Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.54
Filip Doksimovski, E. Ginovska-Tasevska, I. Arnaudova-Danevska, T. Jakjovska
{"title":"Rising Trends in Pseudomonas aeruginosa and MRSA Isolations in CF patients: A 5-Year Retrospective Analysis from CF center","authors":"Filip Doksimovski, E. Ginovska-Tasevska, I. Arnaudova-Danevska, T. Jakjovska","doi":"10.1183/23120541.acf-2023.54","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.54","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"12 8","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139188979","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.51
Matthew Birss, Davina Jugnarain, Josie Cunningham, Chris Orchard
{"title":"Uptake of retinal screening in patients with cystic fibrosis diabetes in a single adult cystic fibrosis centre","authors":"Matthew Birss, Davina Jugnarain, Josie Cunningham, Chris Orchard","doi":"10.1183/23120541.acf-2023.51","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.51","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"23 4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139190130","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.31
Tanne Daniels, K. Van Calsteren, Lieven Dupont
{"title":"Maternal and obstetric outcomes in women with cystic fibrosis: a retrospective case series of patients in UZ Leuven","authors":"Tanne Daniels, K. Van Calsteren, Lieven Dupont","doi":"10.1183/23120541.acf-2023.31","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.31","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"42 4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139187799","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.56
Noreen Tangney, T. Vagg, K. Deasy, M. Mccarthy, James Dorgan, C. Fleming, C. Howlett, Karen Cronin, Edel O'Riordan, Janice Mansfield, S. Twohig, H. Ibrahim, Barry J Plant
{"title":"A patient journey from lumacaftor/ivacaftor (LI) to tezacaftor/ivacaftor (TI) to elexacaftor/tezacaftor/ivacaftor (ETI): a single center case series","authors":"Noreen Tangney, T. Vagg, K. Deasy, M. Mccarthy, James Dorgan, C. Fleming, C. Howlett, Karen Cronin, Edel O'Riordan, Janice Mansfield, S. Twohig, H. Ibrahim, Barry J Plant","doi":"10.1183/23120541.acf-2023.56","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.56","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"16 2","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139188587","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.48
T. Jakovska-Maretti, Marta Foteva, Ivana Arnaudova Daneva
{"title":"Bone health in adults with cystic fibrosis in the Republic of North Macedonia","authors":"T. Jakovska-Maretti, Marta Foteva, Ivana Arnaudova Daneva","doi":"10.1183/23120541.acf-2023.48","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.48","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"39 3-4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139192164","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.6
C. Fevola, S. Campana, D. Dolce, N. Ravenni, C. Bianchimani, Giulia Santini, M. Francalanci, M. Cavicchi, V. Galici, A. Neri, V. Terlizzi, D. Innocenti, E. Masi, B. Ferrari, Chiara Castellani, M. Masolini, E. Camera, T. Orioli, S. Bresci, B. Borchi, A. Cavallo, J. Mencarini, G. Taccetti
{"title":"Respiratory infections of upper and lower airways in patients with cystic fibrosis.","authors":"C. Fevola, S. Campana, D. Dolce, N. Ravenni, C. Bianchimani, Giulia Santini, M. Francalanci, M. Cavicchi, V. Galici, A. Neri, V. Terlizzi, D. Innocenti, E. Masi, B. Ferrari, Chiara Castellani, M. Masolini, E. Camera, T. Orioli, S. Bresci, B. Borchi, A. Cavallo, J. Mencarini, G. Taccetti","doi":"10.1183/23120541.acf-2023.6","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.6","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"51 17","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139193810","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.22
H. Ibrahim, K. Deasy, A. O’Mahony, M. Mccarthy, James Dorgan, C. Fleming, C. Howlett, Yvonne Mccarthy, S. Twohig, Paul O'Regan, Laura Kirwan, Michael M Maher, Owen J O'Connor, Barry J Plant
{"title":"Clinical, radiological and systemic inflammatory outcomes in real-world Kaftrio study (CORK2) in CF patients homozygous for Phe508del mutation.","authors":"H. Ibrahim, K. Deasy, A. O’Mahony, M. Mccarthy, James Dorgan, C. Fleming, C. Howlett, Yvonne Mccarthy, S. Twohig, Paul O'Regan, Laura Kirwan, Michael M Maher, Owen J O'Connor, Barry J Plant","doi":"10.1183/23120541.acf-2023.22","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.22","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"50 3","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139194407","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.41
Hande Yuce, Oğuz Karcioğlu, E. Damadoğlu, A. Kalyoncu
{"title":"Evaluation of post-transfer clinical conditions of the cystic fibrosis(CF) patients transferred to the adult chest diseases","authors":"Hande Yuce, Oğuz Karcioğlu, E. Damadoğlu, A. Kalyoncu","doi":"10.1183/23120541.acf-2023.41","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.41","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"20 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139188308","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.45
D. Gogoi, Michelle Casey, Caoimbhe Bolger, Sabrina Alghamdi, Parisa Acquilini, Lorraine D’Costa, Rory S Baird, Karin Pietsch, Olive Mccabe, C. Gunaratnam, Noel G Mcelvaney, C. Gabillard-Lefort, E. Reeves
{"title":"CFTR Modulator Therapy Rescues CFTR and Lowers P2X7R-induced Inflammasome Activation of Airway Epithelial Cells","authors":"D. Gogoi, Michelle Casey, Caoimbhe Bolger, Sabrina Alghamdi, Parisa Acquilini, Lorraine D’Costa, Rory S Baird, Karin Pietsch, Olive Mccabe, C. Gunaratnam, Noel G Mcelvaney, C. Gabillard-Lefort, E. Reeves","doi":"10.1183/23120541.acf-2023.45","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.45","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"51 7-8","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139190568","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.55
H. Ibrahim, Noreen Tagney, M. Mccarthy, James Dorgan, C. Fleming, C. Howlett, Karen Cronin, Edel O'Riordan, Janice Mansfield, S. Twohig, T. Vagg, Deasy Kevin, Barry J Plant
{"title":"Changes in the cardiometabolic risk factors post elexacaftor-tezacaftor-ivacaftor therapy; a real-world prospective single center study.","authors":"H. Ibrahim, Noreen Tagney, M. Mccarthy, James Dorgan, C. Fleming, C. Howlett, Karen Cronin, Edel O'Riordan, Janice Mansfield, S. Twohig, T. Vagg, Deasy Kevin, Barry J Plant","doi":"10.1183/23120541.acf-2023.55","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.55","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"4 3","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139191396","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}