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Multifocal metachronous occurence of different hystologic sinonasal-type papilloma 多病灶同时发生的不同子宫窦型乳头状瘤
Q4 Medicine Pub Date : 2024-01-16 DOI: 10.57140/mj.53.4.8
J. Ajduk, Mirta Peček, Marija Pierobon, Iva Mažić, T. Gregurić, A. Košec
Introduction: Sinonasal-type papilloma is a very rare tumor, most commonly connected with the sinonasal space, and very rarely with the middle ear. Primary tumors of the temporal bone are extremely rare and only 28 cases have been described in literature, with additional 29 cases of tumor spreading from the sinonasal tract to the temporal bone. Case presentation: We discuss the case of a 49-year-old woman who had a primary right-sided exophytic form of the sinonasal papilloma of the middle ear, which led to right-sided hearing loss, aural fullness, and otorrhea. During postoperative CT and MRI follow-up one year after surgery, a sinonasal oncocytic-type papilloma was discovered in the sphenoid sinus. To our knowledge, this is the first described case of histologically two different primary sinonasal-types of papilloma in a patient. Common presenting symptoms associated with sinonasal papilloma of the middle ear can be easily misdiagnosed with chronic otitis media or Eustachian tube dysfunction. Although primarily benign, sinonasal papillomas are locally aggressive and pose a risk of recurrence and malignant transformation. Therefore, surgery remains the treatment of choice with necessary long-term follow-up, to detect relapse or even a completely new tumor in that area.
简介:鼻窦型乳头状瘤是一种非常罕见的肿瘤:鼻窦型乳头状瘤是一种非常罕见的肿瘤,最常见的是与鼻窦间隙有关,很少与中耳有关。颞骨原发性肿瘤极为罕见,文献中仅描述了 28 例,另有 29 例肿瘤从鼻窦道扩散至颞骨。病例介绍:我们讨论了一名 49 岁女性的病例,她患有原发性中耳鼻窦乳头状瘤右侧外生型,导致右侧听力下降、耳部饱胀和耳痛。术后一年进行 CT 和 MRI 随访时,在蝶窦发现了鼻窦肿瘤型乳头状瘤。据我们所知,这是第一例在一名患者身上出现组织学上两种不同原发性鼻窦乳头状瘤的病例。与中耳鼻窦乳头状瘤相关的常见症状很容易被误诊为慢性中耳炎或咽鼓管功能障碍。鼻窦乳头状瘤虽然主要是良性的,但具有局部侵袭性,有复发和恶变的风险。因此,手术仍是首选的治疗方法,并进行必要的长期随访,以发现复发甚至是该部位全新的肿瘤。
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引用次数: 0
Barotrauma of the ear and paranasal sinuses 耳部和副鼻窦的气压创伤
Q4 Medicine Pub Date : 2024-01-16 DOI: 10.57140/mj.53.4.3
D. Shejbal, Tajana Gudlin Sbull, D. Vagić
With the increasing popularity of amateur scuba diving and the availability of commercial airplane flights, otorhinolaryngologists will increasingly encounter patients suffering from the effects of barotrauma. Barotrauma occurs according to the principles of Boyle's law, more precisely, due to the inability to equalize pressures within the body cavities. The pathophysiology of barotrauma of the ear and paranasal cavities is reviewed, as well as therapeutic options for prevention and treatment.
随着业余潜水运动的日益普及和商业飞机航班的开通,耳鼻喉科医生会越来越多地遇到因气压创伤而痛苦不堪的病人。气压创伤是根据波义耳定律原理发生的,更确切地说,是由于体腔内的压力无法达到平衡。本文回顾了耳部和副鼻腔气压创伤的病理生理学以及预防和治疗方法。
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引用次数: 0
The impact of coronavirus disease on primary and tertiary health care levels from anotorhinolaryngological perspective 从耳鼻喉科角度看冠状病毒疾病对初级和三级医疗保健的影响
Q4 Medicine Pub Date : 2024-01-16 DOI: 10.57140/mj.53.4.5
Mirta Peček, S. Stevanović, Marijana Peček Vidaković, A. Košec
Cilj istraživanja: Pandemija koronavirusa ima značajan utjecaj na društvo i zdravstveni sustav. Cilj ovoga rada je usporediti podatke o broju i strukturi dijagnoza i obavljenih pregleda iz područja otorinolaringologije i kirurgije glave i vrata na razini primarne (PZZ) i tercijarne zdravstvene zaštite, u razdoblju od godinu dana prije i godinu dana nakon proglašenja pandemije koronavirusa. Bolesnici i metode: Podaci su prikupljani retrospektivno, za razdoblja od 20.3.2019. do 19.3.2020. i od 20.3.2020. do 20.3.2021. Uzorak je prigodan, prikupljen iz jedne ustanove na razini primarne i jedne ustanove na razini tercijarne zdravstvene zaštite. Iz dobivenih podataka isključene su one dijagnoze koje se ne odnose na stanja i bolesti iz otorinolaringologije i kirurgije glave i vrata. Rezultati: Tijekom promatranog razdoblja 20.3.2020.-20.3.2021. došlo je do značajnog pada broja pregleda u objema ustanovama u odnosu na razdoblje 20.3.2019.-19.3.2020. Na razini PZZ bilo je ukupno 533 pregleda, što predstavlja 50,5% pregleda obavljenih u istom razdoblju 2019.godine, dok je na razini specijalističko-konzilijarne zdravstvene zaštite (SKZZ) obavljeno 1672 pregleda, odnosno 56,4% pregleda obavljenih 2019. godine. Do najvećeg pada broja pregleda na razini PZZ došlo je među dijagnozama: zloćudni melanom kože, gripa, akutni bronhitis i bronhiolitis, akutne infekcije gornjeg dišnog sustava i bronhitis, emfizem, astma i druge kronične opstruktivne bolesti. Analizirajući preglede obavljene u SKZZ, najveći pad broja pregleda zabilježen je za dijagnoze: pneumonija, bronhitis, emfizem, astma i druge kronične opstruktivne bolesti, oštećenje sluha, zloćudni melanom kože i ostale bolesti dišnog sustava. Zaključci: Smanjeni broj pregleda i hospitalizacija u odnosu na vrijeme prije početka pandemije kao posljedicu mogu imati povećani broj bolesnika s novim dijagnozama, među kojima i karcinoma otkrivenih u kasnijim stadijima bolesti, što će u konačnici rezultirati kasnijim početkom liječenja i lošijim ishodom bolesti, ali i povećanim opterećenjem zdravstvenog sustava i povećanim troškovima liječenja.
研究目的:冠状病毒大流行对社会和卫生系统产生了重大影响。本报告旨在整理冠状病毒疫情公布前一年和公布后一年在初级(PHC)和三级医疗机构耳鼻咽喉科和头颈外科领域的诊断和门诊检查的数量和结构数据。患者和方法:数据收集时间为 2019 年 3 月 20 日至 2020 年 3 月 19 日,2020 年 3 月 20 日至 2021 年 3 月 20 日。 样本从一家初级和一家三级医疗机构收集。获得的数据不包括与耳鼻喉科和头颈部外科手术中的病症和疼痛无关的诊断。结果:Tijekom promatranog razdoblja 20.3.2020.-20.3.2021. došlo je do značajnog pada broja pregled u objema ustanovama u odnosu na razdoblje 20.3.2019.-19.3.2020.2019年,PZZ考试人数为533人,占2019年总人数的50.5%;SKZZ考试人数为1672人,占2019年总人数的56.4%。在初级保健中心接受检查的人数减少最多的是以下诊断:皮肤恶性黑色素瘤、流感、急性支气管炎和支气管炎、上呼吸道急性感染和支气管炎、肺气肿、哮喘和其他慢性阻塞性疼痛。从 CAPS 的检查次数分析,以下诊断的检查次数降幅最大:肺炎、支气管炎、肺气肿、哮喘和其他慢性阻塞性疼痛、听力障碍、皮肤恶性黑色素瘤和肺部系统的其他疼痛。结论与大流行开始时相比,检查和住院次数的减少可能会导致新诊断的患者人数增加,包括疼痛后期的肝癌,这将最终导致治疗次数的减少和疼痛结果的降低,或者导致卫生系统受损程度的增加和治疗费用的增加。
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引用次数: 0
A case report of appendiceal adenoma - a rare entity 阑尾腺瘤--罕见病例报告
Q4 Medicine Pub Date : 2024-01-16 DOI: 10.57140/mj.53.4.7
Fatima Juković Bihorac, Anhel Koluh, Emir Begagić
Appendiceal neoplasms are quite uncommon. They are detected in fewer than 0.5 percent of appendectomies and less than 0.5 percent of all gastrointestinal neoplasms. Similar to a colonic adenoma, an appendiceal adenoma is neoplasm with precancerous nature. A rare case of appendiceal adenoma is presented here in a 65-year-old female patient, incidentally discovered at the orifice of the appendix, during the screening analysis. The patient felt well. Abdominal examination and laboratory analysis were regular. Due to the inaccessibility of the lesion by colonoscopy, surgical treatment was recommended. A laparoscopic appendectomy was performed. On pathological examination, diagnosis of tubulovillous adenoma was performed. Endoscopic screening analysis of precancerous appendiceal neoplasm is very important. The method of choice for any appendiceal neoplasm is surgical removal i.e. appendectomy, preferably with a clean caecal margin, which requires stapling of the cecum. Early detection can prevent complications and decrease the risk of consequential appendiceal or colorectal carcinoma.
阑尾肿瘤并不常见。阑尾肿瘤在阑尾切除术中的发现率不到 0.5%,在所有胃肠道肿瘤中的发现率不到 0.5%。与结肠腺瘤类似,阑尾腺瘤是一种具有癌前病变性质的肿瘤。本文介绍了一例罕见的阑尾腺瘤病例,患者是一名 65 岁的女性,在筛查分析时偶然在阑尾口处发现了该瘤。患者感觉良好。腹部检查和实验室分析均正常。由于结肠镜检查无法触及病灶,建议进行手术治疗。患者接受了腹腔镜阑尾切除术。病理检查诊断为管状腺瘤。阑尾癌前病变的内镜筛查分析非常重要。任何阑尾肿瘤的首选方法都是手术切除,即阑尾切除术,最好是切除干净盲肠边缘,这需要缝合盲肠。早期发现可以预防并发症,降低阑尾癌或结肠直肠癌的风险。
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引用次数: 0
Ishod bolesti u COVID-19 bolesnika liječenih remdesivirom u Općoj bolnici Zadar u razdoblju od 1. kolovoza 2020. do 1. kolovoza 2021. godine 2020年第一轮至2021年第一轮期间扎达尔奥普乔伊医院接受雷米地韦罗治疗的COVID-19患者的疼痛治疗效果
Q4 Medicine Pub Date : 2024-01-16 DOI: 10.57140/mj.53.4.1
Vedrana Terkeš, Željko Čulina, Ana Ribarović, Jurica Arapović
Bolest uzrokovana SARS-CoV-2 (COVID-19) izrazito je zarazna bolest, koja zadnje tri godine ima izuzetno loš utjecaj na svjetsku demografiju, rezultirajući s gotovo 6,5 milijuna umrlih diljem svijeta. U ovom trenutku još uvijek ne postoji učinkoviti ciljani lijek, a liječenje određuje težina bolesti. Terapija remdesivirom pokazala je određeno kliničko poboljšanje, zbog čega ga je Food and Drug Administration odobrio kao prvi ispitivani lijek u liječenju COVID-19. Ovo retrospektvno opservacijsko istraživanje uključilo je bolesnike liječene remdesivirom u Općoj bolnici Zadar u razdoblju od 1. kolovoza 2020. do 1. kolovoza 2021. godine. Primarni cilj bio je utvrditi komorbiditete i klinički ishod bolesnika liječenih remdesivirom. Najčešće kronične bolesti bile su arterijska hipertenzija (80; 58,4%), dijabetes (44; 32,1%) i maligne bolesti (14; 10,2%). Ukupno je 86 bolesnika (62,7%) pripadalo skupinama teško i kritično bolesnih, a preostalih 51 (37,2%) bili su umjereno bolesni. Smrtnost je bila značajno veća u skupini teško bolesnih i iznosila je 23,4%, dok je u skupini umjereno bolesnih bila 5, 9% ( p=0,0287).
由 SARS-CoV-2(COVID-19)引起的疼痛显然是一种严重的疼痛,在过去的三年里对世界人口产生了重大影响,造成全球约 650 万人死亡。目前,还没有有效的针对性治疗方法,治疗方法取决于疼痛的严重程度。雷米替韦疗法显示出显著的临床改善效果,因此被美国食品药品管理局批准为 COVID-19 试验中的首个研究药物。 这项回顾性观察研究包括 2020 年 3 月 1 日至 2021 年 3 月 1 日期间在扎达尔 Općoj 医院接受雷米替韦治疗的患者。研究的主要目的是确认接受雷米替韦治疗的患者的合并症和临床结果。最常见的慢性疼痛是动脉高血压(80;58.4%)、糖尿病(44;32.1%)和恶性疼痛(14;10.2%)。 共有 86 名患者(62.7%)属于严重和危重疼痛组,而其余 51 名患者(37.2%)则处于濒死状态。重度疼痛组患者的死亡率明显较高,为 23.4%,而严重疼痛组患者的死亡率为 5.9%(P=0.0287)。
{"title":"Ishod bolesti u COVID-19 bolesnika liječenih remdesivirom u Općoj bolnici Zadar u razdoblju od 1. kolovoza 2020. do 1. kolovoza 2021. godine","authors":"Vedrana Terkeš, Željko Čulina, Ana Ribarović, Jurica Arapović","doi":"10.57140/mj.53.4.1","DOIUrl":"https://doi.org/10.57140/mj.53.4.1","url":null,"abstract":"Bolest uzrokovana SARS-CoV-2 (COVID-19) izrazito je zarazna bolest, koja zadnje tri godine ima izuzetno loš utjecaj na svjetsku demografiju, rezultirajući s gotovo 6,5 milijuna umrlih diljem svijeta. U ovom trenutku još uvijek ne postoji učinkoviti ciljani lijek, a liječenje određuje težina bolesti. Terapija remdesivirom pokazala je određeno kliničko poboljšanje, zbog čega ga je Food and Drug Administration odobrio kao prvi ispitivani lijek u liječenju COVID-19. Ovo retrospektvno opservacijsko istraživanje uključilo je bolesnike liječene remdesivirom u Općoj bolnici Zadar u razdoblju od 1. kolovoza 2020. do 1. kolovoza 2021. godine. Primarni cilj bio je utvrditi komorbiditete i klinički ishod bolesnika liječenih remdesivirom. Najčešće kronične bolesti bile su arterijska hipertenzija (80; 58,4%), dijabetes (44; 32,1%) i maligne bolesti (14; 10,2%). Ukupno je 86 bolesnika (62,7%) pripadalo skupinama teško i kritično bolesnih, a preostalih 51 (37,2%) bili su umjereno bolesni. Smrtnost je bila značajno veća u skupini teško bolesnih i iznosila je 23,4%, dok je u skupini umjereno bolesnih bila 5, 9% ( p=0,0287).","PeriodicalId":39401,"journal":{"name":"Medica Jadertina","volume":" 2","pages":""},"PeriodicalIF":0.0,"publicationDate":"2024-01-16","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"139618146","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
The impact of early caloric intake on growth parameters in extremely preterm neonates 早期热量摄入对极早产新生儿生长参数的影响
Q4 Medicine Pub Date : 2024-01-16 DOI: 10.57140/mj.53.4.4
Tihana Nađ, Nora Pušeljić, Krešimir Šantić, Lea Arambašić, Darjan Kardum
Introduction: Even though adequate caloric intake is essential for the promotion of growth in extremely premature infants, this is rarely achieved. We investigated how total caloric intake in the first week of life and other events during the hospitalization impact head circumference and weight at 36 weeks of corrected age in extremely preterm infants. Patients and methods: The study sample consisted of extremely preterm infants treated at Osijek University Hospital Centre, born between January 2018 and December 2020. Records were collected regarding nutritional data, sex, gestational age, birth weight and head circumference, invasive respiratory support, bacterial infection, necrotizing enterocolitis, postnatal steroids, need for supplemental oxygen at 36 weeks gestation, day of introduction of enteral nutrition, duration of parenteral nutrition, length of stay, hemodynamically significant patent ductus arteriosus, cystic periventricular leukomalacia and retinopathy of prematurity. Results: The study cohort included 30 infants. At 36 weeks gestation for weight, median Z scores were -1.63 (IQR -2.34 to -1.15; 95% CI -2.09 to -1.52), and for head circumference were -1.32 (IQR 2.37 to - 0.81; 95% CI -1.75 to -0.91). Median energy intake on the first day of life was 33.42 kcal/kg, and 80.78 kcal/kg on day 7. Early caloric intake was not correlated with changes in Z scores for head circumference and weight at 36 weeks of gestation. Other factors influenced changes in head circumference and weight Z scores, namely: gestational age, respiratory support during the first week, need for additional O2 at 36 weeks, and retinopathy of prematurity requiring intervention. Conclusion: In our cohort of premature infants at 36 weeks corrected age other factors, not primarily total caloric intake influenced growth parameters.
简介尽管充足的热量摄入对促进极早产儿的生长至关重要,但极早产儿很少能做到这一点。我们研究了出生后第一周的总热量摄入以及住院期间的其他事件对极度早产儿在 36 周矫正年龄时头围和体重的影响。患者和方法研究样本包括2018年1月至2020年12月期间在奥西耶克大学医院中心接受治疗的极早产儿。收集的记录包括营养数据、性别、胎龄、出生体重和头围、侵入性呼吸支持、细菌感染、坏死性小肠结肠炎、产后类固醇、妊娠36周时补充氧气的需求、引入肠内营养的天数、肠外营养的持续时间、住院时间、血液动力学显著的动脉导管未闭、囊性室周白斑和早产儿视网膜病变。研究结果研究对象包括 30 名婴儿。妊娠36周时,体重的Z评分中位数为-1.63(IQR为-2.34至-1.15;95% CI为-2.09至-1.52),头围的Z评分中位数为-1.32(IQR为2.37至-0.81;95% CI为-1.75至-0.91)。出生第一天的能量摄入中位数为 33.42 千卡/千克,第 7 天为 80.78 千卡/千克。早期热量摄入与妊娠 36 周时头围和体重 Z 值的变化无关。影响头围和体重 Z 值变化的其他因素包括:胎龄、第一周的呼吸支持、36 周时需要额外的氧气以及需要干预的早产儿视网膜病变。结论在我们的早产儿队列中,矫正年龄为 36 周的早产儿的生长参数主要受其他因素的影响,而非主要受总热量摄入的影响。
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引用次数: 0
Utjecaj COVID-19 pandemije na bolesnike s novootkrivenim kolorektalnim karcinomom u Općoj bolnici Zadar COVID-19 大流行对扎达尔综合医院新确诊结直肠癌患者的影响
Q4 Medicine Pub Date : 2023-11-27 DOI: 10.57140/mj.53.3.4
Ivan Dilber, Sara Bilić Knežević, Mirisa Tokić, Jakov Mihanović, Josipa Jović Zlatović
Kolorektalni karcinom je jedna od najučestalijih zloćudnih bolesti u Republici Hrvatskoj.1 Ako se otkrije u ranom, odnosno lokaliziranom stadiju bolesti, petogodišnje preživljenje iznosi oko 90%.5 Iznimno je važno dijagnosticirati bolest u što ranijem stadiju radi boljeg ishoda liječenja. Stoga je odlukom Vlade Republike Hrvatske 2007. godine usvojen Nacionalni program ranog otkrivanja raka debelog crijeva.1 Pojava pandemije koronavirusne bolesti dovela je do izazova u funkcioniranju zdravstvenog sustava diljem svjeta, pa tako i programa ranog otkrivanja raka debelog crijeva.3 Za vrijeme Covid-19 pandemije zabilježen je smanjen broj obavljenih kolonoskopija i odaziv na program ranog otkrivanja raka debelog crijeva. Cilj ovog istraživanja je retrospektivno otvrditi utjecaj COVID-19 pandemije na bolesnike s novootkrivenim kolorektalnim karcinomom u razdoblju od 01.04.2020. do 30.09.2021. (za vrijeme COVID-19 pandemije) u odnosu na razdoblje od 01.04.2018. do 30.09.2019. (vrijeme prije COVID-19 pandemije) u Općoj bolnici Zadar. Glavni cilj istraživanja bio je odrediti vrstu operacije primarnog tumora (elektivne i hitne operacije) prije i za vrijeme COVID-19 pandemije. U našem istraživanju uspjeli smo dokazati hipotezu da će u COVID-19 pandemiji biti povećan udio hitnih operacijskih zahvata u odnosu na elektivne, što se može povezati sa smanjenim brojem preventivnih pregleda u sekundarnim zdravstvenim ustanovama, odnosno smanjenim odazivom na program za rano otkrivanje raka debelog crijeva.
大肠癌是克罗地亚共和国最常见的恶性疼痛之一。1 如果在疼痛的早期或局部阶段发现,五年生存率约为 90%。Stoga je odlukom vlády Republike Hrvatske 2007. Godine usvojen Nacionalni program ranog otkrivanja raka debelog crijeva.1 Pojava pandemije koronavirusne bolesti dovela je do izazova u funkalizaci u zdravog sustava diljem svjeta, pa tako i programu ranog otkrivanja raka debelog crijeva.3在 Covid-19 大流行期间,结肠镜检查的次数和对结肠癌早期检测计划的响应都有所减少。本研究旨在回顾性评估 2020 年 4 月 1 日至 2021 年 9 月 30 日(COVID-19 大流行期间)与 2018 年 4 月 1 日至 2019 年 9 月 30 日(COVID-19 大流行期间)期间,COVID-19 大流行对扎达尔产科克罗恩病医院新诊断结肠直肠癌患者的影响。该研究的主要目的是确定在COVID-19大流行期间的原发性肿瘤手术类型(择期手术和急诊手术)。U naší istraživanju uspjeli smo dokazjeli smo hipotezu da da će u COVID-19 pandemiji biti povećan udio hitnih operace zahvata u odnosu na elektivne, što se može povezati sa smanjenim brojem preventivnih screening u sekundarnim zdravstvenim ustanovama, odnosno smanjenim odazivom na programu za wano otkrivanje raka debelog crijeva.
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引用次数: 0
Locally aggressive giant basal cell carcinoma of the head with focus on surgical treatment - a case report 局部侵袭性头部巨型基底细胞癌的手术治疗--病例报告
Q4 Medicine Pub Date : 2023-11-27 DOI: 10.57140/mj.53.3.6
Fatima Juković-Bihorac, H. Bečulić, Emir Begagić, Rasim Skomorac
Introduction: Basal cell carcinoma is the most common non melanoma skin cancer. It accounts for approximately 80% of all skin cancers. Case report: We presented a 62-year-old patient with a giant, deeply infiltrative, destructive lesion of the head which lasted for 15 years. Microbiological analysis showed contamination, computed tomography (CT) scan showed deep infiltration and bone destruction. The risks of operative treatment were numerous. The treatment was more complicated by infection, infiltrative spreading and the patient's comorbidity. Regardless, we decided on a wide surgical resection with pathohistological evaluation of the resection margins. The patient denied oncological treatment. After 10 years, there were no recurrent tumours. Conclusion: Aggressive surgical treatment is the treatment of choice for giant basal cell carcinoma. In the case of giant locally aggressive and advanced neoplasms, when surgery is not appropriate or not possible, medical treatment becomes oncological.
简介:基底细胞癌是最常见的非黑色素瘤皮肤癌:基底细胞癌是最常见的非黑色素瘤皮肤癌。它约占所有皮肤癌的 80%。病例报告:我们接诊了一名 62 岁的患者,患者头部有一个巨大、深度浸润、破坏性病变,病程长达 15 年。微生物分析表明病灶受到污染,计算机断层扫描(CT)显示病灶深度浸润和骨质破坏。手术治疗的风险很大。感染、浸润扩散和患者的合并症使治疗更加复杂。尽管如此,我们还是决定进行大范围手术切除,并对切除边缘进行病理组织学评估。患者拒绝接受肿瘤治疗。10 年后,肿瘤没有复发。结论积极的手术治疗是巨型基底细胞癌的首选治疗方法。对于局部侵袭性巨大肿瘤和晚期肿瘤,如果不适合或无法进行手术治疗,则需要进行肿瘤内科治疗。
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引用次数: 0
Parathyroid gland carcinoma – a case report 甲状旁腺癌--病例报告
Q4 Medicine Pub Date : 2023-11-27 DOI: 10.57140/mj.53.3.5
Ivan Vučković, Ivana Pajić Matić, Tomislav Stojadinović, D. Sauerborn, Karolina Veselski, A. Mišković, J. Samardžić
Uvod: S prevalencijom od 0,005% svih karcinoma, karcinom paratireoidne žlijezde jedna je od najrjeđih malignih bolesti koja zahvaća oko 1% bolesnika s primarnim hiperparatireoidizmom. Pojavljuje se sporadično ili u sklopu genetskog sindroma. Više od 90% karcinoma paratireoidne žlijezde su hormonski funkcionalni i dovode do hipersekrecije parathormona, što uzrokuje izrazitu hiperkalcijemiju. Zbog sličnih simptoma s benignim uzrocima hiperparatireoze otežano je preoperativno dijagnosticiranje karcinoma paratireoidne žlijezde. Ultrazvuk vrata i scintigrafija s Tc-99m MIBI mogu pomoći u lokalizaciji bolesti, dok se citopunkcija prije primarne operacije ne preporučuje. Primarni modalitet liječenja je potpuna kirurška resekcija s mikroskopski negativnim rubovima i nudi najbolju šansu za izlječenje. Do sada ne postoje dokazi o učinkovitosti kemoterapijskog ili radioterapijskog pristupa. U više od 50% bolesnika dolazi do razvoja recidiva bolesti, kada je ponovna kirurška resekcija najbolji način liječenja koje tada, rijetko kurativno, služi u svrhu ublažavanja metaboličkih poremećaja i komplikacija hiperkalcijemije koje su glavni uzrok letaliteta. Prikaz bolesnice: Šezdesetogodišnja žena s nizom komorbiditeta upućena je od strane nefrologa sa sumnjom na adenom paratireoidne žlijezde. Po učinjenoj ultrazvučnoj i citološkoj obradi ekstirpira se desna donja paratireoidna žlijezda, te se patohistološkom analizom postavi dijagnoza karcinoma paratireoidne žlijezde, što posljedično indicira reoperaciju. Prije reoperacije učinjena je scintigrafija koja ukazuje na hiperfunkcijsko paratireoidno tkivo, te se u sklopu reoperacije učini desnostrana lobektomija štitnjače i ekstirpacija desne gornje uvećane paratireoidne žlijezde s disekcijom regije VI. Patohistološkom obradom izolira se uredno tkivo štitnjače, adenom paratireoidne žlijezde i jedan hormonski aktivni metastatski limfni čvor iz regije VI. Karcinom paratireoidne žlijezde je izrazito rijedak entitet koji zahtijeva operativnu intervenciju i cjeloživotno praćenje vrijednosti serumskog kalcija i parathormona. Kako bi se unaprijedilo i standardiziralo liječenje bolesnika s karcinomom paratireoidne žlijezde, potrebne su daljnje multicentrične studije.
导言:甲状旁腺癌的发病率为所有癌肿的0.005%,是最常见的恶性肿瘤之一,原发性甲状旁腺功能亢进症患者中1%会患上甲状旁腺癌。它可偶发,也可作为遗传综合征的一部分发生。90%以上的甲状旁腺癌具有激素功能,会导致甲状旁腺激素分泌过多,从而引起明显的高钙血症。由于甲状旁腺癌的症状与良性甲状旁腺功能亢进症相似,因此很难进行术前诊断。颈部超声波检查和Tc-99m MIBI闪烁扫描可帮助确定疼痛部位,直至建议进行细胞穿刺进行初级手术。主要的治疗方式是皮下手术切除,并在显微镜下阴性切缘,这样可以提供最佳的愈合机会。迄今为止,还没有证据表明化疗或放疗方法具有疗效。50%以上的患者会出现疼痛复发,此时再次手术切除是最佳治疗方案,虽然可以治愈,但可以缓解代谢紊乱和高钙血症并发症,而这正是导致死亡的主要原因。病例报告:一名患有多种并发症的60岁女性因怀疑患有甲状旁腺腺瘤而被转诊至肾脏科。经过超声波和细胞学检查后,提取了右侧供体甲状旁腺,并通过病理分析确诊为甲状旁腺癌,因此需要再次手术。再次手术时进行了闪烁照相术,结果显示甲状旁腺组织功能亢进,作为再次手术的一部分,对狭窄处进行了右侧分叶切除术,并切除了右侧上尿道甲状旁腺,同时对第VI区进行了解剖。病理组织学手术从VI区分离出狭窄组织、甲状旁腺腺瘤和一个激素活跃的转移淋巴结。甲状旁腺癌具有高度破坏性,需要进行手术干预,并终生降低血清钙和甲状旁腺激素水平。需要进一步开展多中心研究,以确定和规范甲状旁腺癌患者的治疗方法。
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引用次数: 0
Ophthalmologist Albrecht von Graefe (1828-1870) and his assistants and pupils 眼科医生 Albrecht von Graefe(1828-1870 年)及其助手和学生
Q4 Medicine Pub Date : 2023-11-27 DOI: 10.57140/mj.53.3.3
Milan Ivanišević
Albrecht von Graefe (1828. ‒ 1870.) bio je glasoviti njemački oftalmolog koji je živio i radio u Berlinu. Udario je temelje modernoj i znanstvenoj oftalmologiji i prvi je specijalist koji se bavio isključivo oftalmologijom. Smatra ga se jednim od najvažnijih oftalmologa 19. stoljeća. Bio je svestran, ali najviše ga se pamti po tome što je prvi napravio iridektomiju u liječenju akutnog glaukoma. Izumio je nož za operacije katarakti koji se koristio stotinu godina, prvi se koristio Helmholtzovim oftalmoskopom i osnovao je prvo oftalmološko društvo na svijetu. Osnovao je poznatu privatnu očnu kliniku u Berlinu u kojoj je poučavao mnogobrojne studente i liječnike iz cijelog svijeta, od kojih su poslije mnogi postali poznatim oftalmolozima. Imao je oko 130 asistenata i učenika, a među poznatijima su bili Douglas Argyll Robertson, Johann Friedrich Horner, Theodor Leber, Richard Leibreich, Louis de Wecker, Albert Mooren, Edmund Landolt, Louis Émile Javal, Julius Hirschberg. Osim toga, mnogi su liječnici dolazili posjetiti von Graefea i vidjeti njegovu čuvenu očnu kliniku. Iako je umro od plućne tuberkuloze u 42. godini, a oftalmologijom se bavio samo dvadeset godina, ostavio je veliki trag u svjetskoj oftalmologiji. Njegovi učenici prenosili su njegovo znanje i vještine, a svojim radom i inventivnošću uvelike su doprinijeli razvoju oftalmologije kao samostalne struke. Cilj ovoga rada jest prikazati von Graefeove asistente i učenike i njihov utjecaj na razvoj oftalmologije.
Albrecht von Graefe(1828 - 1870 年)是德国著名的眼科医生,曾在柏林生活和工作。他奠定了现代科学眼科学的基础,是第一位专门从事眼科工作的眼科医生。他被认为是 19 世纪最重要的眼科医生之一。他是第一个实施虹膜切除术治疗急性青光眼的人。他发明了白内障手术刀,并沿用了数百年;他是第一个使用亥姆霍兹眼科视镜的人,并成立了世界上第一个眼科协会。他在柏林创办了一家著名的私人眼科诊所,在那里他教授了许多来自世界各地的学生和医生,其中许多人后来成为了著名的眼科医生。他有大约 130 名助手和学生,熟人包括道格拉斯-阿盖尔-罗伯逊、约翰-弗里德里希-霍纳、西奥多-莱伯、理查德-莱布里希、路易斯-德-韦克、阿尔伯特-穆伦、埃德蒙-兰多特、路易斯-埃米尔-贾瓦尔、朱利叶斯-赫希伯格。此外,许多病人还见到了冯-格拉夫,参观了他的眼科诊所。虽然冯-格拉夫在 42 岁时死于肺结核,而且只做了 20 年的眼科医生,但他仍然是世界眼科界的一大悲剧。他的学生们传承了他的知识和技能,并以他们的创造力和发明力为眼科作为一门独立学科的发展做出了巨大贡献。本系列旨在介绍冯-格拉夫的助手和学生及其对眼科学发展的影响。
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引用次数: 0
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Medica Jadertina
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