International journal of pediatric otorhinolaryngology最新文献

英文中文

Evaluation of parental satisfaction regarding early activation in the management of cochlear implant in children 儿童人工耳蜗早期激活治疗的家长满意度评价。

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-03-01 Epub Date: 2026-01-13 DOI: 10.1016/j.ijporl.2026.112726

Valentine Nicolas , Maëlle Raccah , Marie Perrinet , François-Xavier Betolaud , Nathalie Petroff , Salma Jbyeh , Natacha Teissier , Emilie Bois

Introduction

Depending on the habits of the implanting center, the time interval between the surgical procedure and the activation of a cochlear implant varies greatly. Traditionally, the activation occurs several weeks after surgery, particularly in pediatric population. If recent improvements have concern surgical procedures and peri-operative care, early fitting constitutes the next optimization in cochlear implant management; for the past 5 years, we have introduced early fitting with Day 1 activation in the Robert Debré pediatric hospital. This study aims to evaluate the satisfaction of parents regarding early activation of their child's cochlear implant.

Materials and methods

Pediatric patients who underwent an early activation of their cochlear implant between 2021 and 2024 in Robert Debré Hospital were included in the study. A satisfaction questionnaire was handed out to the parents and collected. The questionnaire encompassed informations received before implantation and during the hospital stay, and their feelings regarding early activation, and after hospital discharge.

Results

68 parents of patients completed the questionnaire: 73.5 % were activated on day 1 of surgery. 60.3 % considered that early activation has not been painful for their child. 53 % of the parents identified a reaction to an auditory stimulus in their child during activation. 44 % were satisfied with the clinical pharmacologist's visit. 92.3 % were satisfied with the early activation procedure, and 97 % with returning home with an activated cochlear implant. They felt well informed before and after the surgery. No major complication was reported amongst our patients.

Conclusion

Parents are satisfied with their child's early activation of the cochlear implant and felt relieved to go home with an activated processor and early data on the proper functioning of the implant.

导语：根据植入中心的习惯，手术过程和人工耳蜗激活之间的时间间隔差别很大。传统上，激活发生在手术后几周，特别是在儿科人群中。如果最近的改进涉及手术程序和围手术期护理，早期安装是人工耳蜗管理的下一个优化；在过去的5年里，我们在Robert debr儿科医院引入了第一天激活的早期适配。本研究旨在评估家长对儿童人工耳蜗早期激活的满意度。材料和方法：2021年至2024年间在Robert debr医院接受人工耳蜗早期激活的儿科患者被纳入研究。家长们收到了一份满意度调查问卷。问卷包含植入前和住院期间收到的信息，以及他们对早期激活和出院后的感受。结果：68名患者家长完成了问卷调查，73.5%的家长在手术第一天被激活。60.3%的人认为早期激活对他们的孩子来说没有痛苦。53%的父母在孩子被激活时识别出了对听觉刺激的反应。44%的人对临床药理学家的来访感到满意。92.3%的人对早期激活程序感到满意，97%的人对带激活人工耳蜗回家感到满意。他们在手术前和手术后都感觉很了解情况。在我们的患者中没有重大并发症的报告。结论：家长对孩子早期激活人工耳蜗感到满意，并对带着激活的处理器和人工耳蜗正常功能的早期数据回家感到放心。

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引用次数: 0

Progressive analysis of language and sensory profile skills in children with auditory brainstem implants and cochlear implants 植入听觉脑干和人工耳蜗儿童语言和感觉技能的进展分析

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-03-01 Epub Date: 2026-01-28 DOI: 10.1016/j.ijporl.2026.112747

Nuriye Yildirim Gökay , Banu Baş , Beyza Demi̇rtaş Yilmaz , Esra Yücel

Purpose

This study aimed to analyze and compare the sensory profiles and language skills of children with auditory brainstem implants (ABI) and cochlear implants (CI) over one year.

Method

This prospective comparative study included 24 children aged 6–8 years and 11 months, consisting of 12 bimodal CI-ABI users and 12 bilateral CI users. All children received scheduled auditory rehabilitation and audiological follow-ups. Sensory profiles were assessed using the Sensory Profile scale, while school-age language skills were evaluated using the Test of Language Development-Primary: Fourth Edition. The language and sensory profile scores of the children from one year prior and later to the study were compared. Additionally, the progress levels of the groups within one year were compared.

Results

Both children with CI and ABI demonstrated significant improvements in verbal language skills (e.g., sentence repetition, p < 0.001), registration, sensory seeking, sensory input processing, low endurance, and fine motor skills over the year. However, children with CI showed significantly greater progress in verbal language composite scores (p = 0.015) and subskills such as registration and fine motor skills (p < 0.05) compared to the ABI group. Multivariate analysis further revealed that hearing loss etiology and implantation mode were significant factors influencing developmental outcomes.

Conclusion

Hearing implants not only enhance language skills but also facilitate progress in children's sensory profile sub-skills. A holistic approach that evaluates hearing, language, and overall development is recommended for hearing-impaired children.

目的分析和比较听性脑干植入（ABI）和人工耳蜗植入（CI）儿童1年内的感觉特征和语言技能。方法本前瞻性比较研究纳入24例6-8岁11个月的儿童，其中12例双侧CI- abi使用者和12例双侧CI使用者。所有儿童均接受预定的听力康复和听力学随访。感官档案使用感官档案量表进行评估，而学龄语言技能使用语言发展测试-小学：第四版进行评估。研究人员比较了研究前后一年儿童的语言和感官评分。此外，比较两组在一年内的进展水平。结果CI和ABI患儿在言语语言技能（如句子重复，p < 0.001）、注册、感觉寻找、感觉输入处理、低耐力和精细运动技能方面均有显著改善。然而，与ABI组相比，CI组儿童在口头语言综合得分（p = 0.015）和子技能（如注册和精细运动技能）方面的进步明显更大（p < 0.05）。多因素分析进一步显示，听力损失的病因和植入方式是影响发育结局的重要因素。结论植入助听器不仅能提高儿童的语言能力，还能促进儿童感觉轮廓亚技能的进步。一个全面的方法，评估听力，语言，和整体发展建议听障儿童。

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引用次数: 0

Wideband absorbance measurements in cochlear implant recipients: Insights into the Transcranial Veria Technique 人工耳蜗受者的宽带吸光度测量：经颅Veria技术的见解。

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-03-01 Epub Date: 2026-01-13 DOI: 10.1016/j.ijporl.2026.112727

Nerale Maraiah Mamatha , Raghunath Bansode Rohit , Karuppannan Arunraj

Purpose

Cochlear implantation (CI) significantly improves hearing in individuals with severe to profound sensorineural hearing loss. However, variations in surgical techniques may affect middle and inner ear mechanics. This study explores the effect of transcranial transcanal wall-Veria technique for CI on middle ear mechanics, measured using wideband absorbance (WBA).

Methods

Ten children (4–7 years) who underwent CI using the transcranial Transcanal wall-Veria technique were compared to age- and gender-matched controls with normal-hearing children. Tympanometric measures such as static compliance, tympanometric peak pressure, Ear canal volume, resonance frequency, and wideband absorbance at peak and ambient pressure were measured.

Results

Conventional 226 Hz Tympanometric measures were similar for both CI and Normal hearing groups, showing no significant differences (p > 0.05) between the groups. However, WBA measurements revealed significant changes (p < 0.05) in absorbance across frequencies, particularly at higher frequencies (2000–8000 Hz). The WBA pattern was different, with two maximum absorbance for normal-hearing children, whereas single maxima around 2000 Hz for CI group. Further, WBA at peak pressure differed from ambient pressure in both groups at low and mid-frequencies, with significant differences (p < 0.05) observed only in CI group. These results suggest that the Veria technique causes alterations in middle ear mechanics, specifically in the high-frequency regions.

Conclusions

This study highlights the utility of WBA in detecting subtle, frequency-specific changes in ear mechanics following the Veria CI technique, which may remain undetected by conventional tympanometry. Although functional auditory outcomes such as aided thresholds, speech perception scores, and eSRT were not correlated in this study,the findings underscore the importance of WBA as an advanced diagnostic tools in assessing the impact of surgical techniques on ear function post-CI.

目的：人工耳蜗植入术（CI）可显著改善重度至重度感音神经性听力损失患者的听力。然而，手术技术的变化可能会影响中耳和内耳的力学。本研究探讨了经颅经扫描wall-Veria技术对中耳力学的影响，采用宽带吸光度（WBA）测量。方法：10名4-7岁的儿童使用经颅经scanal wall-Veria技术接受CI，并与年龄和性别匹配的正常听力儿童进行比较。测量了静顺应性、峰值压力、耳道容积、共振频率、峰值压力和环境压力下的宽带吸光度等鼓室测量指标。结果：CI组与正常听力组常规226 Hz鼓室测量值相似，组间无显著差异（p < 0.05）。结论：本研究强调了WBA在检测Veria CI技术后耳力学中细微的频率特异性变化方面的实用性，这可能是传统鼓室测量法无法检测到的。虽然在本研究中，辅助阈值、语音感知评分和eSRT等功能性听觉结果并不相关，但研究结果强调了WBA作为评估手术技术对ci后耳功能影响的先进诊断工具的重要性。

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引用次数: 0

Adenoidectomy with tympanostomy or with myringotomy alone: A systematic review of pediatric randomized controlled trials 腺样体切除联合鼓室切开术或单独鼓膜切开术：一项儿科随机对照试验的系统综述

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-03-01 Epub Date: 2026-01-12 DOI: 10.1016/j.ijporl.2026.112718

Ebraheem Albazee , Noof Albannai , Hajar Alismail , Yasmeen Alazemi , Munawer Alsaeed , Esraa Alhammadi , Abrar Awadh , Abdullah Alabdullah , Mariam AlRaish , Ahmad Alawadhi , Ghezlan Aldawas , Mohmmad Alkaak , Dhoha Ismaeel

Background

Otitis media with effusion (OME) is a leading cause of acquired conductive hearing loss in children. When performing an adenoidectomy for OME, surgeons must decide whether to supplement the procedure with a simple myringotomy or a myringotomy with tympanostomy tube (TT) insertion. While TT offers extended middle ear ventilation, it carries a risk of long-term complications. This systematic review of randomized controlled trials (RCTs) aimed to compare the efficacy and safety of these two approaches.

Methods

A comprehensive search of PubMed, Scopus, CENTRAL, and Web of Science was conducted for RCTs up to August 2025. Eligible RCTs were assessed for quality using the risk of bias (RoB)-2 tool. The primary outcomes were hearing improvement and resolution of effusion. Secondary outcomes included OME recurrence and postoperative complications.

Results

Eleven RCTs involving 955 pediatric patients were included. The addition of TT consistently resulted in superior short-term outcomes, with significantly better hearing levels and faster resolution of middle ear effusion within the first 3–6 months. However, these advantages were not sustained, and no significant differences in hearing or effusion rates were observed at 12-month follow-ups. In contrast, the TT group experienced a significantly higher incidence of long-term complications, including otorrhea, tympanosclerosis, and persistent tympanic membrane perforation.

Conclusion

Adding a TT to adenoidectomy provides a transient benefit in hearing and effusion resolution but significantly increases the risk of long-term tympanic membrane complications. Adenoidectomy with myringotomy alone appears to be a safer and equally effective long-term strategy for managing pediatric OME.

背景：渗出性中耳炎是儿童获得性传导性听力损失的主要原因。当对OME进行腺样体切除术时，外科医生必须决定是否辅以简单的鼓膜切开术或鼓膜切开术并插入鼓膜造瘘管（TT）。虽然TT提供了延长的中耳通气，但它有长期并发症的风险。本系统综述随机对照试验（rct）旨在比较这两种方法的疗效和安全性。方法对截至2025年8月的随机对照试验进行PubMed、Scopus、CENTRAL、Web of Science的综合检索。使用风险偏倚(RoB)-2工具评估符合条件的随机对照试验的质量。主要结果是听力改善和积液的消除。次要结果包括OME复发和术后并发症。结果纳入6项随机对照试验，共955例儿科患者。TT治疗的短期效果一直很好，在最初的3-6个月内，患者的听力水平明显提高，中耳积液的清除速度也更快。然而，这些优势并没有持续，在12个月的随访中没有观察到听力或积液率的显著差异。相比之下，TT组的长期并发症发生率明显更高，包括耳漏、鼓膜硬化和持续性鼓膜穿孔。结论在腺样体切除术中加入TT对听力和积液解决有短暂的好处，但明显增加了长期鼓膜并发症的风险。腺样体切除术联合鼓膜切开术似乎是治疗小儿OME的一种更安全、同样有效的长期策略。

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引用次数: 0

Prevalence of vestibular pathology in patients with congenital inner ear malformation 先天性内耳畸形患者前庭病变的患病率

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-03-01 Epub Date: 2026-01-13 DOI: 10.1016/j.ijporl.2026.112723

Gillian Michaelson , Chelsea Cleveland , Daniel Karasik , Todd Otteson

引用次数: 0

Using artificial intelligence to rewrite the script on pediatric ENT patient education 用人工智能重写儿科耳鼻喉科患者教育的剧本

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-03-01 Epub Date: 2026-01-05 DOI: 10.1016/j.ijporl.2026.112707

Andrew B. Brown , Kastley Marvin , Philip A. Gaudreau

引用次数: 0

Genetic screening for hearing impairment and the genotype-phenotype correlation of GJB2 c.109G>A variants in 47,729 neonates: a population-based study in southern China 47,729名新生儿GJB2 c.109G>A基因型-表型相关性的听力障碍遗传筛查：一项基于华南人群的研究

IF 1.3 4区医学 Q3 OTORHINOLARYNGOLOGY

International journal of pediatric otorhinolaryngology

Pub Date : 2026-03-01 Epub Date: 2026-01-17 DOI: 10.1016/j.ijporl.2026.112737

Jianjun Li, Meng Guo, Wenwen Yu, Li Ma, Qi Zhang, Qi Wang, Xueyu Yang, Hongyun He, Wenlan Liu

Background

This study aimed to characterize the Variant profile of the 4 common deafness-causing genes and evaluated the genotype-phenotype correlation of GJB2 c.109G > A variants in a neonatal cohort, providing insights for early diagnosis of congenital hearing loss.

Methods

A total of 47,729 newborns in Shenzhen underwent integrated deafness gene screening (23 common pathogenic variants across GJB2, SLC26A4, MT-RNR1, and GJB3) and two-stage audiometric assessments from January 2022 to November 2024. Participants were stratified into three groups based on GJB2 c.109G > A genotypes: homozygous (Group A, n = 487), compound heterozygous (Group B, n = 87), and heterozygous carriers (Group C, n = 8055). Hearing function was evaluated via otoacoustic emissions (OAE) at 48 h postpartum, with non-passing cases receiving follow-up OAE and auditory brainstem response (ABR) testing at 42 days.

Results

Deafness-associated Variant were detected in 21.56 % (10,291/47,729) of neonates, with GJB2 exhibiting the highest carrier frequency (20.25 %), followed by SLC26A4 (1.44 %), MT-RNR1 (0.28 %), and GJB3 (0.18 %). The GJB2 c.109G > A locus dominated the variant landscape, with a carrier rate of 18.12 % (n = 8649) and an minor allele frequency of 9.57 %. The overall pass rates for the two-stage audiological assessments differed significantly across the groups: 63.66 % (Group A), 70.11 % (Group B), and 98.92 % (Group C). Bilateral hearing impairment predominated in Groups A and B.

Conclusion

The GJB2 c.109G > A Variant represents the most prevalent pathogenic variant in Shenzhen neonates, and the infants carrying deafness-causing genotypes of this variant presents relatively high hearing screening pass rate. Integrated genetic and audiometric screening could enhance early identification of high-risk infants.

背景：本研究旨在研究新生儿队列中4种常见致聋基因的变异谱，并评估GJB2 c.109G > A变异的基因型-表型相关性，为先天性听力损失的早期诊断提供依据。方法：从2022年1月至2024年11月，深圳共有47,729名新生儿接受了综合耳聋基因筛查（GJB2、SLC26A4、MT-RNR1和GJB3的23种常见致病变异）和两阶段听力评估。根据GJB2 C . 109g > A基因型将参与者分为三组：纯合子（A组，n = 487）、复合杂合子（B组，n = 87）和杂合子携带者（C组，n = 8055）。在产后48 h通过耳声发射（OAE）评估听力功能，未通过的病例在产后42天接受随访的OAE和听觉脑干反应（ABR）测试。结果：新生儿中耳聋相关变异检出率为21.56%(10,291/47,729)，其中GJB2的检出率最高（20.25%），其次为SLC26A4（1.44%）、MT-RNR1（0.28%）、GJB3（0.18%）。GJB2 c.109G > A基因座在变异格局中占主导地位，携带率为18.12% (n = 8649)，等位基因频率为9.57%。两阶段听力学评估的总体通过率在各组之间差异显著：63.66% （A组），70.11% （B组）和98.92% （C组）。结论：GJB2 c.109G > A变异是深圳新生儿中最常见的致病变异，携带该变异致聋基因型的婴儿听力筛查通过率较高。综合遗传和听力筛查可提高高危婴儿的早期识别。

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