B., Nieto Vazquez, Mira, Navarral, M., Martin N. Garramone, M. Tasso, Munoz
A few of the known associations between paediatric cancer and congenital anomalies are attributable to contiguous-gene syndromes. Neuroblastoma (NB) has been linked with an excess of gastrointestinal malformations, but there is a significant scarcity of associated respiratory anomalies. We report on two children having an abdominal NB and a bronchogenic cyst diagnosed simultaneously and in different order of appearance. Both masses were removed in separated procedures, taking into account the priority and the time sequence of chemotherapy. Literature is reviewed, checking that the genetic basis for this association is supported by speculations about the oncogene RON.
{"title":"Neuroblastoma and Bronchogenic Cyst: A Rare Association","authors":"B., Nieto Vazquez, Mira, Navarral, M., Martin N. Garramone, M. Tasso, Munoz","doi":"10.1055/s-2008-1072388","DOIUrl":"https://doi.org/10.1055/s-2008-1072388","url":null,"abstract":"A few of the known associations between paediatric cancer and congenital anomalies are attributable to contiguous-gene syndromes. Neuroblastoma (NB) has been linked with an excess of gastrointestinal malformations, but there is a significant scarcity of associated respiratory anomalies. We report on two children having an abdominal NB and a bronchogenic cyst diagnosed simultaneously and in different order of appearance. Both masses were removed in separated procedures, taking into account the priority and the time sequence of chemotherapy. Literature is reviewed, checking that the genetic basis for this association is supported by speculations about the oncogene RON.","PeriodicalId":269806,"journal":{"name":"European Journal of Pediatric Surgery (EJPS)","volume":"9 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2000-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"116168806","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
The present study evaluates the long-term outcome of elastic stable intramedullary nailing (ESIN) in children with long-bone shaft fractures. 70 patients were examined, the present mean age of patients was 12.7 (+/- 3.26) years, mean time interval since surgery was 3.1 (+/- 1.49) years. Following ESIN at the lower extremity (23 femur fractures, 14 tibia fractures), keloid formation was remarkable in one patient, range of motion (ROM) was adequate in all but one boy (extension deficit of the hip of 10 degrees). Overall leg length discrepancy was +4.1 mm (+/- 5.2 mm) following ESIN for femur fracture and +3.2 mm (+/- 6.4 mm) following tibia fracture. Radiologically, all fractures had healed and no signs of avascular necrosis (AVN) could be detected. Malalignment was documented in one girl following tibia fracture (valgus of 12 degrees). Assessment of the upper extremity (28 forearm fractures, 5 humerus fractures) revealed keloid formation in 5 children. Impaired ROM was found in three children following ESIN for a forearm fracture (limited pro-/supination). Radiological controls detected one case of retrocurvation of the humerus (12 degrees, polytrauma patient) and one varus deviation of the radius in a 10-year old boy. Questioning the children about their opinion of the treatment, 93% considered the cosmetic results as good (6% fair), they judged the functional ability as perfect in 91% (9% fair) and 93% expressed great overall content (6% fair, 1% poor). In conclusion, ESIN provides good long-term results and can be a beneficial method for children with long-bone fractures.
本研究评估弹性稳定髓内钉(ESIN)治疗儿童长骨干骨折的长期疗效。70例患者,目前平均年龄12.7(+/- 3.26)岁,手术后平均时间间隔3.1(+/- 1.49)年。在下肢ESIN(23例股骨骨折,14例胫骨骨折)后,1例患者瘢痕瘤形成明显,除1例男孩外,所有患者的活动范围(ROM)都足够(髋关节伸展不足10度)。股骨骨折ESIN术后腿长差异为+4.1 mm (+/- 5.2 mm),胫骨骨折术后腿长差异为+3.2 mm (+/- 6.4 mm)。影像学上,所有骨折均愈合,无血管坏死(AVN)迹象。一名女孩在胫骨骨折(外翻12度)后出现了错位。对上肢(28例前臂骨折,5例肱骨骨折)的评估显示5例儿童有瘢痕疙瘩形成。3例儿童前臂骨折(前旋/旋位受限)ESIN术后ROM受损。放射学对照发现一例肱骨后屈(12度,多发创伤患者)和一例10岁男孩桡骨内翻偏曲。在询问儿童对治疗的看法时,93%的儿童认为美容效果良好(6%公平),91%的儿童认为功能能力完美(9%公平),93%的儿童表示整体内容很好(6%公平,1%差)。综上所述,ESIN具有良好的远期效果,是治疗儿童长骨骨折的有益方法。
{"title":"Elastic Stable Intramedullary Nailing (ESIN) Provides Good Long-Term Results in Pediatric Long-Bone Fractures","authors":"Holger Till, B. Hüttl, P. Knorr, H. Dietz","doi":"10.1055/s-2008-1072383","DOIUrl":"https://doi.org/10.1055/s-2008-1072383","url":null,"abstract":"The present study evaluates the long-term outcome of elastic stable intramedullary nailing (ESIN) in children with long-bone shaft fractures. 70 patients were examined, the present mean age of patients was 12.7 (+/- 3.26) years, mean time interval since surgery was 3.1 (+/- 1.49) years. Following ESIN at the lower extremity (23 femur fractures, 14 tibia fractures), keloid formation was remarkable in one patient, range of motion (ROM) was adequate in all but one boy (extension deficit of the hip of 10 degrees). Overall leg length discrepancy was +4.1 mm (+/- 5.2 mm) following ESIN for femur fracture and +3.2 mm (+/- 6.4 mm) following tibia fracture. Radiologically, all fractures had healed and no signs of avascular necrosis (AVN) could be detected. Malalignment was documented in one girl following tibia fracture (valgus of 12 degrees). Assessment of the upper extremity (28 forearm fractures, 5 humerus fractures) revealed keloid formation in 5 children. Impaired ROM was found in three children following ESIN for a forearm fracture (limited pro-/supination). Radiological controls detected one case of retrocurvation of the humerus (12 degrees, polytrauma patient) and one varus deviation of the radius in a 10-year old boy. Questioning the children about their opinion of the treatment, 93% considered the cosmetic results as good (6% fair), they judged the functional ability as perfect in 91% (9% fair) and 93% expressed great overall content (6% fair, 1% poor). In conclusion, ESIN provides good long-term results and can be a beneficial method for children with long-bone fractures.","PeriodicalId":269806,"journal":{"name":"European Journal of Pediatric Surgery (EJPS)","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2000-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128680510","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Gastric Electrical Activity Normalises in the First Decade of Life","authors":"W. Cheng, P. Tam","doi":"10.1055/s-2008-1072379","DOIUrl":"https://doi.org/10.1055/s-2008-1072379","url":null,"abstract":"Aim: Methods: Results: Conclusion: Zielsetzung: Methodik: Ergebnisse: Schlussfolgerungen:","PeriodicalId":269806,"journal":{"name":"European Journal of Pediatric Surgery (EJPS)","volume":"32 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2000-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122122162","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
S. Shehata, I. El-Banna, A. Gaber, A. M. El-Samongy
Spondylothoracic dysplasia (Jarcho-Levin syndrome) is a syndrome of unknown etiology. We describe a new case with diaphragmatic eventration. Literature review for cases of Jarcho-Levin syndrome with diaphragmatic defects, which were six cases, revealed that renal affection increased when diaphragmatic defects associate the syndrome with pulmonary hypoplasia. Thus, the subgroup of spondylothoracic dysplasia with diaphragmatic defect is a more severe subgroup of the syndrome rather than the other forms of this syndrome. Relating the described anomalies in this case and that of the literature cases to the known embryological basis may point to a pivotal developmental link between lung, kidney and diaphragm, possibly the posterior mesenchyme.
{"title":"Spondylothoracic Dysplasia with Diaphragmatic Defect: A Case Report with Literature Review","authors":"S. Shehata, I. El-Banna, A. Gaber, A. M. El-Samongy","doi":"10.1055/s-2008-1072387","DOIUrl":"https://doi.org/10.1055/s-2008-1072387","url":null,"abstract":"Spondylothoracic dysplasia (Jarcho-Levin syndrome) is a syndrome of unknown etiology. We describe a new case with diaphragmatic eventration. Literature review for cases of Jarcho-Levin syndrome with diaphragmatic defects, which were six cases, revealed that renal affection increased when diaphragmatic defects associate the syndrome with pulmonary hypoplasia. Thus, the subgroup of spondylothoracic dysplasia with diaphragmatic defect is a more severe subgroup of the syndrome rather than the other forms of this syndrome. Relating the described anomalies in this case and that of the literature cases to the known embryological basis may point to a pivotal developmental link between lung, kidney and diaphragm, possibly the posterior mesenchyme.","PeriodicalId":269806,"journal":{"name":"European Journal of Pediatric Surgery (EJPS)","volume":"20 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2000-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"127963577","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
J. Matute1, M. Benavent2, J. Hernandez3, J. Vázquez1
Summary
总结
{"title":"Results of the Azizkhan Procedure for Long-Term Suprastomal Tracheomalacia","authors":"J. Matute1, M. Benavent2, J. Hernandez3, J. Vázquez1","doi":"10.1055/s-2008-1072376","DOIUrl":"https://doi.org/10.1055/s-2008-1072376","url":null,"abstract":"Summary","PeriodicalId":269806,"journal":{"name":"European Journal of Pediatric Surgery (EJPS)","volume":"4 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2000-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133106135","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
S. Hassett, C. Costigan, M. Mcdermott, R. Fitzgerald
Schlussfolgerungen:
结论:
{"title":"Prophylactic Thyroidectomy in the Treatment of Thyroid Medullary Carcinoma. Age for Surgery?","authors":"S. Hassett, C. Costigan, M. Mcdermott, R. Fitzgerald","doi":"10.1055/s-2008-1072386","DOIUrl":"https://doi.org/10.1055/s-2008-1072386","url":null,"abstract":"Schlussfolgerungen:","PeriodicalId":269806,"journal":{"name":"European Journal of Pediatric Surgery (EJPS)","volume":"30 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"2000-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"114141633","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"Long-Term Outcome of the Fetal Adrenal Gland Transplantation in Rats","authors":"İ. Kiriştioğlu1, H. Doğruyol1, İ. Çavuşoğlu2","doi":"10.1055/s-2008-1072292","DOIUrl":"https://doi.org/10.1055/s-2008-1072292","url":null,"abstract":"Ergebnisse: Schlußfolgerung:","PeriodicalId":269806,"journal":{"name":"European Journal of Pediatric Surgery (EJPS)","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1999-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"114568480","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"European Union of Paediatric Surgical Associations (EUPSA)","authors":"R. Fitzgerald","doi":"10.1055/s-2008-1072215","DOIUrl":"https://doi.org/10.1055/s-2008-1072215","url":null,"abstract":"","PeriodicalId":269806,"journal":{"name":"European Journal of Pediatric Surgery (EJPS)","volume":"9 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1999-04-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"121472097","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
{"title":"In Memoriam: Prof. Dr. Marcel Bettex","authors":"A. Schärli","doi":"10.1055/s-2008-1071108","DOIUrl":"https://doi.org/10.1055/s-2008-1071108","url":null,"abstract":"","PeriodicalId":269806,"journal":{"name":"European Journal of Pediatric Surgery (EJPS)","volume":"15 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1998-02-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"127168813","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
A. Avanoğlu1, Ö. Herek1, I. Ulman1, O. Ergün1, A. Tünger2, M. Alkanat3, A. Erdener1
We experimentally studied the effects of Hz receptor block ers (ranitidine) on bacterial translocation (BT) in 42 male albino rals. Sham group (Group I, n .. 12 rau) wert' exposed to 21"C water while Bum group (Groop 11, n" lS rats) and Ranitidine group (Group 11I. n - 15 ratsl were exposed to 95" C hot water for 10 seconds to produce a full thidmess burn in 30 % of total body surface area. 300 mglkg ranitidine was administered to Group 11I starting immediately after the burn injury. Rats were sacrtficed on the fifth postbum day. Sham group gained weight while groups 11 and 11I had significant weight loss. Gastric pH increased with the admin-Resume
{"title":"Effects of H2 Receptor Blocking Agents on Bacterial Translocation in Burn Injury*","authors":"A. Avanoğlu1, Ö. Herek1, I. Ulman1, O. Ergün1, A. Tünger2, M. Alkanat3, A. Erdener1","doi":"10.1055/s-2008-1071171","DOIUrl":"https://doi.org/10.1055/s-2008-1071171","url":null,"abstract":"We experimentally studied the effects of Hz receptor block ers (ranitidine) on bacterial translocation (BT) in 42 male albino rals. Sham group (Group I, n .. 12 rau) wert' exposed to 21\"C water while Bum group (Groop 11, n\" lS rats) and Ranitidine group (Group 11I. n - 15 ratsl were exposed to 95\" C hot water for 10 seconds to produce a full thidmess burn in 30 % of total body surface area. 300 mglkg ranitidine was administered to Group 11I starting immediately after the burn injury. Rats were sacrtficed on the fifth postbum day. Sham group gained weight while groups 11 and 11I had significant weight loss. Gastric pH increased with the admin-Resume","PeriodicalId":269806,"journal":{"name":"European Journal of Pediatric Surgery (EJPS)","volume":"16 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1997-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"121075085","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}