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Archivos de la Sociedad Espanola de Oftalmologia最新文献

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引用次数: 0
Stellate Multiform Amelanotic Choroidopaty and the importance of its diagnosis to avoid overtreatment 星状多形态无色变性脉络膜病变及其诊断对避免过度治疗的重要性。
Pub Date : 2026-01-01 DOI: 10.1016/j.oftale.2025.502451
E. Gracia-Rovira , V. Miralles Pechuán , D. Hernandez Pérez , E. Cervera Taulet , A.-M. Duch Samper , J. Montero Hernández
SMACH (Stellate Multiform Amelanotic Choroidopathy) is a rare entity that should be considered for differential diagnosis of choroidal lesions with subretinal fluid, particularly in young patients. We present the case of a 15-year-old male with a yellow-orange choroidal lesion in the right eye, initially misinterpreted as an infection process due to the presence of a cutaneous erythema and environmental exposure. Multimodal imaging — including OCT, en-face OCT, and ICG — was essential in identifying the hallmark features of SMACH: dendriform projections, choroidal hyperreflectivity in absence of pachyvessels or deep vascular alteration, and a stellate hypofluorescent pattern. The self-limited nature of the subretinal fluid and the absence of inflammatory signs supported the diagnosis. Recognizing SMACH avoided unnecessary treatments such as anti-VEGF therapy or corticosteroids. This is Spain’s first case, it underscores the importance of early diagnosis through multimodal imaging to prevent overtreatment and to improve both visual and emotional outcomes for the patient.
SMACH(星状多形态无色变性脉络膜病)是一种罕见的疾病,在视网膜下积液脉络膜病变的鉴别诊断中应予以考虑,特别是在年轻患者中。我们报告一例15岁男性右眼黄橙色脉络膜病变,由于皮肤红斑和环境暴露,最初被误解为感染过程。多模式成像(包括OCT、正面OCT和ICG)对于识别SMACH的标志性特征至关重要:树突状突出、脉络膜高反射率(无厚血管或深部血管改变)和星状低荧光模式。视网膜下液的自限性和无炎症体征支持诊断。识别SMACH避免了不必要的治疗,如抗vegf治疗或皮质类固醇。这是西班牙的第一例病例,它强调了通过多模态成像进行早期诊断的重要性,以防止过度治疗,并改善患者的视觉和情感结果。
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引用次数: 0
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引用次数: 0
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引用次数: 0
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引用次数: 0
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引用次数: 0
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引用次数: 0
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引用次数: 0
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引用次数: 0
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引用次数: 0
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Archivos de la Sociedad Espanola de Oftalmologia
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