Pub Date : 2023-01-01DOI: 10.4103/jclpca.jclpca_20_22
Sneha Gulati, A. Yadav, R. Sharma
Congenital palatal fistula (CPF) is the rarest phenotypic variation of cleft palate, commonly associated with submucous cleft palate (SCP). Isolated palatal fistula without SCP has been reported only rarely. We report here the case of a 4-year-old child, with a 10 mm × 5 mm CPF, presenting with nasal regurgitation and speech abnormalities. The patient had unilateral palatal muscular malposition without classical features of SCP. The repair was performed using turnover flaps and Bardach's two-long flap palatoplasty and intravelar veloplasty. Healing occurred without any complications.
{"title":"Congenital palatal fistula: Case report and review of literature","authors":"Sneha Gulati, A. Yadav, R. Sharma","doi":"10.4103/jclpca.jclpca_20_22","DOIUrl":"https://doi.org/10.4103/jclpca.jclpca_20_22","url":null,"abstract":"Congenital palatal fistula (CPF) is the rarest phenotypic variation of cleft palate, commonly associated with submucous cleft palate (SCP). Isolated palatal fistula without SCP has been reported only rarely. We report here the case of a 4-year-old child, with a 10 mm × 5 mm CPF, presenting with nasal regurgitation and speech abnormalities. The patient had unilateral palatal muscular malposition without classical features of SCP. The repair was performed using turnover flaps and Bardach's two-long flap palatoplasty and intravelar veloplasty. Healing occurred without any complications.","PeriodicalId":34294,"journal":{"name":"Journal of Cleft Lip Palate and Craniofacial Anomalies","volume":"10 1","pages":"37 - 39"},"PeriodicalIF":0.0,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"42626806","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-01-01DOI: 10.4103/jclpca.jclpca_13_22
Vijaylaxmi B Mendigeri, Praveenkumar Ramdurg, Fatima Lingadalli, Sanjay V. Ganeshkar
Silver–Russell syndrome (SRS) is a rare congenital abnormality. The incidence ranges from 1 in 3000 to 100,000 live births. It is characterized by low birth weight, asymmetric limb, relative macrocephaly, high forehead, small triangular-shaped face with small jaws, and dental malocclusion. The etiology of SRS is still unclear, but genetic alterations and family history have been attributed. The diagnosis of SRS is mainly based on physical characteristics and appearance. This article enlightens clinical versatility in dental features of SRS in two siblings and discusses the orthodontic management for dental malocclusion in the elder one.
{"title":"Silver–Russell syndrome in siblings with orthodontic management","authors":"Vijaylaxmi B Mendigeri, Praveenkumar Ramdurg, Fatima Lingadalli, Sanjay V. Ganeshkar","doi":"10.4103/jclpca.jclpca_13_22","DOIUrl":"https://doi.org/10.4103/jclpca.jclpca_13_22","url":null,"abstract":"Silver–Russell syndrome (SRS) is a rare congenital abnormality. The incidence ranges from 1 in 3000 to 100,000 live births. It is characterized by low birth weight, asymmetric limb, relative macrocephaly, high forehead, small triangular-shaped face with small jaws, and dental malocclusion. The etiology of SRS is still unclear, but genetic alterations and family history have been attributed. The diagnosis of SRS is mainly based on physical characteristics and appearance. This article enlightens clinical versatility in dental features of SRS in two siblings and discusses the orthodontic management for dental malocclusion in the elder one.","PeriodicalId":34294,"journal":{"name":"Journal of Cleft Lip Palate and Craniofacial Anomalies","volume":"10 1","pages":"31 - 36"},"PeriodicalIF":0.0,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"47048489","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-01-01DOI: 10.4103/jclpca.jclpca_31_22
J. Ferri, Tony Markus, S. Reddy
{"title":"Obituary of Prof. Delaire","authors":"J. Ferri, Tony Markus, S. Reddy","doi":"10.4103/jclpca.jclpca_31_22","DOIUrl":"https://doi.org/10.4103/jclpca.jclpca_31_22","url":null,"abstract":"","PeriodicalId":34294,"journal":{"name":"Journal of Cleft Lip Palate and Craniofacial Anomalies","volume":"10 1","pages":"3 - 4"},"PeriodicalIF":0.0,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"46413900","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-01-01DOI: 10.4103/jclpca.jclpca_25_22
Partha Sadhu, Neelam Chauhan
Cleft palate is the most common craniofacial anomaly with multiple surgical options in the armamentarium of a surgeon. Following the principles and right surgical techniques can yield excellent functional results. The various techniques have gradually developed over time and each has their own peculiarities along with specific advantages and disadvantages. Here, in this article, we will be discussing a few palatoplasty techniques which have stood the test of time and are commonly performed.
{"title":"Cleft palate: Part II – The concept and techniques","authors":"Partha Sadhu, Neelam Chauhan","doi":"10.4103/jclpca.jclpca_25_22","DOIUrl":"https://doi.org/10.4103/jclpca.jclpca_25_22","url":null,"abstract":"Cleft palate is the most common craniofacial anomaly with multiple surgical options in the armamentarium of a surgeon. Following the principles and right surgical techniques can yield excellent functional results. The various techniques have gradually developed over time and each has their own peculiarities along with specific advantages and disadvantages. Here, in this article, we will be discussing a few palatoplasty techniques which have stood the test of time and are commonly performed.","PeriodicalId":34294,"journal":{"name":"Journal of Cleft Lip Palate and Craniofacial Anomalies","volume":"10 1","pages":"48 - 53"},"PeriodicalIF":0.0,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"70783665","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-01-01DOI: 10.4103/jclpca.jclpca_29_22
Hardeep Singh, R. Khazanchi
Postoperative palatal fistulas are common after surgery to correct a cleft palate. The repair is hindered by palatoplasty-related scar tissue, reduced vascularity, and restricted mobility of flaps. Surgical repair of fistulae is often effective, but recurrence is common. A 3.5-year-old boy presented with anterior palatal fistula. The presence of peri-fistulous scarring prevented two-layered closure. Nasal layer closure was achieved but not the oral layer. The dermal matrix was reinforced in a one-step procedure over the nasal layer and fixed in place using a gel foam. At 6 months, the fistula almost completely healed, with only a pinpoint track remaining that occasionally leaked into the nasal cavity. These results indicate that the application of dermal matrix is a promising technique to repair fistula with surrounding scarring, but larger, prospective trials are needed to confirm its potential benefits.
{"title":"Dermal substitute reinforced single-layer closure of the palatal fistula","authors":"Hardeep Singh, R. Khazanchi","doi":"10.4103/jclpca.jclpca_29_22","DOIUrl":"https://doi.org/10.4103/jclpca.jclpca_29_22","url":null,"abstract":"Postoperative palatal fistulas are common after surgery to correct a cleft palate. The repair is hindered by palatoplasty-related scar tissue, reduced vascularity, and restricted mobility of flaps. Surgical repair of fistulae is often effective, but recurrence is common. A 3.5-year-old boy presented with anterior palatal fistula. The presence of peri-fistulous scarring prevented two-layered closure. Nasal layer closure was achieved but not the oral layer. The dermal matrix was reinforced in a one-step procedure over the nasal layer and fixed in place using a gel foam. At 6 months, the fistula almost completely healed, with only a pinpoint track remaining that occasionally leaked into the nasal cavity. These results indicate that the application of dermal matrix is a promising technique to repair fistula with surrounding scarring, but larger, prospective trials are needed to confirm its potential benefits.","PeriodicalId":34294,"journal":{"name":"Journal of Cleft Lip Palate and Craniofacial Anomalies","volume":"10 1","pages":"45 - 47"},"PeriodicalIF":0.0,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"43050903","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-01-01DOI: 10.4103/jclpca.jclpca_22_22
Gaurav Singh, G. Vohra
Cleft lip and palate (CLP) is one of the most common craniofacial birth defects. Its incidence varies according to race, sex and region. As ubiquitous as the condition may be, when it comes to clinical presentation, CLP manifests in a myriad of forms and varieties. The most common clinical presentation is that of a unilateral cleft lip and palate (UCLP). Management of CLP is a challenging proposition but in recent times, the results have become better owing to standardization of treatment protocol and the availability of multidisciplinary teams at specialized cleft centers worldwide. Management of CLP is initiated right from birth with parental counselling followed by presurgical infant orthopedics (PSIO). Nasoalveolar moulding (NAM) is on of the most widely accepted modalities of PSIO and is used to achieve alignment of the cleft alveolar segments into a more ideal relationship prior to the primary lip repair surgery. In its bare essence, NAM uses an acrylic molding plate with selective addition and removal of soft liner to mould the segments into a more ideal position. The molding plate is held in place with elastics which are retained by the use of adherent tapes on the cheek. The use of these tapes on a young infant often leads to tissue irritation and results in reduced compliance and treatment effect. Herein this case report we aim to highlight a novel approach of retaining the molding plate which dispenses with the need of adherent tapes. This technique has the benefit of no tissue irritation, easier application and improved compliance.
{"title":"A novel modification of nasoalveolar molding procedure to enhance ease of use","authors":"Gaurav Singh, G. Vohra","doi":"10.4103/jclpca.jclpca_22_22","DOIUrl":"https://doi.org/10.4103/jclpca.jclpca_22_22","url":null,"abstract":"Cleft lip and palate (CLP) is one of the most common craniofacial birth defects. Its incidence varies according to race, sex and region. As ubiquitous as the condition may be, when it comes to clinical presentation, CLP manifests in a myriad of forms and varieties. The most common clinical presentation is that of a unilateral cleft lip and palate (UCLP). Management of CLP is a challenging proposition but in recent times, the results have become better owing to standardization of treatment protocol and the availability of multidisciplinary teams at specialized cleft centers worldwide. Management of CLP is initiated right from birth with parental counselling followed by presurgical infant orthopedics (PSIO). Nasoalveolar moulding (NAM) is on of the most widely accepted modalities of PSIO and is used to achieve alignment of the cleft alveolar segments into a more ideal relationship prior to the primary lip repair surgery. In its bare essence, NAM uses an acrylic molding plate with selective addition and removal of soft liner to mould the segments into a more ideal position. The molding plate is held in place with elastics which are retained by the use of adherent tapes on the cheek. The use of these tapes on a young infant often leads to tissue irritation and results in reduced compliance and treatment effect. Herein this case report we aim to highlight a novel approach of retaining the molding plate which dispenses with the need of adherent tapes. This technique has the benefit of no tissue irritation, easier application and improved compliance.","PeriodicalId":34294,"journal":{"name":"Journal of Cleft Lip Palate and Craniofacial Anomalies","volume":"10 1","pages":"40 - 44"},"PeriodicalIF":0.0,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"42080997","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-01-01DOI: 10.4103/jclpca.jclpca_26_22
Harsha Vardhan, M. Verma
Cleft lip and palate is one of the most common craniofacial anomaly. The management of this entity has led to the development of the field of craniofacial surgery. Improvement in understanding of clefts and refinement in surgical techniques have improved the life of children with clefts. However, like with all congenital anomalies, the impulse is to look earlier. Fetal management of cleft lip and palate is an attractive avenue. In this paper we explore this less travelled road, to see the advances in the field of detection of cleft lip and palate in the fetus, and to see the current state of fetal surgery for cleft lip and palate.
{"title":"Prenatal management in clefts","authors":"Harsha Vardhan, M. Verma","doi":"10.4103/jclpca.jclpca_26_22","DOIUrl":"https://doi.org/10.4103/jclpca.jclpca_26_22","url":null,"abstract":"Cleft lip and palate is one of the most common craniofacial anomaly. The management of this entity has led to the development of the field of craniofacial surgery. Improvement in understanding of clefts and refinement in surgical techniques have improved the life of children with clefts. However, like with all congenital anomalies, the impulse is to look earlier. Fetal management of cleft lip and palate is an attractive avenue. In this paper we explore this less travelled road, to see the advances in the field of detection of cleft lip and palate in the fetus, and to see the current state of fetal surgery for cleft lip and palate.","PeriodicalId":34294,"journal":{"name":"Journal of Cleft Lip Palate and Craniofacial Anomalies","volume":"10 1","pages":"26 - 30"},"PeriodicalIF":0.0,"publicationDate":"2023-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"48011823","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2022-12-31DOI: 10.31136/kjclp.2022.25.2.45
dong-min Lee, Yong-Deok Kim
{"title":"Consideration for Orthognathic Surgery on Tessier No.5 Cleft Patient – A Case Report","authors":"dong-min Lee, Yong-Deok Kim","doi":"10.31136/kjclp.2022.25.2.45","DOIUrl":"https://doi.org/10.31136/kjclp.2022.25.2.45","url":null,"abstract":"","PeriodicalId":34294,"journal":{"name":"Journal of Cleft Lip Palate and Craniofacial Anomalies","volume":"111 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2022-12-31","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"88727616","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2022-12-31DOI: 10.31136/kjclp.2022.25.2.52
Ji-Yeon Kang
{"title":"Restoration of Nasolabial Volume Using Implants and Secondary Cleft Rhinoplasty in a Patient with Unilateral Cleft Lip and Palate: A Case Report","authors":"Ji-Yeon Kang","doi":"10.31136/kjclp.2022.25.2.52","DOIUrl":"https://doi.org/10.31136/kjclp.2022.25.2.52","url":null,"abstract":"","PeriodicalId":34294,"journal":{"name":"Journal of Cleft Lip Palate and Craniofacial Anomalies","volume":"PP 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2022-12-31","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"84172768","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}