Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.57
C. Premuda, A. Gramegna, Gianfranco Alicandro, Francesca Lucca, M. Retucci, Sonia Volpi, M. Cipolli, Francesco Blasi
{"title":"Effect of elexacaftor/tezacaftor/ivacaftor on body plethysmography measurements in patients with cystic fibrosis and advanced lung disease.","authors":"C. Premuda, A. Gramegna, Gianfranco Alicandro, Francesca Lucca, M. Retucci, Sonia Volpi, M. Cipolli, Francesco Blasi","doi":"10.1183/23120541.acf-2023.57","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.57","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"91 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139193386","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.47
D. Škrbić, Mirna Djurić, Jelena Papovic, B. Tušek
{"title":"COVID-19 vaccine and morbidity in the Adult Cystic Fibrosis Centre in Institute for Pulmonary Diseases of Vojvodina Sremska Kamenica, Serbia","authors":"D. Škrbić, Mirna Djurić, Jelena Papovic, B. Tušek","doi":"10.1183/23120541.acf-2023.47","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.47","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"7 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139188268","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.44
Adrienn Bánki, T. Pincikova
{"title":"Plasma concentrations of elexacaftor, tezacaftor and ivacaftor in adult people with cystic fibrosis: A pilot study","authors":"Adrienn Bánki, T. Pincikova","doi":"10.1183/23120541.acf-2023.44","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.44","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"44 8","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139192012","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.42
Hande Yuce, S. Mumusoglu, A. Kalyoncu, E. Damadoğlu
{"title":"Knowledge, attitudes and behaviors on reproductive health of patients followed at hacettepe university adult cystic fibrosis (CF) center","authors":"Hande Yuce, S. Mumusoglu, A. Kalyoncu, E. Damadoğlu","doi":"10.1183/23120541.acf-2023.42","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.42","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"13 4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139192858","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.29
Nadine Asir, Noor Al-Sulaiti, Abdusamea Shabani, Atqah Abdul Wahab
{"title":"First case of pott's disease in a cystic fibrosis adolescent with a homozygous CFTR mutation c.3700 A > G (p. Ile1234Val)","authors":"Nadine Asir, Noor Al-Sulaiti, Abdusamea Shabani, Atqah Abdul Wahab","doi":"10.1183/23120541.acf-2023.29","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.29","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"23 2","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139189138","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.50
Giulia Orpheu, Stefania Patrito, Marta Saporito, Erica Falzone, Nausicaa Scopelliti, L. Riberi, Andrea Falco, Sonia Moi, S. Demichelis, Alberto Perboni, B. Messore, Letizia Valsecchi
{"title":"Even grandparents can be diagnosed with Cystic Fibrosis!","authors":"Giulia Orpheu, Stefania Patrito, Marta Saporito, Erica Falzone, Nausicaa Scopelliti, L. Riberi, Andrea Falco, Sonia Moi, S. Demichelis, Alberto Perboni, B. Messore, Letizia Valsecchi","doi":"10.1183/23120541.acf-2023.50","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.50","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"52 7","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139192379","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.33
A. Orenti, E. Hatziagorou, Eitan Kerem, Christiane De Boeck, Pierre-Régis Burgel
{"title":"Evolution of cystic fibrosis adult population over the last 10-years in Europe","authors":"A. Orenti, E. Hatziagorou, Eitan Kerem, Christiane De Boeck, Pierre-Régis Burgel","doi":"10.1183/23120541.acf-2023.33","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.33","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"65 3","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139196350","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.4
U. Skogeland, Anna Hedborg, Cecilia Rodriguez, Adrienn Bánki, Tove Godskesen
{"title":"Adherence to medical regimens after lung transplantation among adults with Cystic Fibrosis increased during COVID-19 pandemic","authors":"U. Skogeland, Anna Hedborg, Cecilia Rodriguez, Adrienn Bánki, Tove Godskesen","doi":"10.1183/23120541.acf-2023.4","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.4","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"11 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139188406","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.15
K. Deasy, H. Ibrahim, Mairead Mc Carthy, C. Fleming, James Dorgan, Yvonne Mc Carthy, C. Howlett, S. Twohig, Paul O'Regan, Laura Kirwan, Desmond M Murphy, Barry J Plant
{"title":"Real-world Elexacaftor/Tezacaftor/Ivacaftor(ETI) changes prospective sputum collection and microbiological reporting in a single centre pilot CF cohort.","authors":"K. Deasy, H. Ibrahim, Mairead Mc Carthy, C. Fleming, James Dorgan, Yvonne Mc Carthy, C. Howlett, S. Twohig, Paul O'Regan, Laura Kirwan, Desmond M Murphy, Barry J Plant","doi":"10.1183/23120541.acf-2023.15","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.15","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"44 5","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139192322","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}