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Adult Cystic Fibrosis最新文献

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Effect of elexacaftor/tezacaftor/ivacaftor on body plethysmography measurements in patients with cystic fibrosis and advanced lung disease. elexacaftor/tezacaftor/ivacaftor 对囊性纤维化和晚期肺部疾病患者体褶测量的影响。
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.57
C. Premuda, A. Gramegna, Gianfranco Alicandro, Francesca Lucca, M. Retucci, Sonia Volpi, M. Cipolli, Francesco Blasi
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引用次数: 0
COVID-19 vaccine and morbidity in the Adult Cystic Fibrosis Centre in Institute for Pulmonary Diseases of Vojvodina Sremska Kamenica, Serbia COVID-19 疫苗与塞尔维亚斯雷姆斯卡-卡梅尼察 Vojvodina 肺病研究所成人囊性纤维化中心的发病率
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.47
D. Škrbić, Mirna Djurić, Jelena Papovic, B. Tušek
{"title":"COVID-19 vaccine and morbidity in the Adult Cystic Fibrosis Centre in Institute for Pulmonary Diseases of Vojvodina Sremska Kamenica, Serbia","authors":"D. Škrbić, Mirna Djurić, Jelena Papovic, B. Tušek","doi":"10.1183/23120541.acf-2023.47","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.47","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"7 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139188268","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Outcomes of short-term modulatory therapy in adult cystic fibrosis 成人囊性纤维化短期调节疗法的疗效
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.40
Oğuz Karcioğlu, Aytekin İdikut, E. Damadoğlu
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引用次数: 0
Plasma concentrations of elexacaftor, tezacaftor and ivacaftor in adult people with cystic fibrosis: A pilot study 囊性纤维化成年患者体内 elexacaftor、tezacaftor 和 ivacaftor 的血浆浓度:试点研究
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.44
Adrienn Bánki, T. Pincikova
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引用次数: 0
Knowledge, attitudes and behaviors on reproductive health of patients followed at hacettepe university adult cystic fibrosis (CF) center 哈杰泰佩大学成人囊性纤维化(CF)中心随访患者的生殖健康知识、态度和行为
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.42
Hande Yuce, S. Mumusoglu, A. Kalyoncu, E. Damadoğlu
{"title":"Knowledge, attitudes and behaviors on reproductive health of patients followed at hacettepe university adult cystic fibrosis (CF) center","authors":"Hande Yuce, S. Mumusoglu, A. Kalyoncu, E. Damadoğlu","doi":"10.1183/23120541.acf-2023.42","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.42","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"13 4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139192858","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
First case of pott's disease in a cystic fibrosis adolescent with a homozygous CFTR mutation c.3700 A > G (p. Ile1234Val) 首例患有同型 CFTR 基因突变 c.3700 A > G (p. Ile1234Val) 的囊性纤维化青少年 Pott's 病例
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.29
Nadine Asir, Noor Al-Sulaiti, Abdusamea Shabani, Atqah Abdul Wahab
{"title":"First case of pott's disease in a cystic fibrosis adolescent with a homozygous CFTR mutation c.3700 A > G (p. Ile1234Val)","authors":"Nadine Asir, Noor Al-Sulaiti, Abdusamea Shabani, Atqah Abdul Wahab","doi":"10.1183/23120541.acf-2023.29","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.29","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"23 2","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139189138","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Even grandparents can be diagnosed with Cystic Fibrosis! 甚至祖父母也可能被诊断出患有囊性纤维化!
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.50
Giulia Orpheu, Stefania Patrito, Marta Saporito, Erica Falzone, Nausicaa Scopelliti, L. Riberi, Andrea Falco, Sonia Moi, S. Demichelis, Alberto Perboni, B. Messore, Letizia Valsecchi
{"title":"Even grandparents can be diagnosed with Cystic Fibrosis!","authors":"Giulia Orpheu, Stefania Patrito, Marta Saporito, Erica Falzone, Nausicaa Scopelliti, L. Riberi, Andrea Falco, Sonia Moi, S. Demichelis, Alberto Perboni, B. Messore, Letizia Valsecchi","doi":"10.1183/23120541.acf-2023.50","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.50","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"52 7","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139192379","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Evolution of cystic fibrosis adult population over the last 10-years in Europe 过去 10 年欧洲囊性纤维化成年人口的变化情况
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.33
A. Orenti, E. Hatziagorou, Eitan Kerem, Christiane De Boeck, Pierre-Régis Burgel
{"title":"Evolution of cystic fibrosis adult population over the last 10-years in Europe","authors":"A. Orenti, E. Hatziagorou, Eitan Kerem, Christiane De Boeck, Pierre-Régis Burgel","doi":"10.1183/23120541.acf-2023.33","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.33","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"65 3","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139196350","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Adherence to medical regimens after lung transplantation among adults with Cystic Fibrosis increased during COVID-19 pandemic 在 COVID-19 大流行期间,成人囊性纤维化患者肺移植后坚持治疗的人数有所增加
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.4
U. Skogeland, Anna Hedborg, Cecilia Rodriguez, Adrienn Bánki, Tove Godskesen
{"title":"Adherence to medical regimens after lung transplantation among adults with Cystic Fibrosis increased during COVID-19 pandemic","authors":"U. Skogeland, Anna Hedborg, Cecilia Rodriguez, Adrienn Bánki, Tove Godskesen","doi":"10.1183/23120541.acf-2023.4","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.4","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"11 1","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139188406","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Real-world Elexacaftor/Tezacaftor/Ivacaftor(ETI) changes prospective sputum collection and microbiological reporting in a single centre pilot CF cohort. 在一个 CF 单中心试点队列中,Elexacaftor/Tezacaftor/Ivacaftor(ETI)对前瞻性痰液收集和微生物学报告的实际影响。
Pub Date : 2023-12-01 DOI: 10.1183/23120541.acf-2023.15
K. Deasy, H. Ibrahim, Mairead Mc Carthy, C. Fleming, James Dorgan, Yvonne Mc Carthy, C. Howlett, S. Twohig, Paul O'Regan, Laura Kirwan, Desmond M Murphy, Barry J Plant
{"title":"Real-world Elexacaftor/Tezacaftor/Ivacaftor(ETI) changes prospective sputum collection and microbiological reporting in a single centre pilot CF cohort.","authors":"K. Deasy, H. Ibrahim, Mairead Mc Carthy, C. Fleming, James Dorgan, Yvonne Mc Carthy, C. Howlett, S. Twohig, Paul O'Regan, Laura Kirwan, Desmond M Murphy, Barry J Plant","doi":"10.1183/23120541.acf-2023.15","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.15","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"44 5","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139192322","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
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Adult Cystic Fibrosis
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