International journal of pediatric otorhinolaryngology最新文献_第2页

Evaluation of central auditory processing in children with developmental dyslexia 发展性阅读障碍儿童中枢听觉加工的评价。

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-01-30 DOI: 10.1016/j.ijporl.2026.112742

Senanur Kahraman Beğen , Müge Müzeyyen Çiyiltepe , Berkay Arslan

Objective

Developmental dyslexia is a neurodevelopmental disorder primarily characterized by phonological and reading difficulties. This study aimed to investigate temporal auditory processing and dichotic listening performance in children with developmental dyslexia and to explore their potential contribution to reading-related difficulties.

Methods

Sixty children aged 8–13 years participated in the study, including 30 children diagnosed with developmental dyslexia and 30 age-matched typically developing peers. Central auditory processing was assessed using the Staggered Spondaic Word (SSW) test for dichotic listening and the Frequency Pattern Test (FPT), Duration Pattern Test (DPT), and Random Gap Detection Test (RGDT) for temporal auditory processing.

Results

Children with developmental dyslexia demonstrated significantly poorer performance than controls across all temporal and dichotic auditory processing measures (p < 0.05). In the SSW test, the greatest performance difference was observed in the left competing condition. Temporal processing deficits were evident in frequency discrimination, duration pattern recognition, and gap detection tasks.

Conclusion

Children with developmental dyslexia exhibit weaknesses in temporal and dichotic auditory processing tasks. Given the linguistic demands inherent in some dichotic measures, these findings likely reflect an interaction between auditory and language-related processing rather than isolated auditory pathway dysfunction. Incorporating central auditory processing assessment into multidisciplinary dyslexia evaluations may contribute to more targeted diagnostic and intervention approaches.

目的：发展性阅读障碍是一种以语音和阅读困难为主要特征的神经发育障碍。本研究旨在探讨发展性阅读障碍儿童的时间听觉加工和二元听力表现，并探讨它们对阅读相关困难的潜在影响。方法：60名8-13岁的儿童参与研究，其中30名诊断为发展性阅读障碍的儿童和30名年龄匹配的典型发展同伴。中央听觉加工采用双听交错词（SSW）测试和时间听觉加工的频率模式测试（FPT）、持续时间模式测试（DPT）和随机间隙检测测试（RGDT）进行评估。结果：发展性阅读障碍儿童在所有时间和二元听觉加工测试中的表现明显低于对照组(p结论：发展性阅读障碍儿童在时间和二元听觉加工任务中表现出弱点。考虑到某些二分法固有的语言需求，这些发现可能反映了听觉和语言相关处理之间的相互作用，而不是孤立的听觉通路功能障碍。将中枢听觉处理评估纳入多学科阅读障碍评估可能有助于更有针对性的诊断和干预方法。

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引用次数: 0

Examining Tympanostomy Tube Outcomes in Indigenous vs. Non-Indigenous Children of Northern Quebec 北魁北克省土著儿童与非土著儿童鼓膜造瘘管结果的比较

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-01-28 DOI: 10.1016/j.ijporl.2026.112743

Saruchi Bandargal , Catherine F. Roy , Lily HP. Nguyen , Lamiae Himdi , Tamara Mijovic , Jeffrey C. Yeung

Objectives

Chronic otitis media with effusion (COME) and recurrent acute otitis media (rAOM) pose significant burdens on pediatric patients and their families. These conditions disproportionately affect marginalized populations, such as Indigenous communities in Canada, where higher incidence rates and reduced access to care are well documented. This study aims to better understand the sequelae of rAOM/COME following tympanostomy tube (TT) insertion in Indigenous pediatric patients living in northern Quebec.

Methods

A retrospective matched cohort study was conducted on children who underwent TT insertion. Indigenous patients were matched 1:2 by age and gender with non-Indigenous controls. Data collected included comorbidities, TT indications, surgical history, cancellation rates, otolaryngology and audiology assessments (pre- and post-operative), operative notes, and follow-up documentation.

Results

A total of 240 patients (80 Indigenous and 160 non-Indigenous) were analyzed. Baseline characteristics, surgical wait times (p = 0.18), and time to first follow-up (p = 0.33) were similar. At first follow-up (mean 5.4–5.9 months), Indigenous children were more likely to have tympanic membrane perforation (6.2 % vs. 1.3 %, p = 0.04). Tube extrusion was observed in 23.8 % of Indigenous children versus 15 % of non-Indigenous children (p = 0.054). Among Indigenous patients, Inuit children had a significantly higher extrusion rate (50 %) compared to First Nations children (23.3 %) (p = 0.04).

Conclusion

While access to care appears equitable post-referral, Indigenous children—particularly Inuit—exhibit higher rates of tympanic membrane perforation and possible early tube extrusion. These differences underscore the need for tailored approaches and further investigation into population-specific pathophysiology.

目的慢性中耳炎伴渗出性中耳炎（COME）和复发性急性中耳炎（rAOM）给儿童患者及其家庭带来了沉重的负担。这些疾病对边缘化人群的影响尤为严重，例如加拿大的土著社区，那里的发病率较高，获得医疗服务的机会减少，这是有据可查的。本研究旨在更好地了解居住在魁北克北部的土著儿童患者中鼓膜造瘘管（TT）置入后rAOM/COME的后遗症。方法采用回顾性匹配队列研究方法对接受TT插入的儿童进行研究。土著患者按年龄和性别与非土著对照组1:2匹配。收集的数据包括合并症、TT适应症、手术史、取消率、耳鼻喉和听力学评估（术前和术后）、手术记录和随访文件。结果共分析240例患者，其中原住民80例，非原住民160例。基线特征、手术等待时间（p = 0.18）和首次随访时间（p = 0.33）相似。在第一次随访时（平均5.4-5.9个月），土著儿童更容易出现鼓膜穿孔（6.2%比1.3%,p = 0.04）。23.8%的土著儿童出现管挤压，而非土著儿童为15% （p = 0.054）。在土著患者中，因纽特儿童的挤压率（50%）明显高于第一民族儿童（23.3%）（p = 0.04）。结论：虽然转诊后获得护理的机会公平，但土著儿童，特别是因纽特人，鼓膜穿孔和早期管挤压的发生率较高。这些差异强调需要量身定制的方法和进一步研究人群特异性病理生理学。

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引用次数: 0

Does a TEOAE refer / AABR pass profile at the neonatal hearing screening indicate risk? 新生儿听力筛查时的TEOAE参考/ AABR通过情况是否表明存在风险？

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-01-28 DOI: 10.1016/j.ijporl.2026.112748

Francesca Forli , Silvia Capobianco , Letizia Palazzo , Luca Bruschini , Stefano Berrettini , Francesco Lazzerini

Objectives

To evaluate the long-term outcomes of infants with a “refer” result on transient evoked otoacoustic emissions (TEOAE) but a subsequent bilateral “pass” on the automated auditory brainstem response (AABR) at neonatal screening, with the goal of determining the risk of permanent hearing loss and potential functional consequences during childhood of this profile.

Methods

We retrospectively analyzed infants born between 2011 and 2019 at Pisa University Hospital (Italy) who failed TEOAE but passed bilateral AABR. Long-term follow-up was conducted ≥5 years after screening using a structured telephone questionnaire on functional outcomes (speech therapy, language delay, school difficulties, formal diagnosis of hearing loss). Children with positive responses were recalled for in-person audiological testing.

Results

Among 16,574 screened newborns, 74 (0.45 %) showed a TEOAE “refer” but bilateral AABR “pass”. Long-term data were obtained for 63 children (85.1 %), with a mean follow-up age of 9.2 years (median 10, range 5–12). Of the 25 children who reported at least one functional difficulty and underwent in-person audiological reassessment, three (4.7 % of the total cohort) showed conductive hearing loss, while all others had normal pure-tone thresholds (≤20 dB HL bilaterally). The conductive losses were associated with otitis media with effusion and underlying conditions such as Down syndrome or cleft palate. Despite these findings, 25 children (39.7 %) were reported to have functional difficulties, including need for speech therapy, language delay, or school problems.

Conclusions

This is the first study to report long-term (>5 years) outcomes in children with a TEOAE “refer”/bilateral AABR “pass” profile. In this cohort, no cases of permanent hearing loss were identified. However, the relatively high prevalence of functional difficulties highlights the importance of pediatric surveillance to ensure timely recognition of developmental issues.

目的：评估新生儿筛查中瞬时诱发耳声发射（TEOAE）结果为“参考”，但随后双侧自动听觉脑干反应（AABR）结果为“通过”的婴儿的长期预后，目的是确定这种情况下儿童时期永久性听力损失的风险和潜在的功能后果。方法：回顾性分析2011年至2019年在意大利比萨大学医院出生的TEOAE失败但通过双侧AABR的婴儿。筛选后使用结构化电话问卷对功能结果（语言治疗、语言延迟、学习困难、听力损失的正式诊断）进行长期随访≥5年。阳性反应的儿童被召回进行现场听力学测试。结果：16574例新生儿中，74例（0.45%）TEOAE“正常”，但双侧AABR“通过”。63名儿童（85.1%）获得了长期数据，平均随访年龄为9.2年（中位10年，范围5-12年）。在25名报告至少一项功能困难并接受现场听力学重新评估的儿童中，3名（占总队列的4.7%）表现为传导性听力损失，而所有其他儿童的纯音阈值正常（双侧≤20 dB HL）。传导性损失与中耳炎积液和潜在疾病如唐氏综合征或腭裂有关。尽管有这些发现，25名儿童（39.7%）报告有功能障碍，包括需要言语治疗、语言迟缓或学校问题。结论：这是第一个报告TEOAE“参考”/双侧AABR“通过”患儿长期（50 - 5年）结局的研究。在这个队列中，没有发现永久性听力损失的病例。然而，相对较高的功能障碍患病率突出了儿科监测的重要性，以确保及时识别发育问题。

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引用次数: 0

Progressive analysis of language and sensory profile skills in children with auditory brainstem implants and cochlear implants 植入听觉脑干和人工耳蜗儿童语言和感觉技能的进展分析

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-01-28 DOI: 10.1016/j.ijporl.2026.112747

Nuriye Yildirim Gökay , Banu Baş , Beyza Demi̇rtaş Yilmaz , Esra Yücel

Purpose

This study aimed to analyze and compare the sensory profiles and language skills of children with auditory brainstem implants (ABI) and cochlear implants (CI) over one year.

Method

This prospective comparative study included 24 children aged 6–8 years and 11 months, consisting of 12 bimodal CI-ABI users and 12 bilateral CI users. All children received scheduled auditory rehabilitation and audiological follow-ups. Sensory profiles were assessed using the Sensory Profile scale, while school-age language skills were evaluated using the Test of Language Development-Primary: Fourth Edition. The language and sensory profile scores of the children from one year prior and later to the study were compared. Additionally, the progress levels of the groups within one year were compared.

Results

Both children with CI and ABI demonstrated significant improvements in verbal language skills (e.g., sentence repetition, p < 0.001), registration, sensory seeking, sensory input processing, low endurance, and fine motor skills over the year. However, children with CI showed significantly greater progress in verbal language composite scores (p = 0.015) and subskills such as registration and fine motor skills (p < 0.05) compared to the ABI group. Multivariate analysis further revealed that hearing loss etiology and implantation mode were significant factors influencing developmental outcomes.

Conclusion

Hearing implants not only enhance language skills but also facilitate progress in children's sensory profile sub-skills. A holistic approach that evaluates hearing, language, and overall development is recommended for hearing-impaired children.

目的分析和比较听性脑干植入（ABI）和人工耳蜗植入（CI）儿童1年内的感觉特征和语言技能。方法本前瞻性比较研究纳入24例6-8岁11个月的儿童，其中12例双侧CI- abi使用者和12例双侧CI使用者。所有儿童均接受预定的听力康复和听力学随访。感官档案使用感官档案量表进行评估，而学龄语言技能使用语言发展测试-小学：第四版进行评估。研究人员比较了研究前后一年儿童的语言和感官评分。此外，比较两组在一年内的进展水平。结果CI和ABI患儿在言语语言技能（如句子重复，p < 0.001）、注册、感觉寻找、感觉输入处理、低耐力和精细运动技能方面均有显著改善。然而，与ABI组相比，CI组儿童在口头语言综合得分（p = 0.015）和子技能（如注册和精细运动技能）方面的进步明显更大（p < 0.05）。多因素分析进一步显示，听力损失的病因和植入方式是影响发育结局的重要因素。结论植入助听器不仅能提高儿童的语言能力，还能促进儿童感觉轮廓亚技能的进步。一个全面的方法，评估听力，语言，和整体发展建议听障儿童。

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引用次数: 0

Analyses of GJB2 status in hereditary and non-syndromic hearing loss cases in Turkey reveal pathogenicity of rare c.247_249delTTC variant 对土耳其遗传性和非综合征性听力损失病例GJB2状态的分析揭示了罕见的c.247_249delTTC变异的致病性

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-01-26 DOI: 10.1016/j.ijporl.2026.112739

Sait Tümer , Mustafa Bülent Şerbetçioğlu , Günay Kırkım , Seda Nur Homurlu , Oğuz Altungöz

引用次数: 0

Composite chondroperichondrial clip (“Triple-C”) tympanoplasty in pediatric patients 复合软骨软骨膜夹（“3c”）鼓室成形术在儿科患者中的应用。

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-01-25 DOI: 10.1016/j.ijporl.2026.112746

Shadi Shinnawi , Roni Barzilai , Majd Khoury , Muhammad Zahlaka , Ali Hammad , Mauricio Cohen-Vaizer

引用次数: 0

Tracheal cartilaginous sleeve prevalence in syndromic craniosynostosis: A single institution study 气管软骨套筒在综合征性颅缝闭塞中的患病率：一项单机构研究。

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-01-24 DOI: 10.1016/j.ijporl.2026.112745

Roy K. Park , Katherine Hu , Zoe H. Fullerton , Melissa C. Lee , Rohit K. Khosla , Karthik Balakrishnan

Purpose

This study aimed to evaluate the incidence of tracheal cartilaginous sleeve (TCS) among syndromic craniosynostosis patients, as well as describe their genetic profiles, associated co-morbidities, and operative outcomes.

Methods

We performed a retrospective analysis of syndromic craniosynostosis patients (Apert, Crouzon, and Pfeiffer) at a single tertiary academic center between January 1, 2002, and February 1, 2024.

Results

39 patients with syndromic craniosynostosis were identified, with 17 patients (17/39, 43.6%) undergoing airway evaluation. 1 patient (1/17, 5.9%) was diagnosed with TCS, but 5 patients (5/17, 29.4%) had other airway abnormalities, all reflecting abnormalities of the airway wall or some type of airway stenosis. 28 patients (28/39, 73.7%) presented with a diagnosis of OSA, and 7 patients (7/39, 17.9%) of patients presented with choanal anomaly (atresia or stenosis). 32 patients (32/39, 82.1%) had genetic sequencing information available, with the most common mutations affecting p.P253R within the FGFR2 gene in 7 patients. No patients in our cohort presented with a p.W290 mutation and 7 patients presented with a p.C342 mutation, of which 4 patients had the p.C342Y mutation.

Conclusion

The true prevalence of TCS may be likely lower than prior reports, which may aid with alleviating some familial anxiety and provide additional context and data for medical counseling and decision-making. Nonetheless, all patients should be strongly recommended to undergo airway evaluation given the risks associated with TCS, the high prevalence of structural airway anomalies, and the overall low risk of airway evaluation.

目的：本研究旨在评估气管软骨套（TCS）在综合征性颅缝闭塞患者中的发病率，并描述其遗传谱、相关合并症和手术结果。方法：回顾性分析2002年1月1日至2024年2月1日在一个三级学术中心的综合征性颅缝闭锁患者（Apert， Crouzon和Pfeiffer）。结果：39例综合征性颅缝闭锁患者中，17例（17/39,43.6%）接受气道评估。1例（1/17,5.9%）患者被诊断为TCS， 5例（5/17,29.4%）患者有其他气道异常，均反映气道壁异常或某种类型的气道狭窄。28例（28/39,73.7%）患者诊断为OSA， 7例（7/39,17.9%）患者表现为后鼻孔异常（闭锁或狭窄）。32例患者（32/39,82.1%）有基因测序信息，其中最常见的突变影响7例FGFR2基因内的p.P253R。我们的队列中没有患者出现p.W290突变，7例患者出现p.C342突变，其中4例患者出现p.C342Y突变。结论：TCS的真实患病率可能低于之前的报道，这可能有助于减轻一些家庭焦虑，并为医疗咨询和决策提供额外的背景和数据。尽管如此，考虑到TCS的相关风险、结构性气道异常的高患病率以及气道评估的总体低风险，强烈建议所有患者接受气道评估。

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引用次数: 0

The role of nasopharyngeal airways in Robin sequence: Insights from a retrospective cohort study with review of the literature 鼻咽气道在罗宾序列中的作用：来自回顾性队列研究的见解，并回顾了文献

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-01-24 DOI: 10.1016/j.ijporl.2026.112744

Shirley van de Velde , Maartje Haasnoot , Saskia Coenraad , J. Peter W. Don Griot , Aebele B. Mink van der Molen , Emma C. Paes

引用次数: 0

Demography and outcomes of frozen tongue: a scoping review of Scandinavian tundra tongue cases 人口统计学和冰冻舌的结果：斯堪的纳维亚苔原舌病例的范围审查。

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-01-20 DOI: 10.1016/j.ijporl.2026.112740

Anders Hagen Jarmund , Sofie Eline Tollefsen , Baard Cristoffer Sakshaug , Yashar Honarmandi , Sverre Helge Torp

Background

Children occasionally adhere their tongues to cold metal surfaces during winter (“tundra tongue”), but little is known about the epidemiology and outcomes of these cases.

Objectives

To explore the following questions: who experiences tundra tongue, under which circumstances does it occur, and what are the outcomes?

Methods

We conducted a scoping review to identify case reports published in historical newspapers from Norway, Sweden and Denmark using national library databases. Epidemiological data were charted manually from newspaper items describing literal frozen tongues.

Results

Among 17,009 unique search hits, 856 reports of 113 different cases were identified. Almost all cases (96 %) involved children, median age 5.25 years, and the majority were boys (63 %). Tongues were most often frozen to railings (40 %). Ambient temperature was reported in 18 cases with a median of −16.5 °C. Outcomes ranged from discomfort to potential amputation of tongue tissue, with 20 (18 %) cases involving a doctor or a hospital. Severe injuries were reported in several cases through three distinct mechanisms: (1) the direct effect of cold on tissue, (2) detachment injuries, and (3) the consequences of immobility.

Conclusion

Children, and especially boys, in wintertime, are vulnerable to tundra tongue. Most cases had no or mild consequences but severe injuries were also described in multiple cases. Hence, parents, health care professionals and policymakers should not underestimate the potential harm of tundra tongue.

背景：儿童在冬季偶尔会将舌头粘在寒冷的金属表面（“苔原舌头”），但对这些病例的流行病学和结果知之甚少。目的：探讨以下问题：谁会经历冻土带舌头，在什么情况下会发生，结果是什么？方法：我们使用国家图书馆数据库对挪威、瑞典和丹麦的历史报纸上发表的病例报告进行了范围综述。流行病学数据是根据报纸上描述冰冻舌头的文字手工绘制的。结果：在17,009个独立搜索命中，确定了113个不同病例的856个报告。几乎所有病例（96%）涉及儿童，中位年龄5.25岁，大多数为男孩（63%）。舌头最常冻僵在栏杆上（40%）。18例报告环境温度中位数为-16.5°C。结果从不适到可能的舌组织截肢不等，其中20例（18%）涉及医生或医院。据报道，在一些病例中，严重的损伤有三种不同的机制：(1)冷对组织的直接影响，(2)脱离损伤，(3)不活动的后果。结论：冬季儿童，尤其是男孩易患冻土带舌病。大多数情况下没有或轻微的后果，但严重的伤害也在多个情况下描述。因此，家长、卫生保健专业人员和决策者不应低估冻土带舌头的潜在危害。

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引用次数: 0

Exploring cochlear implantation and quality of life in pediatric recipients with autism spectrum disorder 探讨人工耳蜗植入对儿童自闭症谱系障碍患者生活质量的影响

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-01-20 DOI: 10.1016/j.ijporl.2026.112725

Meredith Allen , Camille Reeves , Sofia Torres-Small , Robert J. Yawn , Charles B. Macdonald , Samuel H. Smith , Celine Richard

Objective

This study aims to comprehensively assess the timing and accessibility of cochlear implantation, patterns of its utilization, and the associated outcomes related to quality of life (QoL), in children diagnosed with autism spectrum disorder (ASD).

Study design

Retrospective case-control review, and cross-sectional hearing-related QoL survey.

Setting

Tertiary children's hospital.

Methods

This investigation employed a retrospective case-control design, complemented by a cross-sectional hearing-related QoL survey using the HEAR-QL questionnaires. Outcomes were compared between two populations of pediatric cochlear implant recipients: one group with a preoperative diagnosis of ASD and a control group of neurotypical peers. A review of 413 patient records from 2000 to 2022 identified 22 eligible patients with ASD and matched controls. Of these, 16 participants from the ASD group and 16 controls completed the prospective quality-of-life surveys.

Results

The time between the definitive diagnosis of profound sensorineural hearing loss and the cochlear implantation evaluation was longer for patients with ASD. However, no other significant differences in care delays were observed between ASD children and controls, including time to CI qualification, and implantation. Nevertheless, children with ASD aged 2–6 years showed poorer outcomes in social interaction (p = 0.02) and new social situations (p = 0.02 and 0.04). Despite these behavioral differences, no significant disparity in hearing-related QoL-related communication outcomes was observed.

Conclusion

The study shows that cochlear implant benefit children with ASD, with expected challenges not affecting overall success. It underscores the importance of individualized approaches to address delays in CI evaluation, communication, and social interaction challenges. These insights can help guide care teams, parents and educators in setting realistic expectations following cochlear implantation.

目的综合评价自闭症谱系障碍（ASD）儿童人工耳蜗植入的时机、可及性、使用模式以及与生活质量（QoL）相关的结果。研究设计：回顾性病例对照研究和听力相关生活质量横断面调查。设置三级儿童医院。方法本研究采用回顾性病例对照设计，并辅以使用听力- ql问卷进行听力相关生活质量横断面调查。比较两组儿童人工耳蜗受者的结果：一组术前诊断为ASD，对照组为神经正常的同龄人。对2000年至2022年413例患者记录的回顾确定了22例符合条件的ASD患者和匹配的对照组。其中，来自ASD组的16名参与者和对照组的16名参与者完成了预期生活质量调查。结果ASD患者从明确诊断为重度感音神经性听力损失到人工耳蜗植入评估的时间较长。然而，在ASD儿童和对照组之间，在护理延迟方面没有观察到其他显著差异，包括CI认证时间和植入时间。然而，2-6岁ASD儿童在社交互动（p = 0.02）和新社会情境（p = 0.02和0.04）方面表现较差。尽管存在这些行为差异，但在听力相关的生活质量相关的沟通结果中没有观察到显著差异。结论：研究表明人工耳蜗对ASD儿童有益，预期的挑战不会影响整体的成功。它强调了个性化方法在解决CI评估、沟通和社会互动挑战中的延迟的重要性。这些见解可以帮助指导护理团队、家长和教育工作者在人工耳蜗植入后设定切合实际的期望。

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引用次数: 0