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Paediatric cystic fibrosis (CF)最新文献

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Recommended shielding against SARS-CoV-2 impacts physical activity levels and adherence to airway clearance therapy in patients with cystic fibrosis 建议屏蔽SARS-CoV-2会影响囊性纤维化患者的身体活动水平和对气道清除治疗的依从性
Pub Date : 2021-09-05 DOI: 10.1183/13993003.congress-2021.pa3371
E. Hatziagorou, I. Toulia, P. Peftoulidou, Eleana Kouroukli, E. Tasika, E. Chrysochoou, J. Tsanakas
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引用次数: 0
Late Breaking Abstract - Lessons from introducing DEKAs as a means of vitamin supplementation in paediatric Cystic Fibrosis patients 最新突破摘要-引入deka作为儿科囊性纤维化患者维生素补充手段的经验教训
Pub Date : 2021-09-05 DOI: 10.1183/13993003.congress-2021.pa3380
Elizabeth Bearblock, D. Mcshane, H. Milroy, S. Aldridge, D. Kotzia
{"title":"Late Breaking Abstract - Lessons from introducing DEKAs as a means of vitamin supplementation in paediatric Cystic Fibrosis patients","authors":"Elizabeth Bearblock, D. Mcshane, H. Milroy, S. Aldridge, D. Kotzia","doi":"10.1183/13993003.congress-2021.pa3380","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3380","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"2 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115379359","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Lung function in children with cystic fibrosis liver disease 囊性纤维化肝病患儿肺功能的研究
Pub Date : 2021-09-05 DOI: 10.1183/13993003.congress-2021.pa3376
D. Popin, L. Pop, M. Dediu, C. Pienar, Laura Savu, I. Ciuca
{"title":"Lung function in children with cystic fibrosis liver disease","authors":"D. Popin, L. Pop, M. Dediu, C. Pienar, Laura Savu, I. Ciuca","doi":"10.1183/13993003.congress-2021.pa3376","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3376","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"32 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"134183891","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
RCT Abstract - The effect of inhaled hypertonic saline on lung structure in preschool children with cystic fibrosis 摘要:吸入高渗盐水对学龄前囊性纤维化患儿肺结构的影响
Pub Date : 2021-09-05 DOI: 10.1183/13993003.congress-2021.pa3382
H. Tiddens, Yu-Xin Chen, E. Andrinopoulou, S. Davis, M. Rosenfeld, F. Ratjen, R. Kronmal, K. D. Stukovsky, S. Stick
{"title":"RCT Abstract - The effect of inhaled hypertonic saline on lung structure in preschool children with cystic fibrosis","authors":"H. Tiddens, Yu-Xin Chen, E. Andrinopoulou, S. Davis, M. Rosenfeld, F. Ratjen, R. Kronmal, K. D. Stukovsky, S. Stick","doi":"10.1183/13993003.congress-2021.pa3382","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3382","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"24 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"113968463","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
TNF and LTA gene polymorphisms in cystic fibrosis patients with Burkholderia cepacia complex (Bcc) 囊性纤维化伴洋葱伯克霍尔德菌复合体(Bcc)患者TNF和LTA基因多态性
Pub Date : 2021-09-05 DOI: 10.1183/13993003.congress-2021.pa2105
D. Pukhalskaya, V. Shmarin, T. Bukina, S. Krasovsky, S. Semykin, M. Usacheva, L. Avakian, N. Kashirskaya, G. Shmarina
{"title":"TNF and LTA gene polymorphisms in cystic fibrosis patients with Burkholderia cepacia complex (Bcc)","authors":"D. Pukhalskaya, V. Shmarin, T. Bukina, S. Krasovsky, S. Semykin, M. Usacheva, L. Avakian, N. Kashirskaya, G. Shmarina","doi":"10.1183/13993003.congress-2021.pa2105","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa2105","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"863 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"123781894","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Changes in the Lung Clearance Index outside 15% are clinically relevant in children with cystic fibrosis 肺清除率指数在15%以上的变化与囊性纤维化儿童有临床相关性
Pub Date : 2021-09-05 DOI: 10.1183/13993003.congress-2021.oa2672
L. Perrem, S. Stanojevic, S. Davis, D. Sanders, R. Jensen, M. Shaw, M. Solomon, H. Grasemann, V. Waters, N. Sweezey, N. Mcdonald, Julia Guido, C. Clem, F. Ratjen
{"title":"Changes in the Lung Clearance Index outside 15% are clinically relevant in children with cystic fibrosis","authors":"L. Perrem, S. Stanojevic, S. Davis, D. Sanders, R. Jensen, M. Shaw, M. Solomon, H. Grasemann, V. Waters, N. Sweezey, N. Mcdonald, Julia Guido, C. Clem, F. Ratjen","doi":"10.1183/13993003.congress-2021.oa2672","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.oa2672","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"20 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"126904568","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 1
LSC - 2021 - Effect of elexacaftor-tezacaftor-ivacaftor on pulmonary and endothelial function in a patient with advanced cystic fibrosis LSC - 2021 - elexaftor -tezacaftor-ivacaftor对晚期囊性纤维化患者肺和内皮功能的影响
Pub Date : 2021-09-05 DOI: 10.1183/13993003.congress-2021.pa2104
Rink Saša, M. Janić, M. Šabovič, B. Salobir
{"title":"LSC - 2021 - Effect of elexacaftor-tezacaftor-ivacaftor on pulmonary and endothelial function in a patient with advanced cystic fibrosis","authors":"Rink Saša, M. Janić, M. Šabovič, B. Salobir","doi":"10.1183/13993003.congress-2021.pa2104","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa2104","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"198 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"124237062","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Inflammation in cystic fibrosis patients: study of the eicosanoid pathway and severity correlations 囊性纤维化患者的炎症:类二十烷途径和严重程度相关性的研究
Pub Date : 2021-09-05 DOI: 10.1183/13993003.congress-2021.pa2106
S. Gartner, P. Fernández-Álvarez, I. Lima, S. Rovira, C. Picado, E. García-Arumí, Inés De Mir, A. Torrent, A. Moreno, I. Iglesias, E. Tizzano
{"title":"Inflammation in cystic fibrosis patients: study of the eicosanoid pathway and severity correlations","authors":"S. Gartner, P. Fernández-Álvarez, I. Lima, S. Rovira, C. Picado, E. García-Arumí, Inés De Mir, A. Torrent, A. Moreno, I. Iglesias, E. Tizzano","doi":"10.1183/13993003.congress-2021.pa2106","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa2106","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"15 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128031025","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 1
Late Breaking Abstract - Can individualised skin prick tests detect sensitisations against colonising fungal species in cystic fibrosis patients? 摘要-个体化皮肤点刺试验能否检测囊性纤维化患者对定植真菌的敏感性?
Pub Date : 2021-09-05 DOI: 10.1183/13993003.congress-2021.pa3381
S. Zanella, V. Strenger, W. Buzina, Sophie Kienreich, M. Egger, A. Pfleger, E. Eber
{"title":"Late Breaking Abstract - Can individualised skin prick tests detect sensitisations against colonising fungal species in cystic fibrosis patients?","authors":"S. Zanella, V. Strenger, W. Buzina, Sophie Kienreich, M. Egger, A. Pfleger, E. Eber","doi":"10.1183/13993003.congress-2021.pa3381","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa3381","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"130000438","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Real-world effects of lumacaftor/ivacaftor (LUM/IVA) in people with cystic fibrosis (pwCF): interim results of a long-term safety study using US CF Foundation Patient Registry (CFFPR) data lumacaftor/ivacaftor (LUM/IVA)对囊性纤维化(pwCF)患者的实际影响:使用美国CF基金会患者登记(cfpr)数据的长期安全性研究的中期结果
Pub Date : 2021-09-05 DOI: 10.1183/13993003.congress-2021.pa2098
C. Kim, Christopher Lee, R. Zahigian, N. Nair, A. Sewall, A. Elbert
{"title":"Real-world effects of lumacaftor/ivacaftor (LUM/IVA) in people with cystic fibrosis (pwCF): interim results of a long-term safety study using US CF Foundation Patient Registry (CFFPR) data","authors":"C. Kim, Christopher Lee, R. Zahigian, N. Nair, A. Sewall, A. Elbert","doi":"10.1183/13993003.congress-2021.pa2098","DOIUrl":"https://doi.org/10.1183/13993003.congress-2021.pa2098","url":null,"abstract":"","PeriodicalId":307768,"journal":{"name":"Paediatric cystic fibrosis (CF)","volume":"58 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2021-09-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"131932479","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
期刊
Paediatric cystic fibrosis (CF)
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