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Adult Cystic Fibrosis最新文献

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Rising Trends in Pseudomonas aeruginosa and MRSA Isolations in CF patients: A 5-Year Retrospective Analysis from CF center CF 患者铜绿假单胞菌和 MRSA 分离率的上升趋势:来自 CF 中心的 5 年回顾性分析
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.54
Filip Doksimovski, E. Ginovska-Tasevska, I. Arnaudova-Danevska, T. Jakjovska
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引用次数: 0
Uptake of retinal screening in patients with cystic fibrosis diabetes in a single adult cystic fibrosis centre 单一成人囊性纤维化中心囊性纤维化糖尿病患者接受视网膜筛查的情况
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.51
Matthew Birss, Davina Jugnarain, Josie Cunningham, Chris Orchard
{"title":"Uptake of retinal screening in patients with cystic fibrosis diabetes in a single adult cystic fibrosis centre","authors":"Matthew Birss, Davina Jugnarain, Josie Cunningham, Chris Orchard","doi":"10.1183/23120541.acf-2023.51","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.51","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"23 4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139190130","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Maternal and obstetric outcomes in women with cystic fibrosis: a retrospective case series of patients in UZ Leuven 囊性纤维化妇女的孕产结局:鲁汶大学患者的回顾性病例系列
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.31
Tanne Daniels, K. Van Calsteren, Lieven Dupont
{"title":"Maternal and obstetric outcomes in women with cystic fibrosis: a retrospective case series of patients in UZ Leuven","authors":"Tanne Daniels, K. Van Calsteren, Lieven Dupont","doi":"10.1183/23120541.acf-2023.31","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.31","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"42 4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139187799","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
A patient journey from lumacaftor/ivacaftor (LI) to tezacaftor/ivacaftor (TI) to elexacaftor/tezacaftor/ivacaftor (ETI): a single center case series 从 lumacaftor/ivacaftor (LI) 到 tezacaftor/ivacaftor (TI) 再到 elexacaftor/tezacaftor/ivacaftor (ETI)的患者之旅:单中心病例系列
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.56
Noreen Tangney, T. Vagg, K. Deasy, M. Mccarthy, James Dorgan, C. Fleming, C. Howlett, Karen Cronin, Edel O'Riordan, Janice Mansfield, S. Twohig, H. Ibrahim, Barry J Plant
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引用次数: 0
Bone health in adults with cystic fibrosis in the Republic of North Macedonia 北马其顿共和国患有囊性纤维化的成年人的骨骼健康状况
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.48
T. Jakovska-Maretti, Marta Foteva, Ivana Arnaudova Daneva
{"title":"Bone health in adults with cystic fibrosis in the Republic of North Macedonia","authors":"T. Jakovska-Maretti, Marta Foteva, Ivana Arnaudova Daneva","doi":"10.1183/23120541.acf-2023.48","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.48","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"39 3-4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139192164","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Respiratory infections of upper and lower airways in patients with cystic fibrosis. 囊性纤维化患者上下气道的呼吸道感染。
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.6
C. Fevola, S. Campana, D. Dolce, N. Ravenni, C. Bianchimani, Giulia Santini, M. Francalanci, M. Cavicchi, V. Galici, A. Neri, V. Terlizzi, D. Innocenti, E. Masi, B. Ferrari, Chiara Castellani, M. Masolini, E. Camera, T. Orioli, S. Bresci, B. Borchi, A. Cavallo, J. Mencarini, G. Taccetti
{"title":"Respiratory infections of upper and lower airways in patients with cystic fibrosis.","authors":"C. Fevola, S. Campana, D. Dolce, N. Ravenni, C. Bianchimani, Giulia Santini, M. Francalanci, M. Cavicchi, V. Galici, A. Neri, V. Terlizzi, D. Innocenti, E. Masi, B. Ferrari, Chiara Castellani, M. Masolini, E. Camera, T. Orioli, S. Bresci, B. Borchi, A. Cavallo, J. Mencarini, G. Taccetti","doi":"10.1183/23120541.acf-2023.6","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.6","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"51 17","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139193810","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Clinical, radiological and systemic inflammatory outcomes in real-world Kaftrio study (CORK2) in CF patients homozygous for Phe508del mutation. 同源 Phe508del 突变的 CF 患者在真实世界 Kaftrio 研究(CORK2)中的临床、放射学和全身炎症结果。
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.22
H. Ibrahim, K. Deasy, A. O’Mahony, M. Mccarthy, James Dorgan, C. Fleming, C. Howlett, Yvonne Mccarthy, S. Twohig, Paul O'Regan, Laura Kirwan, Michael M Maher, Owen J O'Connor, Barry J Plant
{"title":"Clinical, radiological and systemic inflammatory outcomes in real-world Kaftrio study (CORK2) in CF patients homozygous for Phe508del mutation.","authors":"H. Ibrahim, K. Deasy, A. O’Mahony, M. Mccarthy, James Dorgan, C. Fleming, C. Howlett, Yvonne Mccarthy, S. Twohig, Paul O'Regan, Laura Kirwan, Michael M Maher, Owen J O'Connor, Barry J Plant","doi":"10.1183/23120541.acf-2023.22","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.22","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"50 3","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139194407","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Evaluation of post-transfer clinical conditions of the cystic fibrosis(CF) patients transferred to the adult chest diseases 对转入成人胸腔疾病治疗的囊性纤维化(CF)患者转院后临床状况的评估
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.41
Hande Yuce, Oğuz Karcioğlu, E. Damadoğlu, A. Kalyoncu
{"title":"Evaluation of post-transfer clinical conditions of the cystic fibrosis(CF) patients transferred to the adult chest diseases","authors":"Hande Yuce, Oğuz Karcioğlu, E. Damadoğlu, A. Kalyoncu","doi":"10.1183/23120541.acf-2023.41","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.41","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"20 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139188308","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
CFTR Modulator Therapy Rescues CFTR and Lowers P2X7R-induced Inflammasome Activation of Airway Epithelial Cells CFTR 调节剂疗法可挽救 CFTR 并降低 P2X7R 诱导的气道上皮细胞炎症体活化
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.45
D. Gogoi, Michelle Casey, Caoimbhe Bolger, Sabrina Alghamdi, Parisa Acquilini, Lorraine D’Costa, Rory S Baird, Karin Pietsch, Olive Mccabe, C. Gunaratnam, Noel G Mcelvaney, C. Gabillard-Lefort, E. Reeves
{"title":"CFTR Modulator Therapy Rescues CFTR and Lowers P2X7R-induced Inflammasome Activation of Airway Epithelial Cells","authors":"D. Gogoi, Michelle Casey, Caoimbhe Bolger, Sabrina Alghamdi, Parisa Acquilini, Lorraine D’Costa, Rory S Baird, Karin Pietsch, Olive Mccabe, C. Gunaratnam, Noel G Mcelvaney, C. Gabillard-Lefort, E. Reeves","doi":"10.1183/23120541.acf-2023.45","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.45","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"51 7-8","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139190568","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Changes in the cardiometabolic risk factors post elexacaftor-tezacaftor-ivacaftor therapy; a real-world prospective single center study. elexacaftor-tezacaftor-ivacaftor 治疗后心脏代谢风险因素的变化;一项真实世界前瞻性单中心研究。
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.55
H. Ibrahim, Noreen Tagney, M. Mccarthy, James Dorgan, C. Fleming, C. Howlett, Karen Cronin, Edel O'Riordan, Janice Mansfield, S. Twohig, T. Vagg, Deasy Kevin, Barry J Plant
{"title":"Changes in the cardiometabolic risk factors post elexacaftor-tezacaftor-ivacaftor therapy; a real-world prospective single center study.","authors":"H. Ibrahim, Noreen Tagney, M. Mccarthy, James Dorgan, C. Fleming, C. Howlett, Karen Cronin, Edel O'Riordan, Janice Mansfield, S. Twohig, T. Vagg, Deasy Kevin, Barry J Plant","doi":"10.1183/23120541.acf-2023.55","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.55","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"4 3","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139191396","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
期刊
Adult Cystic Fibrosis
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