Pub Date : 2017-07-05DOI: 10.20418/JRCD.VOL3NO3.285
Fateh Ali Tipoo Sultan, Y. Hasan
Endomyocardial fibrosis (EMF) is a rare disease of unknown etiology which is more prevalent in tropical countries. EMF is associated with fibrosis of endomyocardium, involving one or both ventricles. It usually presents with heart failure and has a poor prognosis. The diagnosis is usually made on echocardiogram, however cardiac magnetic resonance (CMR) is ideal for the diagnosis of EMF. We report a rare case of right ventricular endomyocardial fibrosis in a young male with chronic myeloid leukemia but no eosinophilia. Right ventricular EMF was diagnosed on the basis of classic findings on CMR. JRCD 2017; 3 (3): 98–100.
{"title":"Isolated right ventricular endomyocardial fibrosis in a young male with chronic myeloid leukemia (RCD code: III‑3F.2)","authors":"Fateh Ali Tipoo Sultan, Y. Hasan","doi":"10.20418/JRCD.VOL3NO3.285","DOIUrl":"https://doi.org/10.20418/JRCD.VOL3NO3.285","url":null,"abstract":"Endomyocardial fibrosis (EMF) is a rare disease of unknown etiology which is more prevalent in tropical countries. EMF is associated with fibrosis of endomyocardium, involving one or both ventricles. It usually presents with heart failure and has a poor prognosis. The diagnosis is usually made on echocardiogram, however cardiac magnetic resonance (CMR) is ideal for the diagnosis of EMF. We report a rare case of right ventricular endomyocardial fibrosis in a young male with chronic myeloid leukemia but no eosinophilia. Right ventricular EMF was diagnosed on the basis of classic findings on CMR. JRCD 2017; 3 (3): 98–100.","PeriodicalId":37488,"journal":{"name":"Journal of Rare Cardiovascular Diseases","volume":"63 1","pages":"98-100"},"PeriodicalIF":0.0,"publicationDate":"2017-07-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"84123594","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2017-07-05DOI: 10.20418/JRCD.VOL3NO3.281
J. Majewski, J. Lelakowski
Myotonic dystrophy is a rare inherited condition affecting primarily skeletal muscles and commonly associated with cardiovascular pathology. We report a case of a 50- year old female with myotonic dystrophy type 1 who presented with wide‑QRS complex tachycardia and hemodynamic compromise which was treated with direct current cardioversion. Echocardiogram did not reveal any structural heart disease and coronary angiogram was normal. Electrocardiogram in sinus rhythm showed non‑specific intraventricular conduction delay and borderline PR interval. She refused cardioverter‑defibrillator (ICD) implantation and was discharged on oral amiodarone. The case report shows that life‑threatening arrhythmia could be the first cardiac manifestation in patients with myotonic dystrophy. JRCD 2017; 3 (3): 89–91.
{"title":"Broad QRS complex tachycardia in a patient with myotonic dystrophy (Steinert disease) (RCD code: V‑4O)","authors":"J. Majewski, J. Lelakowski","doi":"10.20418/JRCD.VOL3NO3.281","DOIUrl":"https://doi.org/10.20418/JRCD.VOL3NO3.281","url":null,"abstract":"Myotonic dystrophy is a rare inherited condition affecting primarily skeletal muscles and commonly associated with cardiovascular pathology. We report a case of a 50- year old female with myotonic dystrophy type 1 who presented with wide‑QRS complex tachycardia and hemodynamic compromise which was treated with direct current cardioversion. Echocardiogram did not reveal any structural heart disease and coronary angiogram was normal. Electrocardiogram in sinus rhythm showed non‑specific intraventricular conduction delay and borderline PR interval. She refused cardioverter‑defibrillator (ICD) implantation and was discharged on oral amiodarone. The case report shows that life‑threatening arrhythmia could be the first cardiac manifestation in patients with myotonic dystrophy. JRCD 2017; 3 (3): 89–91.","PeriodicalId":37488,"journal":{"name":"Journal of Rare Cardiovascular Diseases","volume":"1 1","pages":"89-91"},"PeriodicalIF":0.0,"publicationDate":"2017-07-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"88678104","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2017-07-05DOI: 10.20418/JRCD.VOL3NO3.278
Tomasz Matusik, M. Komar, J. Podolec, G. Karkowski, J. Lelakowski, P. Podolec
Sports‑associated sudden cardiac arrest (SCA) constitutes an important problem. Causes of SCA during sport activities include Brugada syndrome (BrS) among others. We describe a 29‑year‑old male, without a history of cardiovascular disease, who suffered from SCA during football training and despite intensive treatment, after almost 4 weeks of hospitalization, unfortunately died. Detailed medical documentation review showed grade I atrioventricular block, intraventricular conduction abnormalities and BrS type 2 morphology of ST-segment elevation on resting 12‑lead electrocardiogram (ECG). The patient had a history of syncope during physical activity. Further echocardiographic study did not reveal significant structural heart disease. Submaximal exercise testing was performed and showed ventricular extrasystoles during physical activity and type 1 BrS morphology of ST-segment elevation during recovery phase. We compared observed ECG changes to those present in a healthy football player and described noticeable similarities. Exercise ECG testing, especially in patients after syncope of probable arrhythmic etiology, may unmask BrS ECG pattern and lead to BrS diagnosis. JRCD 2017; 3 (3): 92–97.
{"title":"Exercise ECG unmasked Brugada sign: manifestation of the risk of sports‑associated sudden cardiac arrest (RCD code: V‑1A.1)","authors":"Tomasz Matusik, M. Komar, J. Podolec, G. Karkowski, J. Lelakowski, P. Podolec","doi":"10.20418/JRCD.VOL3NO3.278","DOIUrl":"https://doi.org/10.20418/JRCD.VOL3NO3.278","url":null,"abstract":"Sports‑associated sudden cardiac arrest (SCA) constitutes an important problem. Causes of SCA during sport activities include Brugada syndrome (BrS) among others. We describe a 29‑year‑old male, without a history of cardiovascular disease, who suffered from SCA during football training and despite intensive treatment, after almost 4 weeks of hospitalization, unfortunately died. Detailed medical documentation review showed grade I atrioventricular block, intraventricular conduction abnormalities and BrS type 2 morphology of ST-segment elevation on resting 12‑lead electrocardiogram (ECG). The patient had a history of syncope during physical activity. Further echocardiographic study did not reveal significant structural heart disease. Submaximal exercise testing was performed and showed ventricular extrasystoles during physical activity and type 1 BrS morphology of ST-segment elevation during recovery phase. We compared observed ECG changes to those present in a healthy football player and described noticeable similarities. Exercise ECG testing, especially in patients after syncope of probable arrhythmic etiology, may unmask BrS ECG pattern and lead to BrS diagnosis. JRCD 2017; 3 (3): 92–97.","PeriodicalId":37488,"journal":{"name":"Journal of Rare Cardiovascular Diseases","volume":"12 1","pages":"92-97"},"PeriodicalIF":0.0,"publicationDate":"2017-07-05","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"79160067","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2017-03-31DOI: 10.20418/JRCD.VOL3NO2.277
A. Sarnecka, P. Weryński, P. Wilkołek, L. Tomkiewicz-Pajak, M. Brózda, P. Podolec
Ventricular septal defect (VSD) is the most common congenital heart defect at birth but is relatively rare in adult population. Apart from congenital, VSD may also be acquired. It can be caused by trauma, myocardial infarction or previous cardiac surgeries such as valvular replacements or VSD closure attempts. Surgical closure of VSD remains the treatment of choice while transcatheter closure could be considered in selected patients. Herein, we present a case of a 53-year-old man with symptomatic perimembranous VSD after infective endocarditis and a history of previous primum atrial septal defect closure and prosthetic aortic and mitral valves replacement. The VSD was successfully percutaneously closed across the prosthetic aortic valve. JRCD 2017; 3 (2): 59–64
{"title":"Transcatheter closure of perimembranous ventricular septal defect with muscular VSD occluder after infective endocarditis in a patient with previous primum atrial septal defect closure, prosthetic aortic and mitral valves replacement. (RCD code IV‑2B.3)","authors":"A. Sarnecka, P. Weryński, P. Wilkołek, L. Tomkiewicz-Pajak, M. Brózda, P. Podolec","doi":"10.20418/JRCD.VOL3NO2.277","DOIUrl":"https://doi.org/10.20418/JRCD.VOL3NO2.277","url":null,"abstract":"Ventricular septal defect (VSD) is the most common congenital heart defect at birth but is relatively rare in adult population. Apart from congenital, VSD may also be acquired. It can be caused by trauma, myocardial infarction or previous cardiac surgeries such as valvular replacements or VSD closure attempts. Surgical closure of VSD remains the treatment of choice while transcatheter closure could be considered in selected patients. Herein, we present a case of a 53-year-old man with symptomatic perimembranous VSD after infective endocarditis and a history of previous primum atrial septal defect closure and prosthetic aortic and mitral valves replacement. The VSD was successfully percutaneously closed across the prosthetic aortic valve. JRCD 2017; 3 (2): 59–64","PeriodicalId":37488,"journal":{"name":"Journal of Rare Cardiovascular Diseases","volume":"43 1","pages":"59-64"},"PeriodicalIF":0.0,"publicationDate":"2017-03-31","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"74283637","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2017-03-31DOI: 10.20418/JRCD.VOL3NO2.275
Tariq Hamza, F. Sharkey
Fibromuscular dysplasia (FMD) is a nonatherosclerotic, noninflammatory arterial disease of unknown etiology. Histologically, FMD is classified on the basis of arterial layer involved into intimal, medial and perimedial types. The medial form represents approximately 80% of the cases of FMD, perimedial and intimal forms are rare and account for 10% and 5% of the cases respectively. Clinically, FMD can manifest as arterial stenosis, occlusion, aneurysm or dissection. Coronary artery manifestations of FMD are rare but potentially fatal. Most cases present as a dissection of the involved coronary artery or its branch, which clinically leads to unstable angina, myocardial infarction, left ventricular dysfunction, or potentially sudden cardiac death. Various recent studies have established FMD as the leading risk factor for Spontaneous Coronary Artery Dissection (SCAD). We present autopsy findings of a 71 year old woman who suffered a spontaneous dissection of the posterior descending artery secondary to FMD‑intimal type. The optimal diagnostic and treatment guidelines for SCAD secondary to FMD have not been established due to the lack of evidence. Further research into the pathogenesis, molecular and cellular biology, epidemiology and clinical management of FMD and its coronary artery manifestations is required. JRCD 2017; 3 (2): 56–58
{"title":"Spontaneous coronary artery dissection secondary to intimal fibromuscular dysplasia (RCD code: I‑1C.O)","authors":"Tariq Hamza, F. Sharkey","doi":"10.20418/JRCD.VOL3NO2.275","DOIUrl":"https://doi.org/10.20418/JRCD.VOL3NO2.275","url":null,"abstract":"Fibromuscular dysplasia (FMD) is a nonatherosclerotic, noninflammatory arterial disease of unknown etiology. Histologically, FMD is classified on the basis of arterial layer involved into intimal, medial and perimedial types. The medial form represents approximately 80% of the cases of FMD, perimedial and intimal forms are rare and account for 10% and 5% of the cases respectively. Clinically, FMD can manifest as arterial stenosis, occlusion, aneurysm or dissection. Coronary artery manifestations of FMD are rare but potentially fatal. Most cases present as a dissection of the involved coronary artery or its branch, which clinically leads to unstable angina, myocardial infarction, left ventricular dysfunction, or potentially sudden cardiac death. Various recent studies have established FMD as the leading risk factor for Spontaneous Coronary Artery Dissection (SCAD). We present autopsy findings of a 71 year old woman who suffered a spontaneous dissection of the posterior descending artery secondary to FMD‑intimal type. The optimal diagnostic and treatment guidelines for SCAD secondary to FMD have not been established due to the lack of evidence. Further research into the pathogenesis, molecular and cellular biology, epidemiology and clinical management of FMD and its coronary artery manifestations is required. JRCD 2017; 3 (2): 56–58","PeriodicalId":37488,"journal":{"name":"Journal of Rare Cardiovascular Diseases","volume":"21 1","pages":"56-58"},"PeriodicalIF":0.0,"publicationDate":"2017-03-31","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"73151802","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2017-03-31DOI: 10.20418/JRCD.VOL3NO2.284
P. Podolec
Mottos of the Rare Disease Day Dear Readers, Just few days ago, on 28th February, the tenth edition of Rare Disease Day was launched by EURORDIS and its Council for National Alliances to attract thousands people all over the world to come together to advocate for more research on rare diseases. Rare Disease Day goes globally, where all stakeholders, including patients and families, patient organizations, politicians, carers, medical professionals, researchers and industry come together to raise awareness of rare diseases through thousands of events all over the world. Among many topics, patients’ involvement in research is getting momentum. Thanks to patients’ actions, such as advocacy for research, funding research, governance of research, and last but not least participate in research, actually resulted in more research. It has been numerously underlined that research in rare diseases is a key factor as it brings hope to the millions of people living with rare disease across the world and their families. There are numerous types of research and frameworks that are important to rare disease community, including: infrastructures such as registries (databases of patients with their clinical and genetic information) and biobanks (catalogues of human biological samples), basic research to identify the cause and mechanisms of rare diseases, translational research, which focuses on using the conclusions of basic research to develop therapeutics for patients living with a rare disease, clinical research, when medicinal products are tested in humans through clinical trials, and finally research into quality of life, working conditions, social needs, integration at school, as well as multidisciplinary education of social service providers. Hopefully, all those noble initiatives will move the field forward for the good of all patients and their families. In this first issue of the Journal in 2017, we start with an interesting Review on cardiac sarcoidosis. The Original paper comes from the study group involving several centers, specializing in the treatment of pulmonary hypertension (PH) and is about non-invasive assessment of hemodynamics in PH. Then, as usual, we have several clinical cases of rare cardiovascular diseases with informative discussions and overview of the problems. Finally, there is a report from the annual meeting of the European Association of Cardiovascular Imaging (EACVI) – EuroEcho.
{"title":"“A rare day to put rare diseases in the spotlight!” “With research possibilities are limitless”","authors":"P. Podolec","doi":"10.20418/JRCD.VOL3NO2.284","DOIUrl":"https://doi.org/10.20418/JRCD.VOL3NO2.284","url":null,"abstract":"Mottos of the Rare Disease Day Dear Readers, Just few days ago, on 28th February, the tenth edition of Rare Disease Day was launched by EURORDIS and its Council for National Alliances to attract thousands people all over the world to come together to advocate for more research on rare diseases. Rare Disease Day goes globally, where all stakeholders, including patients and families, patient organizations, politicians, carers, medical professionals, researchers and industry come together to raise awareness of rare diseases through thousands of events all over the world. Among many topics, patients’ involvement in research is getting momentum. Thanks to patients’ actions, such as advocacy for research, funding research, governance of research, and last but not least participate in research, actually resulted in more research. It has been numerously underlined that research in rare diseases is a key factor as it brings hope to the millions of people living with rare disease across the world and their families. There are numerous types of research and frameworks that are important to rare disease community, including: infrastructures such as registries (databases of patients with their clinical and genetic information) and biobanks (catalogues of human biological samples), basic research to identify the cause and mechanisms of rare diseases, translational research, which focuses on using the conclusions of basic research to develop therapeutics for patients living with a rare disease, clinical research, when medicinal products are tested in humans through clinical trials, and finally research into quality of life, working conditions, social needs, integration at school, as well as multidisciplinary education of social service providers. Hopefully, all those noble initiatives will move the field forward for the good of all patients and their families. In this first issue of the Journal in 2017, we start with an interesting Review on cardiac sarcoidosis. The Original paper comes from the study group involving several centers, specializing in the treatment of pulmonary hypertension (PH) and is about non-invasive assessment of hemodynamics in PH. Then, as usual, we have several clinical cases of rare cardiovascular diseases with informative discussions and overview of the problems. Finally, there is a report from the annual meeting of the European Association of Cardiovascular Imaging (EACVI) – EuroEcho.","PeriodicalId":37488,"journal":{"name":"Journal of Rare Cardiovascular Diseases","volume":"3 1","pages":"35-36"},"PeriodicalIF":0.0,"publicationDate":"2017-03-31","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"74369835","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2017-03-31DOI: 10.20418/JRCD.VOL3NO2.269
Monika Różewicz-Juraszek, T. Hryniewiecki, K. Faber, E. Abramczuk, E. Orłowska-Baranowska, P. Szymański
We present a case of a 50 year-old woman who was referred to our department with severe symptomatic aortic stenosis and systemic mastocytosis. Conventional mechanical aortic valve replacement was performed successfully with the use of perioperative protocol based on dexamethasone, cetirizine and ranitidine. The only postoperative event was an onset of atrial fibrillation which was treated with amiodarone infusion. 8 days after surgery the patient was discharged home. JRCD 2017; 3 (2): 54–55
{"title":"Case report on aortic valve replacement in adult woman with systemic mastocytosis (RCD code: VIII)","authors":"Monika Różewicz-Juraszek, T. Hryniewiecki, K. Faber, E. Abramczuk, E. Orłowska-Baranowska, P. Szymański","doi":"10.20418/JRCD.VOL3NO2.269","DOIUrl":"https://doi.org/10.20418/JRCD.VOL3NO2.269","url":null,"abstract":"We present a case of a 50 year-old woman who was referred to our department with severe symptomatic aortic stenosis and systemic mastocytosis. Conventional mechanical aortic valve replacement was performed successfully with the use of perioperative protocol based on dexamethasone, cetirizine and ranitidine. The only postoperative event was an onset of atrial fibrillation which was treated with amiodarone infusion. 8 days after surgery the patient was discharged home. JRCD 2017; 3 (2): 54–55","PeriodicalId":37488,"journal":{"name":"Journal of Rare Cardiovascular Diseases","volume":"130 1","pages":"54-55"},"PeriodicalIF":0.0,"publicationDate":"2017-03-31","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"78760799","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2017-03-31DOI: 10.20418/JRCD.VOL3NO2.270
R. Kazimierczyk, Jasiewicz, Marta Marcinkiewicz-Siemion, Knapp, A. Lisowska, Piotr, Sobkowicz, Jerzy, R. Grzywna, Karol Adam
Background: Electrical cardiometry (EC) technique could estimate cardiac output (CO), cardiac index (CI) and other parameters related to cardiac contractility and fluid status by measuring the thoracic electrical bioimpedance. We hypothesized that EC could assess right ventricle (RV) hemodynamic function in patients diagnosed with pulmonary arterial hypertension (PAH). Results: In our pilot study, enrolling 23 PAH patients, we observed a significant correlation (r = 0.71; p <0.001) between thermodilution CO measurement results (4.59 ±1.05 l/min) and CO results obtained by EC (4.86 ±1.20 l/min) and between systemic vascular resistance calculated by EC monitor and obtained during right heart catheterization (RHC) (r = 0.68; p = 0.002). Furthermore, EC parameter index of contractility (ICON) sig‑ nificantly correlated with tricuspid annular plane systolic excursion assessed by echocardiography (r = 0.57; p = 0.01). Conclusions: RHC cannot be replaced in obtaining accurate results of CO, however EC technique provides feasible insight into RV function at the bedside or outpatient care. JRCD 2017; 3 (2): 44–49
{"title":"The pilot study of role of electrical cardiometry in non‑invasive assessment of hemodynamic parameters in patients with pulmonary arterial hypertension (RCD code: II‑1A.1)","authors":"R. Kazimierczyk, Jasiewicz, Marta Marcinkiewicz-Siemion, Knapp, A. Lisowska, Piotr, Sobkowicz, Jerzy, R. Grzywna, Karol Adam","doi":"10.20418/JRCD.VOL3NO2.270","DOIUrl":"https://doi.org/10.20418/JRCD.VOL3NO2.270","url":null,"abstract":"Background: Electrical cardiometry (EC) technique could estimate cardiac output (CO), cardiac index (CI) and other parameters related to cardiac contractility and fluid status by measuring the thoracic electrical bioimpedance. We hypothesized that EC could assess right ventricle (RV) hemodynamic function in patients diagnosed with pulmonary arterial hypertension (PAH). Results: In our pilot study, enrolling 23 PAH patients, we observed a significant correlation (r = 0.71; p <0.001) between thermodilution CO measurement results (4.59 ±1.05 l/min) and CO results obtained by EC (4.86 ±1.20 l/min) and between systemic vascular resistance calculated by EC monitor and obtained during right heart catheterization (RHC) (r = 0.68; p = 0.002). Furthermore, EC parameter index of contractility (ICON) sig‑ nificantly correlated with tricuspid annular plane systolic excursion assessed by echocardiography (r = 0.57; p = 0.01). Conclusions: RHC cannot be replaced in obtaining accurate results of CO, however EC technique provides feasible insight into RV function at the bedside or outpatient care. JRCD 2017; 3 (2): 44–49","PeriodicalId":37488,"journal":{"name":"Journal of Rare Cardiovascular Diseases","volume":"31 1","pages":"44-49"},"PeriodicalIF":0.0,"publicationDate":"2017-03-31","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"80746999","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2017-03-31DOI: 10.20418/JRCD.VOL3NO2.268
M. Gierba, E. Kwiecień, Leszek Drabik, Paweł Heród, Monika Dzieciuch-Rojek, P. Iwaszczuk, W. Płazak
Right ventricular outflow tract obstruction is a narrowing of the way that conducts blood from the right ventricle to the pulmonary ar‑ tery. Left ventricular outflow tract obstruction is a stenosis of the path that leads blood from the left ventricle to the aorta. Combination of right and left ventricular outflow tract obstruction is a very rare finding. We report a case of a 67‑year‑old male with asymptomatic bi‑ ventricular outflow tract obstruction. We discuss the clinical presentation, diagnostic procedures, treatment opportunities for the patient based on review of literature and actual recommendations. JRCD 2017; 3 (2): 50–53
{"title":"Clinically silent, right and left ventricular outflow tract obstructions in an adult patient (RCD code: IV‑3A)","authors":"M. Gierba, E. Kwiecień, Leszek Drabik, Paweł Heród, Monika Dzieciuch-Rojek, P. Iwaszczuk, W. Płazak","doi":"10.20418/JRCD.VOL3NO2.268","DOIUrl":"https://doi.org/10.20418/JRCD.VOL3NO2.268","url":null,"abstract":"Right ventricular outflow tract obstruction is a narrowing of the way that conducts blood from the right ventricle to the pulmonary ar‑ tery. Left ventricular outflow tract obstruction is a stenosis of the path that leads blood from the left ventricle to the aorta. Combination of right and left ventricular outflow tract obstruction is a very rare finding. We report a case of a 67‑year‑old male with asymptomatic bi‑ ventricular outflow tract obstruction. We discuss the clinical presentation, diagnostic procedures, treatment opportunities for the patient based on review of literature and actual recommendations. JRCD 2017; 3 (2): 50–53","PeriodicalId":37488,"journal":{"name":"Journal of Rare Cardiovascular Diseases","volume":"38 1","pages":"50-53"},"PeriodicalIF":0.0,"publicationDate":"2017-03-31","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"87585692","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2017-03-31DOI: 10.20418/JRCD.VOL3NO2.282
S. Wiśniowska-Śmiałek
EuroEcho-Imaging is the annual meeting of the European Association of Cardiovascular Imaging (EACVI), that attracts participants from all over the world with all modalities of cardiovascular non-invasive imaging. This time Congress was held in Leipzig in Germany, the city of two great artists Wilhelm Wagner and Johann Sebastian Bach. The Congress was attended by more than 3200 healthcare professionals from over 90 countries and it unified community of four imaging modalities, such as Echocardiography, Cardiovascular Magnetic Resonance, Nuclear Cardiology and Cardiac Computed Tomography under one entity. During four days of Congress over 140 scientific sessions, 20 hands-on sessions and 20 industry sponsored sessions and workshops took place. Attenders could take part in wide range of sessions dedicated to advanced imaging and had an opportunity to discussed with world-leading Imaging experts. There were over than 1250 abstracts and clinical cases submitted. Moreover participants could benefit with the certification exams and numerous courses, such as course on Congenital Heart Disease, Cardiac Resynchronization Therapy, three-dimensional echocardiography, n Imaging and Anesthesiology, Valvular Heart Disease, modern trans-catheter heart valve interventions, Cardiovascular Magnetic Resonance and finally course on Computed Tomography. The scientific programme addressed the latest developments in many fields of imaging but especially it highlighted the role of imaging in arrhythmias, aortic valve diseases and cardiomyopathies. The first theme was about he role of imaging in the prediction and stratification the risk of new or potentially life-threatening arrhythmias during the treatment .There was an interesting session entitled „“Walking dead”, in which the innovative and comprehensive approach to imaging after sudden cardiac death (SCD) was presented. The special attention was put towards the role of early imaging after SCD in ischaemic and non ischaemic diseases, and aslo in secondary prevention of SCD. There was also a session dedicated to imaging in atrial fibrillation: from diagnosis to treatment, which related to the new ESC/EACTS 2016 guidelines for the management of atrial fibrillation. The numerous aspects relating to aortic valve disease were addressed with many sessions dedicated to pathophysiology and classification of aortic valve diseases, changes in treatment, including new techniques such as percutaneous implantation of the valves, which have been adopted into the ESC Guidelines for Valvular Heart Disease. As EuroEcho Imaging Congress is a multimodality imaging meeting there were also lot of joint sessions with presentations of cardiac magnetic resonance imaging (CMR) and nuclear computed tomography (CT), as well as echocardiography which gave a different perspective on the same problems. Additionally, the scientific programme concentrated around the important issue of heart failure, highlighting many aspects of non-invasive imaging
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