Ignacio Morales-Rey, Elena Sandoval, Mykhailo Kryvetskyi, Daniel Pereda
Robotic aortic valve replacement is the latest advance in the field of aortic valve intervention and is increasingly being adopted by various centres with favourable early results. It allows surgeons to implant any commercially available aortic valve prosthesis (sutureless, biological, mechanical) in a surgically conventional manner, while offering minimal surgical trauma (sternum-free, rib-free, pectoralis muscle sparing). We present a step-by-step standardized procedure of robotic aortic valve replacement with a mechanical prosthesis for a young female patient with severe symptomatic aortic valve stenosis in a unicuspid aortic valve.
{"title":"Robotic aortic valve replacement with a mechanical prosthesis: procedural steps.","authors":"Ignacio Morales-Rey, Elena Sandoval, Mykhailo Kryvetskyi, Daniel Pereda","doi":"10.1510/mmcts.2025.144","DOIUrl":"10.1510/mmcts.2025.144","url":null,"abstract":"<p><p>Robotic aortic valve replacement is the latest advance in the field of aortic valve intervention and is increasingly being adopted by various centres with favourable early results. It allows surgeons to implant any commercially available aortic valve prosthesis (sutureless, biological, mechanical) in a surgically conventional manner, while offering minimal surgical trauma (sternum-free, rib-free, pectoralis muscle sparing). We present a step-by-step standardized procedure of robotic aortic valve replacement with a mechanical prosthesis for a young female patient with severe symptomatic aortic valve stenosis in a unicuspid aortic valve.</p>","PeriodicalId":53474,"journal":{"name":"Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery","volume":"2026 ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2026-01-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145913822","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Marco Mammana, Giovanni Zambello, Alberto Busetto, Giuseppe Cataldi, Francesco Zaraca, Andrea Dell'Amore
This video tutorial presents a step-by-step description of percutaneous lung nodule localization performed in a hybrid operating room using indocyanine green and Lipiodol under cone-beam computed tomography guidance. Preoperative localization is indicated when the surgeon anticipates difficulty identifying a pulmonary nodule by digital palpation during video-assisted thoracoscopic surgery. The combined use of indocyanine green fluorescence and fluoroscopy allows accurate intraoperative detection and confirmation of adequate resection margins.
{"title":"Step-by-step lung nodule localization in the hybrid operating room using a double marking technique with Lipiodol and indocyanine green.","authors":"Marco Mammana, Giovanni Zambello, Alberto Busetto, Giuseppe Cataldi, Francesco Zaraca, Andrea Dell'Amore","doi":"10.1510/mmcts.2025.133","DOIUrl":"https://doi.org/10.1510/mmcts.2025.133","url":null,"abstract":"<p><p>This video tutorial presents a step-by-step description of percutaneous lung nodule localization performed in a hybrid operating room using indocyanine green and Lipiodol under cone-beam computed tomography guidance. Preoperative localization is indicated when the surgeon anticipates difficulty identifying a pulmonary nodule by digital palpation during video-assisted thoracoscopic surgery. The combined use of indocyanine green fluorescence and fluoroscopy allows accurate intraoperative detection and confirmation of adequate resection margins.</p>","PeriodicalId":53474,"journal":{"name":"Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery","volume":"2026 ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2026-01-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145913809","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Yuriy Stukov, Chasen Croft, Anne-Marie Fassler, Bruce Steinberg, Alexandra Campbell, Jeffrey P Jacobs, Letitia Bible
Blunt diaphragmatic rupture is a rare injury with a high mortality rate. The pathophysiological mechanism of diaphragmatic rupture is hypothesized as an increase in intra-abdominal pressure leading to muscular disruption and subsequent visceral herniation into the pleural cavity. Left-side ruptures are more common, as the right side is protected by the liver. Abdominal contents occupying the chest cavity can become ischaemic or could have been injured during the initial trauma and, additionally, might significantly compress the lung, leading to a variety of clinical presentations ranging from chest pain and peritonitis to increased rate of breathing or respiratory distress. In this video tutorial, we present a polytrauma patient after a motor vehicle collision, who sustained traumatic diaphragmatic rupture and left chest wall herniation.
{"title":"Traumatic diaphragmatic rupture and left chest wall herniation.","authors":"Yuriy Stukov, Chasen Croft, Anne-Marie Fassler, Bruce Steinberg, Alexandra Campbell, Jeffrey P Jacobs, Letitia Bible","doi":"10.1510/mmcts.2025.131","DOIUrl":"10.1510/mmcts.2025.131","url":null,"abstract":"<p><p>Blunt diaphragmatic rupture is a rare injury with a high mortality rate. The pathophysiological mechanism of diaphragmatic rupture is hypothesized as an increase in intra-abdominal pressure leading to muscular disruption and subsequent visceral herniation into the pleural cavity. Left-side ruptures are more common, as the right side is protected by the liver. Abdominal contents occupying the chest cavity can become ischaemic or could have been injured during the initial trauma and, additionally, might significantly compress the lung, leading to a variety of clinical presentations ranging from chest pain and peritonitis to increased rate of breathing or respiratory distress. In this video tutorial, we present a polytrauma patient after a motor vehicle collision, who sustained traumatic diaphragmatic rupture and left chest wall herniation.</p>","PeriodicalId":53474,"journal":{"name":"Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery","volume":"2026 ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2026-01-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145913853","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Henrique Soares Moreira, Alessia Cannone, José Máximo, Elson Salgueiro, Joel Sousa, Rui Cerqueira, Adelino Leite-Moreira
Open surgery remains an essential alternative for descending thoracic aortic aneurysms repair when anatomical constraints preclude endovascular intervention. We present the case of a 63-year-old woman with a complex pseudoaneurysm located at the junction of the distal aortic arch and proximal descending aorta (zones 3/4), approximately 7 mm distal to the origin of the left subclavian artery. The absence of a proximal landing zone rendered thoracic endovascular aortic repair unfeasible. A limited left thoracotomy was performed at the fourth intercostal space. Cardiopulmonary bypass was established with femoral venous and double arterial cannulation (aortic arch and distal thoracic descending aorta). A debranching bypass to the left subclavian artery was created using an 8 mm graft. After proximal and distal clamping, the pseudoaneurysm was resected and replaced with a bevelled 32 mm Dacron graft. Long-shafted instruments under video-assistance enabled precise dissection despite limited exposure and dense adhesions. The patient had an uneventful recovery, with no neurological complications and timely discharge. This case illustrates that open aortic repair can be safely and effectively performed through less invasive access in anatomically complex situations. Incorporating modern techniques allows the refinement of open surgery, preserving its relevance in contemporary thoracic aortic management.
{"title":"Video-assisted open repair of proximal thoracic aortic pseudoaneurysm.","authors":"Henrique Soares Moreira, Alessia Cannone, José Máximo, Elson Salgueiro, Joel Sousa, Rui Cerqueira, Adelino Leite-Moreira","doi":"10.1510/mmcts.2025.136","DOIUrl":"https://doi.org/10.1510/mmcts.2025.136","url":null,"abstract":"<p><p>Open surgery remains an essential alternative for descending thoracic aortic aneurysms repair when anatomical constraints preclude endovascular intervention. We present the case of a 63-year-old woman with a complex pseudoaneurysm located at the junction of the distal aortic arch and proximal descending aorta (zones 3/4), approximately 7 mm distal to the origin of the left subclavian artery. The absence of a proximal landing zone rendered thoracic endovascular aortic repair unfeasible. A limited left thoracotomy was performed at the fourth intercostal space. Cardiopulmonary bypass was established with femoral venous and double arterial cannulation (aortic arch and distal thoracic descending aorta). A debranching bypass to the left subclavian artery was created using an 8 mm graft. After proximal and distal clamping, the pseudoaneurysm was resected and replaced with a bevelled 32 mm Dacron graft. Long-shafted instruments under video-assistance enabled precise dissection despite limited exposure and dense adhesions. The patient had an uneventful recovery, with no neurological complications and timely discharge. This case illustrates that open aortic repair can be safely and effectively performed through less invasive access in anatomically complex situations. Incorporating modern techniques allows the refinement of open surgery, preserving its relevance in contemporary thoracic aortic management.</p>","PeriodicalId":53474,"journal":{"name":"Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery","volume":"2025 ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2025-12-17","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145913858","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Yaroslav Ivanov, Yaroslav Mykychak, Kira Kuschnerus, Maren Kleine-Brueggeney, Alexander Mladenow, Olivier Miera, Mi-Young Cho, Joachim Photiadis
This video tutorial presents the case of surgical correction of left outflow tract obstruction after atrioventricular septal defect repair. The left outflow tract obstruction was presented as a fixed fibromuscular membrane combined with accessory tissues from the left atrioventricular valve. The surgical correction included fibromuscular membrane resection combined with myotomy and resection of additional tissues arising from the atrioventricular valve. The repair was conducted via a transaortic approach. Post-operative echocardiography demonstrated a good result of the surgery without flow acceleration across the left ventricular outflow tract and minimal aortic valve insufficiency. The patient is doing well at 7 months follow-up.
{"title":"Left ventricular outflow tract obstruction repair after atrioventricular septal defect correction.","authors":"Yaroslav Ivanov, Yaroslav Mykychak, Kira Kuschnerus, Maren Kleine-Brueggeney, Alexander Mladenow, Olivier Miera, Mi-Young Cho, Joachim Photiadis","doi":"10.1510/mmcts.2025.134","DOIUrl":"10.1510/mmcts.2025.134","url":null,"abstract":"<p><p>This video tutorial presents the case of surgical correction of left outflow tract obstruction after atrioventricular septal defect repair. The left outflow tract obstruction was presented as a fixed fibromuscular membrane combined with accessory tissues from the left atrioventricular valve. The surgical correction included fibromuscular membrane resection combined with myotomy and resection of additional tissues arising from the atrioventricular valve. The repair was conducted via a transaortic approach. Post-operative echocardiography demonstrated a good result of the surgery without flow acceleration across the left ventricular outflow tract and minimal aortic valve insufficiency. The patient is doing well at 7 months follow-up.</p>","PeriodicalId":53474,"journal":{"name":"Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery","volume":"2025 ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2025-12-17","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145913879","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Filipe Tomasi Keppen Sequeira de Almeida, Mykhailo Kryvetskyi, Maria Ascaso, Robert Pruna-Guillen, Simone Gasser, Eduard Quintana
This video tutorial explains how to treat an aortic aneurysm affecting the arch, descending, and thoracoabdominal segments, in the presence of an anatomical aortic arch variation. The procedure involves replacing the entire aortic arch and ascending aorta using the classic elephant trunk technique, creating a platform for a planned staged endovascular treatment. Special emphasis is placed on cerebral protection strategies, including preservation of an anomalous left vertebral artery and special reinforcement of a distal arch anastomosis. The presence of an anomalous artery arising directly from the aortic arch increased the technical difficulty, requiring customized revascularization to ensure appropriate left posterior cerebral circulation. This case reinforces the idea that open techniques can be safe for selected elderly patients with complex anatomies, highlighting the importance of tailored strategies and careful surgical execution.
{"title":"Total arch replacement and classic elephant trunk in a patient with an anomalous left vertebral artery.","authors":"Filipe Tomasi Keppen Sequeira de Almeida, Mykhailo Kryvetskyi, Maria Ascaso, Robert Pruna-Guillen, Simone Gasser, Eduard Quintana","doi":"10.1510/mmcts.2025.138","DOIUrl":"10.1510/mmcts.2025.138","url":null,"abstract":"<p><p>This video tutorial explains how to treat an aortic aneurysm affecting the arch, descending, and thoracoabdominal segments, in the presence of an anatomical aortic arch variation. The procedure involves replacing the entire aortic arch and ascending aorta using the classic elephant trunk technique, creating a platform for a planned staged endovascular treatment. Special emphasis is placed on cerebral protection strategies, including preservation of an anomalous left vertebral artery and special reinforcement of a distal arch anastomosis. The presence of an anomalous artery arising directly from the aortic arch increased the technical difficulty, requiring customized revascularization to ensure appropriate left posterior cerebral circulation. This case reinforces the idea that open techniques can be safe for selected elderly patients with complex anatomies, highlighting the importance of tailored strategies and careful surgical execution.</p>","PeriodicalId":53474,"journal":{"name":"Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery","volume":"2025 ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2025-12-09","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145710238","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Michele Galeazzi, Erlil Mali, Paolo Berretta, Francesca Spagnolo, Vittoria Fontana, Carlo Zingaro, Mariano Cefarelli, Marco Di Eusanio
The right transaxillary direct-view approach offers substantial advantages over conventional sternotomy when dealing with mitral valve pathology, including reduced post-operative pain, faster recovery and preserved respiratory function. However, its application in patients with complex thoracic deformities remains limited. We report a minimally invasive mitral valve repair in a young woman with severe chest wall deformity and suspected connective tissue disorder. Thorough pre-operative imaging evaluation and tailored surgical planning are crucial to ensure procedural safety and optimal outcomes. Once pre-operative assessment was completed, the procedure was smoothly performed according to our standard technique. Hence, this experience supports the feasibility and safety of the transaxillary approach in selected patients with thoracic deformities, providing excellent functional and cosmetic results, and enhancing recovery.
{"title":"Transaxillary direct-view mitral valve repair in a young patient with severe chest deformity.","authors":"Michele Galeazzi, Erlil Mali, Paolo Berretta, Francesca Spagnolo, Vittoria Fontana, Carlo Zingaro, Mariano Cefarelli, Marco Di Eusanio","doi":"10.1510/mmcts.2025.137","DOIUrl":"10.1510/mmcts.2025.137","url":null,"abstract":"<p><p>The right transaxillary direct-view approach offers substantial advantages over conventional sternotomy when dealing with mitral valve pathology, including reduced post-operative pain, faster recovery and preserved respiratory function. However, its application in patients with complex thoracic deformities remains limited. We report a minimally invasive mitral valve repair in a young woman with severe chest wall deformity and suspected connective tissue disorder. Thorough pre-operative imaging evaluation and tailored surgical planning are crucial to ensure procedural safety and optimal outcomes. Once pre-operative assessment was completed, the procedure was smoothly performed according to our standard technique. Hence, this experience supports the feasibility and safety of the transaxillary approach in selected patients with thoracic deformities, providing excellent functional and cosmetic results, and enhancing recovery.</p>","PeriodicalId":53474,"journal":{"name":"Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery","volume":"2025 ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2025-12-02","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145656299","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Valeria Megretsky, Ibrahim Mashni, Harbi Khalayleh, Guy Pines
Ectopic parathyroid adenomas present a diagnostic and surgical challenge, particularly when located in anatomically complex regions such as the middle mediastinum. This report describes the case of a 76-year-old male with primary hyperparathyroidism caused by a parathyroid adenoma situated anterior to the oesophagus and beneath the aortic arch. Robotic-assisted thoracoscopic resection enabled precise, minimally invasive excision with successful post-operative biochemical resolution. This case highlights the evolving role of robotic techniques in endocrine and thoracic surgery.
{"title":"Robotic resection of parathyroid adenoma in the middle mediastinum.","authors":"Valeria Megretsky, Ibrahim Mashni, Harbi Khalayleh, Guy Pines","doi":"10.1510/mmcts.2025.109","DOIUrl":"https://doi.org/10.1510/mmcts.2025.109","url":null,"abstract":"<p><p>Ectopic parathyroid adenomas present a diagnostic and surgical challenge, particularly when located in anatomically complex regions such as the middle mediastinum. This report describes the case of a 76-year-old male with primary hyperparathyroidism caused by a parathyroid adenoma situated anterior to the oesophagus and beneath the aortic arch. Robotic-assisted thoracoscopic resection enabled precise, minimally invasive excision with successful post-operative biochemical resolution. This case highlights the evolving role of robotic techniques in endocrine and thoracic surgery.</p>","PeriodicalId":53474,"journal":{"name":"Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery","volume":"2025 ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2025-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145650079","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
A 67-year-old female presented with progressive dysphagia to solids and liquids. Imaging was concerning for end-stage achalasia with multiple failed attempts at pneumatic dilation. An outside hospital recommended oesophagectomy, but she came to our clinic for a second opinion. Computed tomography revealed tortuous megaoesophagus measuring up to 7 cm. Barium swallow revealed aperistalsis. Oesophageal manometry revealed an elevated integrated relaxation pressure, 100% failed peristalsis and panoesophageal pressurization in >20% of swallows, consistent with type II achalasia. We recommended a robotic Heller myotomy and Dor fundoplication. The patient was positioned supine with four 8 mm ports across the mid-abdomen. The pars flaccida was opened to access the right crus and oesophageal hiatus. The phreno-oesophageal ligament was taken down and the dissection was carried cephalad into the mediastinum. The greater sac was opened and the short gastric vessels and gastrosplenic ligament were taken down. The gastro-oesophageal junction fat pad was resected. A myotomy was created using a robotic hook without energy extending 6 cm on the oesophagus and 2 cm over the stomach. Modified Dor fundoplication was completed using four interrupted sutures. The patient was given a soft diet and discharged on post-operative Day 1. She subsequently had complete resolution of her dysphagia.
{"title":"Robotic Heller myotomy and modified Dor fundoplication.","authors":"Alexander Pohlman, Zaid M Abdelsattar","doi":"10.1510/mmcts.2025.124","DOIUrl":"10.1510/mmcts.2025.124","url":null,"abstract":"<p><p>A 67-year-old female presented with progressive dysphagia to solids and liquids. Imaging was concerning for end-stage achalasia with multiple failed attempts at pneumatic dilation. An outside hospital recommended oesophagectomy, but she came to our clinic for a second opinion. Computed tomography revealed tortuous megaoesophagus measuring up to 7 cm. Barium swallow revealed aperistalsis. Oesophageal manometry revealed an elevated integrated relaxation pressure, 100% failed peristalsis and panoesophageal pressurization in >20% of swallows, consistent with type II achalasia. We recommended a robotic Heller myotomy and Dor fundoplication. The patient was positioned supine with four 8 mm ports across the mid-abdomen. The pars flaccida was opened to access the right crus and oesophageal hiatus. The phreno-oesophageal ligament was taken down and the dissection was carried cephalad into the mediastinum. The greater sac was opened and the short gastric vessels and gastrosplenic ligament were taken down. The gastro-oesophageal junction fat pad was resected. A myotomy was created using a robotic hook without energy extending 6 cm on the oesophagus and 2 cm over the stomach. Modified Dor fundoplication was completed using four interrupted sutures. The patient was given a soft diet and discharged on post-operative Day 1. She subsequently had complete resolution of her dysphagia.</p>","PeriodicalId":53474,"journal":{"name":"Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery","volume":"2025 ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2025-11-19","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145551894","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Ebstein's anomaly is a rare congenital heart defect characterized by tricuspid valve malformation and right ventricular myopathy. The "cone procedure," introduced by Dr. José Pedro da Silva, represents a major advancement in the repair of Ebstein's anomaly, achieving near-anatomical tricuspid valve reconstruction. We describe the case of a 23-year-old-female with Carpentier type B Ebstein's anomaly, severe tricuspid regurgitation and Wolff-Parkinson-White syndrome, who underwent cone reconstruction combined with right ventricular resection. Detailed preoperative imaging guided the procedure, ensuring precise leaflet mobilization, delamination and cone creation. The atrialized right ventricular portion was reduced via triangular resection, preserving right ventricular geometry. An annuloplasty ring stabilized the repair. Postoperatively, the patient demonstrated excellent recovery, with trivial regurgitation and preserved right ventricular function confirmed at the one-year follow-up. This case highlights the reproducibility and effectiveness of the cone repair, supporting its role as the primary surgical approach for Ebstein's anomaly. Key factors for success include meticulous leaflet delamination, ensuring a complete 360° cone structure and maintaining RV geometry. Although long-term outcomes require further evaluation, the cone procedure offers superior valve competence and symptom relief compared to traditional repairs, minimizing the need for reoperation.
Ebstein异常是一种罕见的先天性心脏缺陷,以三尖瓣畸形和右心室肌病为特征。由jos Pedro da Silva医生介绍的“锥体手术”代表了Ebstein畸形修复的重大进步,实现了接近解剖的三尖瓣重建。我们描述了一例23岁的女性,患有卡彭蒂埃B型Ebstein异常,严重的三尖瓣反流和沃尔夫-帕金森-怀特综合征,她接受了锥体重建和右心室切除术。详细的术前影像指导手术,确保精确的小叶动员、分层和锥体形成。通过三角形切除减少心房化的右心室部分,保留了右心室的几何形状。一个环成形术环稳定修复。术后,患者表现出良好的恢复,在一年的随访中证实了轻微的反流和保留的右心室功能。本病例强调了椎体修复的可重复性和有效性,支持其作为Ebstein畸形的主要手术入路的作用。成功的关键因素包括细致的小叶剥离,确保完整的360°锥体结构和保持RV几何形状。虽然长期结果需要进一步评估,但与传统修复相比,锥形手术提供了更好的瓣膜功能和症状缓解,最大限度地减少了再次手术的需要。
{"title":"Cone repair and right ventricular resection in an adult patient with Ebstein's anomaly.","authors":"Federica Torchio, Alessandro Varrica, Massimo Chessa, Alessandro Giamberti","doi":"10.1510/mmcts.2025.116","DOIUrl":"10.1510/mmcts.2025.116","url":null,"abstract":"<p><p>Ebstein's anomaly is a rare congenital heart defect characterized by tricuspid valve malformation and right ventricular myopathy. The \"cone procedure,\" introduced by Dr. José Pedro da Silva, represents a major advancement in the repair of Ebstein's anomaly, achieving near-anatomical tricuspid valve reconstruction. We describe the case of a 23-year-old-female with Carpentier type B Ebstein's anomaly, severe tricuspid regurgitation and Wolff-Parkinson-White syndrome, who underwent cone reconstruction combined with right ventricular resection. Detailed preoperative imaging guided the procedure, ensuring precise leaflet mobilization, delamination and cone creation. The atrialized right ventricular portion was reduced via triangular resection, preserving right ventricular geometry. An annuloplasty ring stabilized the repair. Postoperatively, the patient demonstrated excellent recovery, with trivial regurgitation and preserved right ventricular function confirmed at the one-year follow-up. This case highlights the reproducibility and effectiveness of the cone repair, supporting its role as the primary surgical approach for Ebstein's anomaly. Key factors for success include meticulous leaflet delamination, ensuring a complete 360° cone structure and maintaining RV geometry. Although long-term outcomes require further evaluation, the cone procedure offers superior valve competence and symptom relief compared to traditional repairs, minimizing the need for reoperation.</p>","PeriodicalId":53474,"journal":{"name":"Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery","volume":"2025 ","pages":""},"PeriodicalIF":0.0,"publicationDate":"2025-11-19","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"145551920","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}