germ cell tumors with ectodermal and mesodermal components. It is a slow-growing lesion that commonly arises in the midline of the head and neck. The last location represented 7%, and the periorbital region was the most frequently arising area. True lateral neck dermoid cysts are rare. We present an unusual location of a dermoid cyst in a newborn. Case presentation We report an unusual location of a 10-day newborn giant dermoid cyst with multiple implantation sites, namely the shoulder, scapula, cervical, temporal, and occipital scalp. Successful surgical resection was achieved, and the patient was discharged after the removal of the stitches. Conclusion Dermoid cysts are unusual neoplasms with rare diagnoses at birth, but often in childhood. Concomitant implantation locations on the shoulder, neck, temporal, and occipital scalps are rare.","PeriodicalId":43372,"journal":{"name":"Annals of Pediatric Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-11-08","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"135340928","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
High magnification versus optical magnification in hypospadias surgery: a randomized controlled trial 尿道下裂手术的高倍放大与光学放大:一项随机对照试验
Q4 Medicine Pub Date : 2023-11-06 DOI: 10.1186/s43159-023-00268-6
Moemen Mohamed Farouk Radwan, Sherif Nabhan Kaddah, Gamal Hasan ElTagy, Khaled S. Abdullateef
Abstract Background Hypospadias is the most common congenital abnormality of the urethra affecting live male births. The incidence is rising with the increasing pollution. During the last 50 years, developments in surgical instrumentation and optical systems allowed surgeons to increasingly undertake microsurgical procedures. Optical magnification is essential in pediatric surgery. Magnifying loupes are the most frequently used, although they often cause neck pain to the surgeon. Recent advances led to the development of a compact video microscope (VITOM; Karl Storz Endoscopy GmbH, Tuttlingen, Germany) that displays high-definition magnified images on a flat screen. Objective Evaluate VITOM as a potential substitute for loupes in complex open pediatric procedures and explore VITOM as an effective intraoperative teaching modality for open surgery. Methods Fifty-two patients enrolled in our study were divided into two groups: Group A (26): high magnification was used either (VITOM Karl Storz Endoscopy GmbH, Tuttlingen, Germany) or (Surgical microscope, Carl Zeiss Microscopy GmbH), along with microsurgical instruments. Vicryl 8-0 suture was used for urethroplasty. Group B (26): patients were operated upon by conventional instruments (fine tip but not microsurgical instruments), sutures, and magnification (3.5×). Vicryl 6-0 suture was used for urethroplasty, with loupes-assisted magnification. Results More complications were found in group B. Using VITOM was accompanied by less neck pain, enhanced visualization, and an enhanced teaching environment. Conclusion Operating with high magnification tools minimizes post-operative complications in hypospadias surgery. They enhanced identification of the penile anatomy and topography which facilitated reconstruction techniques as well as enhanced the comfort of the surgeon. Level of evidence I.
摘要背景尿道下裂是影响男婴出生的最常见的先天性尿道异常。随着污染的加剧,发病率也在上升。在过去的50年里,手术器械和光学系统的发展使外科医生越来越多地进行显微外科手术。光学放大在儿科手术中是必不可少的。放大镜是最常用的,尽管它们经常给外科医生带来颈部疼痛。最近的进展导致了紧凑的视频显微镜(VITOM;Karl Storz内窥镜公司(德国Tuttlingen),在平面屏幕上显示高清放大图像。目的评价VITOM在复杂儿科开放手术中作为镜的潜在替代品,探讨VITOM作为开放手术术中有效的教学方式。方法将52例患者分为两组:A组(26例):使用高倍镜(德国Tuttlingen的VITOM Karl Storz内镜公司)或手术显微镜(德国卡尔蔡司显微镜公司),并使用显微手术器械。尿道成形术采用Vicryl 8-0缝线。B组(26例):采用常规器械(细针尖不使用显微手术器械)、缝合、3.5倍放大镜进行手术。使用Vicryl 6-0缝线进行尿道成形术,镜下辅助放大。结果b组并发症发生率高,使用VITOM后颈部疼痛减轻,视觉效果增强,教学环境改善。结论在尿道下裂手术中使用高倍镜可减少术后并发症。他们提高了阴茎解剖和地形的识别,促进了重建技术,并提高了外科医生的舒适度。证据水平1。
{"title":"High magnification versus optical magnification in hypospadias surgery: a randomized controlled trial","authors":"Moemen Mohamed Farouk Radwan, Sherif Nabhan Kaddah, Gamal Hasan ElTagy, Khaled S. Abdullateef","doi":"10.1186/s43159-023-00268-6","DOIUrl":"https://doi.org/10.1186/s43159-023-00268-6","url":null,"abstract":"Abstract Background Hypospadias is the most common congenital abnormality of the urethra affecting live male births. The incidence is rising with the increasing pollution. During the last 50 years, developments in surgical instrumentation and optical systems allowed surgeons to increasingly undertake microsurgical procedures. Optical magnification is essential in pediatric surgery. Magnifying loupes are the most frequently used, although they often cause neck pain to the surgeon. Recent advances led to the development of a compact video microscope (VITOM; Karl Storz Endoscopy GmbH, Tuttlingen, Germany) that displays high-definition magnified images on a flat screen. Objective Evaluate VITOM as a potential substitute for loupes in complex open pediatric procedures and explore VITOM as an effective intraoperative teaching modality for open surgery. Methods Fifty-two patients enrolled in our study were divided into two groups: Group A (26): high magnification was used either (VITOM Karl Storz Endoscopy GmbH, Tuttlingen, Germany) or (Surgical microscope, Carl Zeiss Microscopy GmbH), along with microsurgical instruments. Vicryl 8-0 suture was used for urethroplasty. Group B (26): patients were operated upon by conventional instruments (fine tip but not microsurgical instruments), sutures, and magnification (3.5×). Vicryl 6-0 suture was used for urethroplasty, with loupes-assisted magnification. Results More complications were found in group B. Using VITOM was accompanied by less neck pain, enhanced visualization, and an enhanced teaching environment. Conclusion Operating with high magnification tools minimizes post-operative complications in hypospadias surgery. They enhanced identification of the penile anatomy and topography which facilitated reconstruction techniques as well as enhanced the comfort of the surgeon. Level of evidence I.","PeriodicalId":43372,"journal":{"name":"Annals of Pediatric Surgery","volume":null,"pages":null},"PeriodicalIF":0.0,"publicationDate":"2023-11-06","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"135585104","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
期刊
Annals of Pediatric Surgery
全部 Acc. Chem. Res. ACS Applied Bio Materials ACS Appl. Electron. Mater. ACS Appl. Energy Mater. ACS Appl. Mater. Interfaces ACS Appl. Nano Mater. ACS Appl. Polym. Mater. ACS BIOMATER-SCI ENG ACS Catal. ACS Cent. Sci. ACS Chem. Biol. ACS Chemical Health & Safety ACS Chem. Neurosci. ACS Comb. Sci. ACS Earth Space Chem. ACS Energy Lett. ACS Infect. Dis. ACS Macro Lett. ACS Mater. Lett. ACS Med. Chem. Lett. ACS Nano ACS Omega ACS Photonics ACS Sens. ACS Sustainable Chem. Eng. ACS Synth. Biol. Anal. Chem. BIOCHEMISTRY-US Bioconjugate Chem. BIOMACROMOLECULES Chem. Res. Toxicol. Chem. Rev. Chem. Mater. CRYST GROWTH DES ENERG FUEL Environ. Sci. Technol. Environ. Sci. Technol. Lett. Eur. J. Inorg. Chem. IND ENG CHEM RES Inorg. Chem. J. Agric. Food. Chem. J. Chem. Eng. Data J. Chem. Educ. J. Chem. Inf. Model. J. Chem. Theory Comput. J. Med. Chem. J. Nat. Prod. J PROTEOME RES J. Am. Chem. Soc. LANGMUIR MACROMOLECULES Mol. Pharmaceutics Nano Lett. Org. Lett. ORG PROCESS RES DEV ORGANOMETALLICS J. Org. Chem. J. Phys. Chem. J. Phys. Chem. A J. Phys. Chem. B J. Phys. Chem. C J. Phys. Chem. Lett. Analyst Anal. Methods Biomater. Sci. Catal. Sci. Technol. Chem. Commun. Chem. Soc. Rev. CHEM EDUC RES PRACT CRYSTENGCOMM Dalton Trans. Energy Environ. Sci. ENVIRON SCI-NANO ENVIRON SCI-PROC IMP ENVIRON SCI-WAT RES Faraday Discuss. Food Funct. Green Chem. Inorg. Chem. Front. Integr. Biol. J. Anal. At. Spectrom. J. Mater. Chem. A J. Mater. Chem. B J. Mater. Chem. C Lab Chip Mater. Chem. Front. Mater. Horiz. MEDCHEMCOMM Metallomics Mol. Biosyst. Mol. Syst. Des. Eng. Nanoscale Nanoscale Horiz. Nat. Prod. Rep. New J. Chem. Org. Biomol. Chem. Org. Chem. Front. PHOTOCH PHOTOBIO SCI PCCP Polym. Chem.
×
引用
GB/T 7714-2015
复制
MLA
复制
APA
复制
导出至
BibTeX EndNote RefMan NoteFirst NoteExpress
×
0
微信
客服QQ
Book学术公众号 扫码关注我们
反馈
×
意见反馈
请填写您的意见或建议
请填写您的手机或邮箱
×
提示
您的信息不完整,为了账户安全,请先补充。
现在去补充
×
提示
您因"违规操作"
具体请查看互助需知
我知道了
×
提示
现在去查看 取消
×
提示
确定
Book学术官方微信
Book学术文献互助
Book学术文献互助群
群 号:481959085
Book学术
文献互助 智能选刊 最新文献 互助须知 联系我们:info@booksci.cn
Book学术提供免费学术资源搜索服务,方便国内外学者检索中英文文献。致力于提供最便捷和优质的服务体验。
Copyright © 2023 Book学术 All rights reserved.
ghs 京公网安备 11010802042870号 京ICP备2023020795号-1