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A Saddle Pulmonary Embolism at Transthoracic Echocardiography: A Case Report 经胸超声心动图检查发现鞍状肺栓塞:病例报告
Pub Date : 2024-02-02 DOI: 10.36347/sjmcr.2024.v12i02.007
Wassim Beladel, M. E. Minaoui
Acute Pulmonary embolism (PE) is a life-threatening disease and is considered the third major cause of cardiovascular death with higher incidence and mortality rates. Identifying a saddle PE between the left and the right pulmonary trunk in transthoracic echocardiography (TTE) is rare, and helps to make a rapid diagnosis to avoid complications. Clinical presentation, electrocardiogram, and X-ray guide the diagnosis but are not specific. TTE is helpful and confirms the diagnosis especially when the CT is not available or in other situations when it is not realizable. Visualizing a pulmonary artery thrombus in TTE is unusual. It can be identified in the right cardiac chambers in less than 5% of patients with PE. The severity of acute PE is determined by its hemodynamics, the sudden pulmonary hypertension, and the development of obstructive shock. Anticoagulation therapy is the cornerstone of PE management and should be initiated as soon as possible.
急性肺栓塞(PE)是一种危及生命的疾病,被认为是心血管疾病的第三大死因,发病率和死亡率均较高。在经胸超声心动图(TTE)中发现左肺主干和右肺主干之间的鞍状肺栓塞非常罕见,有助于快速诊断,避免并发症。临床表现、心电图和 X 光检查可指导诊断,但不具有特异性。TTE 有助于确诊,尤其是在 CT 无法使用或其他无法实现 CT 的情况下。在 TTE 中看到肺动脉血栓并不常见。只有不到 5%的 PE 患者能在右心腔发现肺动脉血栓。急性 PE 的严重程度取决于其血液动力学、突发性肺动脉高压和阻塞性休克的发展。抗凝治疗是 PE 治疗的基石,应尽快开始。
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引用次数: 0
A Saddle Pulmonary Embolism at Transthoracic Echocardiography: A Case Report 经胸超声心动图检查发现鞍状肺栓塞:病例报告
Pub Date : 2024-02-02 DOI: 10.36347/sjmcr.2024.v12i02.007
Wassim Beladel, M. E. Minaoui
Acute Pulmonary embolism (PE) is a life-threatening disease and is considered the third major cause of cardiovascular death with higher incidence and mortality rates. Identifying a saddle PE between the left and the right pulmonary trunk in transthoracic echocardiography (TTE) is rare, and helps to make a rapid diagnosis to avoid complications. Clinical presentation, electrocardiogram, and X-ray guide the diagnosis but are not specific. TTE is helpful and confirms the diagnosis especially when the CT is not available or in other situations when it is not realizable. Visualizing a pulmonary artery thrombus in TTE is unusual. It can be identified in the right cardiac chambers in less than 5% of patients with PE. The severity of acute PE is determined by its hemodynamics, the sudden pulmonary hypertension, and the development of obstructive shock. Anticoagulation therapy is the cornerstone of PE management and should be initiated as soon as possible.
急性肺栓塞(PE)是一种危及生命的疾病,被认为是心血管疾病的第三大死因,发病率和死亡率均较高。在经胸超声心动图(TTE)中发现左肺主干和右肺主干之间的鞍状肺栓塞非常罕见,有助于快速诊断,避免并发症。临床表现、心电图和 X 光检查可指导诊断,但不具有特异性。TTE 有助于确诊,尤其是在 CT 无法使用或其他无法实现 CT 的情况下。在 TTE 中看到肺动脉血栓并不常见。只有不到 5%的 PE 患者能在右心腔发现肺动脉血栓。急性 PE 的严重程度取决于其血液动力学、突发性肺动脉高压和阻塞性休克的发展。抗凝治疗是 PE 治疗的基石,应尽快开始。
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引用次数: 0
New Case of Papillary Thyroglossal Tract Cyst Carcinoma, in the Absence of Clear Guidelines, What Should Be Do? 新发乳头状甲状舌管囊肿癌病例,在缺乏明确指南的情况下该怎么办?
Pub Date : 2024-02-01 DOI: 10.36347/sjmcr.2024.v12i02.003
Hamza El Jadi, A. Kessab, Hajar Srifi, Imane Moustaghit
Thyroglossal tract cyst carcinoma (TTCC) is a rare pathological situation, The challenge is mainly in the surgical management. In this article, we report a new case of papillary TTCC in a 51 years old female patient, not suspected preoperatively and confirmed postoperatively by histological analysis of the resected specimen. The therapeutic strategy was completed by a total thyroidectomy with adjuvant treatment with radioactive iodine and hormone restraint therapy. The outcome was favorable after 7 years of follow-up. In the absence of clear guidelines, the management of TTCC depends on the clinical situation and the experience of the treating team.
甲状舌管囊肿癌(TTCC)是一种罕见的病理情况,其难点主要在于手术治疗。本文报告了一例新的乳头状 TTCC 病例,患者 51 岁,女性,术前未怀疑,术后通过切除标本的组织学分析确诊为乳头状 TTCC。治疗策略是进行甲状腺全切除术,并辅以放射性碘和激素抑制疗法。经过7年的随访,结果良好。由于缺乏明确的指导方针,TTCC的治疗取决于临床情况和治疗团队的经验。
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引用次数: 0
Uterine Rupture: A Distressing Catalyst for Severe Postpartum Hemorrhage 子宫破裂:产后严重出血的令人不安的催化剂
Pub Date : 2024-02-01 DOI: 10.36347/sjmcr.2024.v12i02.004
Chirag Sharma, Hina Patel
Uterine rupture is a disruption of the uterine scar, causing foetal expulsion into the peritoneal cavity. This condition, primarily caused by the separation of uterine scar tissue from previous caesarean surgery, reduces foetal survival and increases maternal morbidity and mortality. A 32-year-old woman with a history of four vaginal deliveries and one caesarean section was diagnosed with uterine rupture, leading to a laparotomy procedure and obstetric hysterectomy. Consistent antenatal care can prevent uterine rupture.
子宫破裂是指子宫瘢痕破裂,导致胎儿排入腹腔。这种情况主要是由之前剖腹产手术造成的子宫疤痕组织分离引起的,它降低了胎儿的存活率,增加了产妇的发病率和死亡率。一名 32 岁的产妇曾有过四次阴道分娩史和一次剖腹产史,被诊断为子宫破裂,因此接受了开腹手术和产科子宫切除术。坚持产前护理可预防子宫破裂。
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引用次数: 0
Value of the Myelogram in the Diagnosis of Gaucher Disease: Two Cases Report 骨髓造影在戈谢病诊断中的价值:两例报告
Pub Date : 2024-02-01 DOI: 10.36347/sjmcr.2024.v12i02.002
Houari Mouna, Krichal Lina, Nasfi Abdelmalek, Latifa Jalili, Ammor Abdeslam, Chaimae Errabhi, Majda Elhassouni, Tasnim Kouame, Kaoutar Bahyat, Aissaoui Fqayeh Abderrahmane, Houari Mouna
Among the most common constitutional overload enzymopathies, Gaucher disease is a rare constitutional overload disease and often caused by lysosomal enzyme deficiencies in pediatric population more than adults. The cause of Gaucher disease is a deficiency of glucocerebrosidase resulting in an accumulation of glucocerebroside) in macrophages. These abundant macrophages are present in the lymphoid tissues (spleen, liver, marrow, lymph node), some of which have a characteristic morphological appearance (Gaucher cell) allowing the diagnosis to be suggested during myelogram. Reporting two cases of adult patients in whom the demonstration of overload cells in the myelogram allowed us to direct towards the diagnosis of Gaucher disease.
在最常见的体质性超负荷酶病中,戈谢病是一种罕见的体质性超负荷疾病,通常是由溶酶体酶缺乏引起的,在儿童中的发病率高于成人。戈谢病的病因是葡萄糖脑苷脂酶缺乏,导致巨噬细胞中的葡萄糖苷积累。这些大量的巨噬细胞存在于淋巴组织(脾脏、肝脏、骨髓、淋巴结)中,其中一些具有特征性的形态学外观(戈谢病细胞),因此在进行骨髓造影时可提示诊断。报告了两例成年患者,他们的骨髓造影显示出超负荷细胞,使我们能够做出戈谢病的诊断。
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引用次数: 0
Synovial Sarcomatous Transformation in Recklinghaussen Disease: A Case Report 雷克林豪森氏病的滑膜肉瘤变:病例报告
Pub Date : 2024-02-01 DOI: 10.36347/sjmcr.2024.v12i02.001
J. Mhaili, Mohammed Boussif, Youssef Bouktib Ayoub El Hajjami, B. Boutakioute, M. Idrissi, N. I. Ganouni
Malignant sarcomatous transformation of neurofibromas MSTN are a major cause of mortality in patients with NF1, its optimal management and final prognosis depend on early and accurate detection. Through a case report and a literature review, we will discuss the specificity of sarcomatous transformation in Neurofibromatosis type 1.
神经纤维瘤的恶性肉瘤变 MSTN 是导致 NF1 患者死亡的主要原因,其最佳治疗和最终预后取决于早期和准确的检测。通过病例报告和文献综述,我们将讨论神经纤维瘤病 1 型肉瘤变的特异性。
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引用次数: 0
Synovial Sarcomatous Transformation in Recklinghaussen Disease: A Case Report 雷克林豪森氏病的滑膜肉瘤变:病例报告
Pub Date : 2024-02-01 DOI: 10.36347/sjmcr.2024.v12i02.001
J. Mhaili, Mohammed Boussif, Youssef Bouktib Ayoub El Hajjami, B. Boutakioute, M. Idrissi, N. I. Ganouni
Malignant sarcomatous transformation of neurofibromas MSTN are a major cause of mortality in patients with NF1, its optimal management and final prognosis depend on early and accurate detection. Through a case report and a literature review, we will discuss the specificity of sarcomatous transformation in Neurofibromatosis type 1.
神经纤维瘤的恶性肉瘤变 MSTN 是导致 NF1 患者死亡的主要原因,其最佳治疗和最终预后取决于早期和准确的检测。通过病例报告和文献综述,我们将讨论神经纤维瘤病 1 型肉瘤变的特异性。
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引用次数: 0
Uterine Rupture: A Distressing Catalyst for Severe Postpartum Hemorrhage 子宫破裂:产后严重出血的令人不安的催化剂
Pub Date : 2024-02-01 DOI: 10.36347/sjmcr.2024.v12i02.004
Chirag Sharma, Hina Patel
Uterine rupture is a disruption of the uterine scar, causing foetal expulsion into the peritoneal cavity. This condition, primarily caused by the separation of uterine scar tissue from previous caesarean surgery, reduces foetal survival and increases maternal morbidity and mortality. A 32-year-old woman with a history of four vaginal deliveries and one caesarean section was diagnosed with uterine rupture, leading to a laparotomy procedure and obstetric hysterectomy. Consistent antenatal care can prevent uterine rupture.
子宫破裂是指子宫瘢痕破裂,导致胎儿排入腹腔。这种情况主要是由之前剖腹产手术造成的子宫疤痕组织分离引起的,它降低了胎儿的存活率,增加了产妇的发病率和死亡率。一名 32 岁的产妇曾有过四次阴道分娩史和一次剖腹产史,被诊断为子宫破裂,因此接受了开腹手术和产科子宫切除术。坚持产前护理可预防子宫破裂。
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引用次数: 0
Value of the Myelogram in the Diagnosis of Gaucher Disease: Two Cases Report 骨髓造影在戈谢病诊断中的价值:两例报告
Pub Date : 2024-02-01 DOI: 10.36347/sjmcr.2024.v12i02.002
Houari Mouna, Krichal Lina, Nasfi Abdelmalek, Latifa Jalili, Ammor Abdeslam, Chaimae Errabhi, Majda Elhassouni, Tasnim Kouame, Kaoutar Bahyat, Aissaoui Fqayeh Abderrahmane, Houari Mouna
Among the most common constitutional overload enzymopathies, Gaucher disease is a rare constitutional overload disease and often caused by lysosomal enzyme deficiencies in pediatric population more than adults. The cause of Gaucher disease is a deficiency of glucocerebrosidase resulting in an accumulation of glucocerebroside) in macrophages. These abundant macrophages are present in the lymphoid tissues (spleen, liver, marrow, lymph node), some of which have a characteristic morphological appearance (Gaucher cell) allowing the diagnosis to be suggested during myelogram. Reporting two cases of adult patients in whom the demonstration of overload cells in the myelogram allowed us to direct towards the diagnosis of Gaucher disease.
在最常见的体质性超负荷酶病中,戈谢病是一种罕见的体质性超负荷疾病,通常是由溶酶体酶缺乏引起的,在儿童中的发病率高于成人。戈谢病的病因是葡萄糖脑苷脂酶缺乏,导致巨噬细胞中的葡萄糖苷积累。这些大量的巨噬细胞存在于淋巴组织(脾脏、肝脏、骨髓、淋巴结)中,其中一些具有特征性的形态学外观(戈谢病细胞),因此在进行骨髓造影时可提示诊断。报告了两例成年患者,他们的骨髓造影显示出超负荷细胞,使我们能够做出戈谢病的诊断。
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引用次数: 0
Contribution of Computed Tomography in the Diagnosis of Multifocal Non-Hodgkin’s Lymphoma at the Mother-Child University Hospital the ‘’Luxembourg’’ About a Case 卢森堡母婴大学医院计算机断层扫描在诊断多灶性非霍奇金淋巴瘤中的贡献--关于一个病例
Pub Date : 2024-01-09 DOI: 10.36347/sjmcr.2024.v12i01.007
Alassane Kouma, Sylvain Coulibaly, Mamadou Dembélé, Moussa Konate, M. N’diaye, H. Diarra, Seydou Ly, Issa Cissé, S. Sanogo, Cheick Zoumana Berete, Soumaïla Keïta, Adama Diaman Keïta, Siaka Sidibé
Lymphoma is a malignant proliferation of lymphoid tissue cells. We report a case of multi-focal lymphoma of lymph node, pharyngeal, cardiac and splenic sites. This was a 19-year-old patient received in February 2023, at the radiology and medical imaging department of the Mother and Child University Hospital Center ''Luxembourg'' as part of the CT exploration of a lateral mass. -left cervical. On admission, the clinical examination found a patient with an altered general condition, moderately colored conjunctiva, normal blood pressure and temperature. Examination of the lymph node areas revealed a left latero-cervical swelling, and fixed bilateral axillary swellings, of firm consistency and irregular contours. Palpation revealed hepatosplenomegaly. Cardiopulmonary auscultation was normal. A cervico-thoraco-abdominal CT scan revealed irregular thickening of the left lateral wall of the oropharynx, a hypodense tissue mass in the right cardiac chambers, heterogeneous splenomegaly, cervical, mediastinal, axillary and abdominal ADP. The histological examination carried out after lymph node biopsy revealed a histological appearance of small cell lymphoma. Conclusion: Lymphoma is a very common malignant tumor that can occur at any age. This tumor can affect all organs, however its cardiac location is rare. The positive diagnosis remains histological. Imaging plays an important role in the initial assessment, extension and surveillance.
淋巴瘤是淋巴组织细胞的恶性增生。我们报告了一例淋巴结、咽部、心脏和脾脏多灶性淋巴瘤病例。这是一名 19 岁的患者,于 2023 年 2 月在卢森堡母婴大学医院中心的放射科和医学影像科接受检查,当时正在对侧方肿块进行 CT 检查。-左颈椎。入院时,临床检查发现患者全身状况改变,结膜颜色适中,血压和体温正常。淋巴结区检查发现左侧颈后肿物,双侧腋窝固定肿物,质地坚硬,轮廓不规则。触诊发现肝脾肿大。心肺听诊正常。颈胸腹CT扫描显示口咽部左侧壁不规则增厚,右心腔有低密度组织肿块,脾脏异型肿大,颈部、纵隔、腋窝和腹部有ADP。淋巴结活检后的组织学检查显示其组织学表现为小细胞淋巴瘤。结论:淋巴瘤是一种非常常见的恶性肿瘤:淋巴瘤是一种非常常见的恶性肿瘤,可发生于任何年龄。这种肿瘤可累及所有器官,但位于心脏的淋巴瘤却很少见。阳性诊断仍然是组织学诊断。影像学检查在初步评估、扩展和监测方面发挥着重要作用。
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引用次数: 0
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Scholars Journal of Medical Case Reports
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