Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.34
Till Othmer, Marcus A. Mall, S. Thee, Mirjam Stahl
{"title":"A 5-year monocentric retrospective analysis of the use of Ceftazidim/Avibactam and Ceftolozane/Tazobactam in adult cystic fibrosis patients","authors":"Till Othmer, Marcus A. Mall, S. Thee, Mirjam Stahl","doi":"10.1183/23120541.acf-2023.34","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.34","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"2 2-4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139192266","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.53
Rudi Mauro Pereira Fernandes, E. Fragoso, Carlos Lopes, Pilar Azevedo
{"title":"Is there a role for sweat chloride levels as a marker of clinical response to Elexacaftor/Tezacaftor/Ivacaftor in Cystic Fibrosis patients?","authors":"Rudi Mauro Pereira Fernandes, E. Fragoso, Carlos Lopes, Pilar Azevedo","doi":"10.1183/23120541.acf-2023.53","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.53","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"4 3","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139187897","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.46
Daniela Savi, Francesca Lucca, Gloria Tridello, S. Tomezzoli, Monica Signorini, Giulia Cucchetto, Marisol Ocampo Barao, M. Cipolli
{"title":"Pulmonary exacerbation rates after three years of Elexacaftor/Tezacaftor/Ivacaftor therapy in adults with cystic fibrosis and severe lung disease","authors":"Daniela Savi, Francesca Lucca, Gloria Tridello, S. Tomezzoli, Monica Signorini, Giulia Cucchetto, Marisol Ocampo Barao, M. Cipolli","doi":"10.1183/23120541.acf-2023.46","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.46","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"168 1-4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139188275","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.17
Natascha Remus, G. Leignadier, E. Thomas, C. Delestrain, Michael Shum, Bernard Maitre, Ralph Epaud, Benoit Douvry
{"title":"The A-Step - a new incremental exercise test defying space and infection control measures","authors":"Natascha Remus, G. Leignadier, E. Thomas, C. Delestrain, Michael Shum, Bernard Maitre, Ralph Epaud, Benoit Douvry","doi":"10.1183/23120541.acf-2023.17","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.17","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"44 5","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139188856","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.20
Cecilia Brignole, Chiara Cimbalo, S. Rigon, Francesca Lucca, Gloria Tridello, Giulia Paiola, S. Tomezzoli, Sonia Volpi, M. Cipolli
{"title":"Changes in nutritional status and muscular strength in adult patients with cystic fibrosis (pwCF) treated with elexacaftor/tezacaftor/ivacaftor (ETI)","authors":"Cecilia Brignole, Chiara Cimbalo, S. Rigon, Francesca Lucca, Gloria Tridello, Giulia Paiola, S. Tomezzoli, Sonia Volpi, M. Cipolli","doi":"10.1183/23120541.acf-2023.20","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.20","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"52 4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139191880","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.43
Joshua Sill, Benjamin Chilampath, Matthew Bernens, Patricia Banks, Samuel Stein
{"title":"Assessing and improving patient knowledge gaps relating to the administration of elexacaftor/tezacaftor/ivacaftor in an adult cystic fibrosis clinic population","authors":"Joshua Sill, Benjamin Chilampath, Matthew Bernens, Patricia Banks, Samuel Stein","doi":"10.1183/23120541.acf-2023.43","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.43","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"49 2","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139187789","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.3
Guergana Petrova, N. Yaneva, Alexey Savov
{"title":"CF diagnosed at the sixth decade of life","authors":"Guergana Petrova, N. Yaneva, Alexey Savov","doi":"10.1183/23120541.acf-2023.3","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.3","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"13 4","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139190504","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.37
N. Duplacie, T. Havermans, Janne Houben, Marianne Schulte, Linda Boulanger, L. Moyens, Cindy Ruelens, L. Dupont
{"title":"Side-effects and ETI-treatment: a multidisciplinary challenge","authors":"N. Duplacie, T. Havermans, Janne Houben, Marianne Schulte, Linda Boulanger, L. Moyens, Cindy Ruelens, L. Dupont","doi":"10.1183/23120541.acf-2023.37","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.37","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"291 5","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139193008","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
Pub Date : 2023-12-01DOI: 10.1183/23120541.acf-2023.49
Irene Tomarelli, Claudia De Petro, Annalisa Orienti, Luigi Annicchiarico, Sofia Misuraca, M. Contarini, A. Gramegna, Francesco Blasi
{"title":"Patients not eligible for CFTR-modulators (CFTRm) in Europe: characteristics and distribution","authors":"Irene Tomarelli, Claudia De Petro, Annalisa Orienti, Luigi Annicchiarico, Sofia Misuraca, M. Contarini, A. Gramegna, Francesco Blasi","doi":"10.1183/23120541.acf-2023.49","DOIUrl":"https://doi.org/10.1183/23120541.acf-2023.49","url":null,"abstract":"","PeriodicalId":505181,"journal":{"name":"Adult Cystic Fibrosis","volume":"45 9","pages":""},"PeriodicalIF":0.0,"publicationDate":"2023-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139193265","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}